title: Reconstruction of Ollier disease in a severely involved hand.
abstract: Ollier disease is a nonhereditary disorder characterized by multiple enchondromata, with a random asymmetrical distribution. We report an unusual case of massive ulcerating multiple enchondromata of the left hand of an 11-year-old male patient. A methodical approach to treating such a massive tumor burden and steps in reconstructing the hand are described. This case report demonstrates a radical expression of this disease; however, no malignancy was identified despite the aggressive and chronic nature of the disease. Unlike previously reported cases with less severe involvement, this patient did not undergo amputation, and this approach demonstrates a strategy for limb salvage not previously described. In particular, despite bony defects of 6 cm, no autograph was necessary for the reconstruction of the hand.
authors.affiliation: From The Division of Plastic and Reconstructive Surgery, USC Keck School of Medicine, University of California; and Cedars Sinai Hospital, Los Angeles, CA.
authors.forename: Melissa A
authors.initials: MA
authors.lastname: Klausmeyer
authors.forename: Myles J
authors.initials: MJ
authors.lastname: Cohen
authors.forename: David A
authors.initials: DA
authors.lastname: Kulber
mesh_terms: D002648:Child; D004687:Enchondromatosis / Q000473:pathology / Q000601:surgery*; D006225:Hand / Q000473:pathology / Q000601:surgery*; D006801:Humans; D023821:Limb Salvage / Q000379:methods*; D008297:Male; D019651:Plastic Surgery Procedures