title: Thoracic computed tomography in absent pulmonary valve syndrome management.
abstract: A neonate with absent pulmonary valve syndrome (APVS) and features of tetralogy of Fallot presented respiratory distress. The prolonged need for mechanical ventilation was an indication for surgical repair. Preoperative thoracic CT imaging showed nearly complete closure of the distal trachea, compressed by the aneurysmal dilatation of the pulmonary arteries, and its reopening after ventilator pressure was increased. Management of APVS may require high-pressure ventilation to prevent bronchial collapse due to compression by the pulmonary arteries. In this context, thoracic CT imaging is very useful for adjusting ventilation support so that surgical repair can be performed in optimal conditions.
authors.affiliation: Neonatal Intensive Care Unit, Arnaud de Villeneuve Hospital, Montpellier, France.
authors.forename: Marie
authors.initials: M
authors.lastname: Vincenti
authors.forename: Aurélien
authors.initials: A
authors.lastname: Jacquot
authors.forename: Sophie
authors.initials: S
authors.lastname: Guillaumont
authors.forename: Christophe
authors.initials: C
authors.lastname: Milési
authors.forename: Magali
authors.initials: M
authors.lastname: Saguintaah
authors.forename: Odile
authors.initials: O
authors.lastname: Pidoux
authors.forename: Bernard
authors.initials: B
authors.lastname: Kreitmann
authors.forename: Aline
authors.initials: A
authors.lastname: Rideau
authors.forename: Gilles
authors.initials: G
authors.lastname: Cambonie
mesh_terms: D003937:Diagnosis, Differential; D006330:Heart Defects, Congenital / Q000000981:diagnostic imaging*; D006349:Heart Valve Diseases / Q000151:congenital / Q000000981:diagnostic imaging*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011664:Pulmonary Valve / Q000002:abnormalities*; D013902:Radiography, Thoracic; D013577:Syndrome; D014057:Tomography, X-Ray Computed / Q000379:methods*