title: Low-grade fibromyxoid sarcoma of the vulva:  a case report.
abstract: OBJECTIVE
  The study aimed to describe a case of low-grade fibromyxoid sarcoma arising from the vulva and to discuss the diagnostic challenges, clinical management, and epidemiology of this rare malignancy.
  
  
  METHODS
  A 36-year-old woman presented to 3 separate emergency departments with complaints of a painful and slowly enlarging vulvar mass. Eventual gynecologic referral resulted in excision of a 6-cm, noncystic vulvar mass. Pathological diagnosis revealed low-grade fibromyxoid sarcoma. Later, a right radical hemivulvectomy ensured adequate margins, and 2 years later, the patient is free of recurrent and metastatic disease.
  
  
  CONCLUSIONS
  Low-grade fibromyxoid sarcoma is a rare malignancy that may present in the lower genital tract. Definitive diagnosis is essential because low-grade fibromyxoid sarcoma may metastasize many years after diagnosis, thereby requiring indefinite clinical surveillance.
authors.affiliation: Departments of Pathology, Oregon Health and Science University, Portland, OR 97239, USA. vansanda@ohsu.edu
authors.forename: Amanda M
authors.initials: AM
authors.lastname: VanSandt
authors.forename: Joline
authors.initials: J
authors.lastname: Bronson
authors.forename: Catherine
authors.initials: C
authors.lastname: Leclair
authors.forename: Atiya
authors.initials: A
authors.lastname: Mansoor
authors.forename: Martha
authors.initials: M
authors.lastname: Goetsch
mesh_terms: D000328:Adult; D005260:Female; D005350:Fibroma / Q000175:diagnosis* / Q000453:epidemiology / Q000473:pathology* / Q000601:surgery; D006651:Histocytochemistry; D006801:Humans; D008853:Microscopy; D014844:Vulva / Q000473:pathology; D014846:Vulvar Neoplasms / Q000175:diagnosis* / Q000453:epidemiology / Q000473:pathology* / Q000601:surgery