title: Rupture of sinus of Valsalva aneurysm with aorto-biventricular fistulas and right-ventricular outflow tract obstruction: a unique association.
abstract: Sinus of Valsalva aneurysms are a rare entity. Rupture of such aneurysms is a major cause of aortocardiac fistulas usually occurring between the right sinus of Valsalva and right cardiac chambers. We report an exceptional case of a ruptured congenital sinus of Valsalva aneurysm with fistulas involving both the right- and left-ventricular outflow tracts and causing RVOT obstruction. We also demonstrate the utility of computed tomography angiography and transesophageal echocardiography in diagnosing these fistulas.
authors.affiliation: Division of Pediatric Cardiology, Department of Pediatrics, Children's Heart Center, American University of Beirut Medical Center, Beirut, Lebanon.
authors.forename: Samer I
authors.initials: SI
authors.lastname: Masri
authors.forename: Fadi F
authors.initials: FF
authors.lastname: Bitar
authors.forename: Mariam T
authors.initials: MT
authors.lastname: Arabi
authors.forename: Marianne N
authors.initials: MN
authors.lastname: Majdalani
authors.forename: Mounir Y
authors.initials: MY
authors.lastname: Obeid
authors.forename: Zohair Y
authors.initials: ZY
authors.lastname: Al Halees
authors.forename: Karim A
authors.initials: KA
authors.lastname: Diab
mesh_terms: D017542:Aneurysm, Ruptured / Q000150:complications / Q000151:congenital* / Q000175:diagnosis; D000792:Angiography; D001013:Aorta, Thoracic; D001014:Aortic Aneurysm / Q000150:complications* / Q000151:congenital / Q000175:diagnosis; D003937:Diagnosis, Differential; D017548:Echocardiography, Transesophageal; D006322:Heart Aneurysm / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D008297:Male; D061330:Multidetector Computed Tomography; D012850:Sinus of Valsalva; D016157:Vascular Fistula / Q000175:diagnosis / Q000209:etiology*; D014694:Ventricular Outflow Obstruction / Q000175:diagnosis / Q000209:etiology*; D055815:Young Adult