title: Incontinentia pigmenti presenting as encephalopathy.
abstract: Incontinentia Pigmenti is a rare neurocutaneous disorder that may present with neurological symptoms in early infancy in addition to characteristic skin rashes. We report a two-mo-old girl presenting with a rash and encephalopathy. Magnetic resonance imaging of brain showed hemorrhagic infarcts. First we thought baby was suffering from a skin infection with meningo-encephalitis and later with development of characteristic skin lesions, neuroimaging and skin biopsy changes we reconsidered our diagnosis as Incontinentia pigmenti.
authors.affiliation: Indira Gandhi Institute of Child Health, Bangalore, Karnataka, India, drknvraju@hotmail.com.
authors.forename: Vykuntaraju
authors.initials: V
authors.lastname: K N Gowda
authors.forename: Chandra
authors.initials: C
authors.lastname: Mouly
authors.forename: Asthik
authors.initials: A
authors.lastname: Biswas
authors.forename: Shivananda
authors.initials: S
authors.lastname: Shivananda
mesh_terms: D001927:Brain Diseases / Q000175:diagnosis*; D002675:Child, Preschool; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007184:Incontinentia Pigmenti / Q000175:diagnosis*