title: Magnetic resonance imaging findings of isolated right ventricular hypoplasia.
abstract: Isolated right ventricular hypoplasia, unassociated with severe pulmonary or tricuspid valvular malformation, is a rare congenital heart disease. Herein the authors report a case of a 6-year-old girl having isolated right ventricular hypoplasia treated with one and a half ventricular repair, and describe the cardiac magnetic resonance (CMR) imaging findings. CMR imaging revealed diffuse subendocardial or transmural late gadolinium enhancement of the right ventricle with a thin, smooth wall due to the absence of trabeculations. Noncompaction of the left ventricle was also demonstrated, although the relevance to isolated right ventricular hypoplasia is not obviously explicable.
authors.affiliation: Department of Radiology, Seoul National University Hospital, 101 Daehak-ro, Jongno-gu, Seoul, Korea.
authors.forename: Hyungjin
authors.initials: H
authors.lastname: Kim
authors.forename: Eun-Ah
authors.initials: EA
authors.lastname: Park
authors.forename: Whal
authors.initials: W
authors.lastname: Lee
authors.forename: Jin Wook
authors.initials: JW
authors.lastname: Chung
authors.forename: Jae Hyung
authors.initials: JH
authors.lastname: Park
authors.forename: Gi Beom
authors.initials: GB
authors.lastname: Kim
authors.forename: Woong-Han
authors.initials: WH
authors.lastname: Kim
mesh_terms: D000293:Adolescent; D006348:Cardiac Surgical Procedures; D002648:Child; D003287:Contrast Media; D004452:Echocardiography; D005260:Female; D006330:Heart Defects, Congenital / Q000473:pathology* / Q000601:surgery; D006352:Heart Ventricles / Q000002:abnormalities / Q000473:pathology / Q000601:surgery; D006801:Humans; D056830:Isolated Noncompaction of the Ventricular Myocardium / Q000473:pathology; D008279:Magnetic Resonance Imaging; D011237:Predictive Value of Tests; D016896:Treatment Outcome
chemical_list: D003287:Contrast Media