title: [Dopamine-secreting pheochromocytoma with neurofibromatosis type 1 : a case report].
abstract: Pheochromocytoma occurs in 0.1-5.7% of patients with neurofibromatosis type 1 (NF1), while dopamine-secreting pheochromocytoma is rare. We report here a rare case of dopamine-secreting pheochromocytoma in a patient with NF1. A 46-year-old woman with NF1 was referred to our hospital with epigastralgia. The patient had no history of hypertension. Abdominal sonography incidentally revealed a left adrenal tumor, while abdominal computed tomography and magnetic resonance imaging findings showed a left adrenal tumor, sized 63×58 mm. Laboratory evaluations revealed exclusively elevated urine dopamine levels in addition to elevated serum adrenaline and noradrenaline levels. Laparoscopic left adrenalectomy was performed and the dopamine levels and other cathecolamine levels returned to normal postoperatively.
authors.affiliation: The Department of Urology, Hyogo Prefectural Nishinomiya Hospital, Japan.
authors.forename: Shigeaki
authors.initials: S
authors.lastname: Nakazawa
authors.forename: Hidefumi
authors.initials: H
authors.lastname: Kishikawa
authors.forename: Kotaro
authors.initials: K
authors.lastname: Akiyama
authors.forename: Kazuaki
authors.initials: K
authors.lastname: Yamanaka
authors.forename: Toshiaki
authors.initials: T
authors.lastname: Hirai
authors.forename: Kenji
authors.initials: K
authors.lastname: Nishimura
authors.forename: Yasuji
authors.initials: Y
authors.lastname: Ichikawa
mesh_terms: D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000378:metabolism* / Q000601:surgery; D004298:Dopamine / Q000378:metabolism*; D004837:Epinephrine / Q000097:blood; D005260:Female; D006801:Humans; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications*; D009638:Norepinephrine / Q000097:blood; D010673:Pheochromocytoma / Q000150:complications* / Q000378:metabolism* / Q000601:surgery
chemical_list: D004298:Dopamine; D009638:Norepinephrine; D004837:Epinephrine