title: Incidentally detected cholangiocarcinoma in an explanted liver with biliary atresia after Kasai operation.
abstract: This report presents the case of a 30-yr-old woman with BA who developed incidental cholangiocarcinoma following the Kasai operation. She showed progressive liver dysfunction and cirrhosis at the age of 30 yr and underwent LDLT. A 4-cm-diameter liver tumor in the anastomotic site of portoenterostomy was incidentally found as a result of a pathological examination of the explanted native liver. The tumor was pathologically diagnosed to be intrahepatic cholangiocarcinoma. Although cholangiocarcinoma in patients with BA has been previously reported in only three cases, it should be nevertheless always considered in the differential diagnosis of hepatic tumors during a long follow-up course in patients with BA.
authors.affiliation: Division of Transplant Surgery, National Center for Child Health and Development, Setagaya-ku, Tokyo, Japan. fukuda-a@ncchd.go.jp
authors.forename: Akinari
authors.initials: A
authors.lastname: Fukuda
authors.forename: Seisuke
authors.initials: S
authors.lastname: Sakamoto
authors.forename: Hiroyuki
authors.initials: H
authors.lastname: Kanazawa
authors.forename: Takanobu
authors.initials: T
authors.lastname: Shigeta
authors.forename: Chiaki
authors.initials: C
authors.lastname: Karaki
authors.forename: Ikumi
authors.initials: I
authors.lastname: Hamano
authors.forename: Hajime
authors.initials: H
authors.lastname: Uchida
authors.forename: Hiroaki
authors.initials: H
authors.lastname: Kitagawa
authors.forename: Chiaki
authors.initials: C
authors.lastname: Okuse
authors.forename: Osamu
authors.initials: O
authors.lastname: Miyazaki
authors.forename: Shunsuke
authors.initials: S
authors.lastname: Nosaka
authors.forename: Atsuko
authors.initials: A
authors.lastname: Nakazawa
authors.forename: Mureo
authors.initials: M
authors.lastname: Kasahara
mesh_terms: D000328:Adult; D001650:Bile Duct Neoplasms / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery; D001653:Bile Ducts, Intrahepatic; D001656:Biliary Atresia / Q000150:complications / Q000601:surgery*; D018281:Cholangiocarcinoma / Q000175:diagnosis* / Q000209:etiology / Q000601:surgery; D005260:Female; D006498:Hepatectomy; D006801:Humans; D033162:Incidental Findings; D016031:Liver Transplantation; D011171:Portoenterostomy, Hepatic; D012086:Reoperation