title: Mondini dysplasia presenting as otorrhea without meningitis.
abstract: Mondini dysplasia is a rare inner ear malformation that is usually only diagnosed after recurrent meningitis. Surgical intervention is mandatory. This report highlights the case of a patient with Mondini dysplasia who presented with hearing impairment and otorrhea and was diagnosed and treated before the occurrence of meningitis, thus preventing morbidity and neurologic sequelae. Hearing impairment may be the only manifestation of Mondini dysplasia, and the benefit of hearing screening is emphasized. Temporal bone computed tomography should be considered in children with unilateral sensorineural or mixed-type hearing impairment.
authors.affiliation: Department of Pediatrics, Mackay Memorial Hospital, Hsin Chu Branch, Taiwan.
authors.forename: Chien-Yu
authors.initials: CY
authors.lastname: Lin
authors.forename: Hung-Ching
authors.initials: HC
authors.lastname: Lin
authors.forename: Chun-Chih
authors.initials: CC
authors.lastname: Peng
authors.forename: Kuo-Sheng
authors.initials: KS
authors.lastname: Lee
authors.forename: Nan-Chang
authors.initials: NC
authors.lastname: Chiu
mesh_terms: D002558:Cerebrospinal Fluid Otorrhea / Q000209:etiology*; D007758:Ear, Inner / Q000002:abnormalities*; D005260:Female; D034381:Hearing Loss / Q000209:etiology; D006801:Humans; D007223:Infant; D008581:Meningitis / Q000209:etiology