title: Extended aortic repair using frozen elephant trunk technique for Marfan syndrome with acute aortic dissection.
abstract: OBJECTIVE
  The aim of this study was to analyze midterm results of frozen elephant trunk technique for Marfan syndrome with acute aortic dissection.
  
  
  METHODS
  Between February 1999 and August 2011 we performed arch replacement uisng frozen elephant trunk technique for acute aortic dissection in 8 patients with Marfan syndrome containing two complicated type B dissections and six type A dissections.Five patients compromised annulo-aortic ectasia who performed Bentall operation.
  
  
  RESULTS
  No patients died in the initial operation. Fate of false lumen on the stent graft border was expressed by CT scan follow-up that were patent in 0, thrombosis in 5 and absorption in 3 patients. One patient who had new aortic dissection 8 years after initial surgery required the Crawford V operation. Ten-years-survival rate was 100% and ten years-event free rate was 67%.
  
  
  CONCLUSIONS
  Frozen elephant trunk technique was feasible for Marfan syndrome with acute aortic dissection and might become alternative prophylactic treatment to the downstream aorta for acute aortic dissection.
authors.affiliation: Division of Surgery, Hiroshima University, Hiroshima, Japan.
authors.forename: Naomichi
authors.initials: N
authors.lastname: Uchida
authors.forename: Akira
authors.initials: A
authors.lastname: Katayama
authors.forename: Masatsugu
authors.initials: M
authors.lastname: Kuraoka
authors.forename: Keijiro
authors.initials: K
authors.lastname: Katayama
authors.forename: Shinya
authors.initials: S
authors.lastname: Takahashi
authors.forename: Taiichi
authors.initials: T
authors.lastname: Takasaki
authors.forename: Taijiro
authors.initials: T
authors.lastname: Sueda
mesh_terms: D000208:Acute Disease; D000328:Adult; D000784:Aortic Dissection / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D001014:Aortic Aneurysm / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D001027:Aortography / Q000379:methods; D001807:Blood Vessel Prosthesis; D019917:Blood Vessel Prosthesis Implantation / Q000295:instrumentation / Q000379:methods*; D018572:Disease-Free Survival; D057510:Endovascular Procedures / Q000295:instrumentation / Q000379:methods*; D005260:Female; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D008875:Middle Aged; D012008:Recurrence; D012086:Reoperation; D012189:Retrospective Studies; D015607:Stents; D013997:Time Factors; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome