title: Congenital glaucoma from Sturge-Weber syndrome: a modified surgical approach.
abstract: Sturge-Weber syndrome (SWS) is a rare congenital neurocutaneous disorder that causes congenital glaucoma. Previous experiences have shown that drainage procedures are often required to control associated glaucoma. The conventional surgical approach in trabeculectomy carries a significant risk of intraoperative expulsive hemorrhage. Here, we describe a modified approach of the conventional trabeculectomy technique, which may lower the risk of expulsive hemorrhage. A viscoelastic device was employed to maintain a steady intraocular pressure throughout the procedure. Details of the surgical technique and material used are described. One patient with congenital glaucoma associated with SWS underwent a successful trabeculectomy using the modified technique. Postoperative intraocular pressure was successfully reduced and no intraoperative complications occurred. We describe a successful case of trabeculectomy in a SWS case where a modified technique was applied.
authors.affiliation: The Hong Kong Ophthalmic Associates, Central, Hong Kong.
authors.forename: Nancy Shi Yin
authors.initials: NS
authors.lastname: Yuen
authors.forename: Ian Yat Hin
authors.initials: IY
authors.lastname: Wong
mesh_terms: D005901:Glaucoma / Q000151:congenital*; D006801:Humans; D007231:Infant, Newborn; D007429:Intraocular Pressure; D008297:Male; D013341:Sturge-Weber Syndrome / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D014130:Trabeculectomy / Q000379:methods*; D014792:Visual Acuity