title: Case for diagnosis.
abstract: We report a clinical case of a rare variant of pemphigus - pemphigus herpetiformis - which combines the clinical features of dermatitis herpetiformis with the immunological findings of pemphigus. Due to its atypical presentation, it is frequently misdiagnosed as dermatitis herpetiformis. It is basically characterized by the herpetiform pattern of skin lesions, severe pruritus and by the presence of eosinophilic spongiosis confirmed on histopathology. We call attention to the excellent response to dapsone.
authors.affiliation: Service of Dermatology, Centro Hospitalar do Porto (Porto Hospital Center), EPE - Hospital de Santo Antonio (Santo Antonio Hospital) - Porto, Portugal. iolanda.c.fernandes@iol.pt
authors.forename: Iolanda Conde
authors.initials: IC
authors.lastname: Fernandes
authors.forename: Madalena
authors.initials: M
authors.lastname: Sanches
authors.forename: Rosário
authors.initials: R
authors.lastname: Alves
authors.forename: Manuela
authors.initials: M
authors.lastname: Selores
mesh_terms: D003874:Dermatitis Herpetiformis / Q000473:pathology*; D003937:Diagnosis, Differential; D006801:Humans; D008297:Male; D008875:Middle Aged; D010392:Pemphigus / Q000473:pathology*; D012867:Skin / Q000473:pathology*