title: Dental treatment in Angelman syndrome patients. 8 case reports.
abstract: OBJECTIVE
  Angelman syndrome is a rare neurogenetic disorder resulting in delayed neuropsychological development,  intellectual disability, speech impairment, movement or balance disorder and a behavioural uniqueness. It is caused by  deletion of maternal chromosome 15q11-13. The syndrome has oral manifestations such as diastemas, tongue thrusting,  sucking/swallowing disorder, mandibular prognathism, and wide mouth. The dental literature on the syndrome is scarce.
  
  
  METHODS
  We report our approach to dental procedures in Angelman syndrome patients, and the relationship between  the dental staff and the patient and his family. The purpose of this paper is to highlight the possibility of dental treatment in  general anaesthesia, due to the lack of cooperation of some of these patients.
authors.affiliation: Department of Community Dentistry, Piove di Sacco Hospital, ULSS 16 Padua, Italy. claudio.gallo@sanita.padova.it
authors.forename: C
authors.initials: C
authors.lastname: Gallo
authors.forename: A
authors.initials: A
authors.lastname: Marcato
authors.forename: M
authors.initials: M
authors.lastname: Beghetto
authors.forename: E
authors.initials: E
authors.lastname: Stellini
mesh_terms: D017204:Angelman Syndrome / Q000150:complications*; D002648:Child; D019140:Dental Care for Children; D017742:Dental Care for Chronically Ill; D003777:Dental Prophylaxis / Q000379:methods; D003793:Dental Restoration, Permanent / Q000379:methods; D005247:Feeding Behavior; D005260:Female; D006801:Humans; D008297:Male; D009910:Oral Hygiene; D010353:Patient Education as Topic; D014081:Tooth Extraction / Q000379:methods