title: An unexpected diagnosis in a dyspnoeic patient with primary Sjogren syndrome.
abstract: We describe a case of a 50-year-old lady with newly diagnosed primary Sjogren syndrome who presented with severe pulmonary artery hypertension and pericardial effusion. She was managed by immunosuppressive agents and a combination of standard therapy for pulmonary hypertension. Our patient had a clinically significant involvement of cardio-pulmonary system that is atypical of this disease. Prompt recognition and management of this condition are extremely crucial as untreated cases carry a grave prognosis. However, the ideal treatment strategy is yet to be defined for this condition.
authors: Department of Cardiology, Rashid Hospital, Dubai Health Authority, Dubai, United Arab Emirates. rajani_ali@hotmail.com
authors: Ali Raza
authors: AR
authors: Rajani
authors: Kosar
authors: K
authors: Hussain
authors: Fahad Omar
authors: FO
authors: Baslaib
authors: Kabad N S
authors: KN
authors: Rao
mesh_terms: D003937:Diagnosis, Differential; D004417:Dyspnea / Q000175:diagnosis / Q000209:etiology*; D004452:Echocardiography; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications* / Q000175:diagnosis; D008875:Middle Aged; D010490:Pericardial Effusion / Q000150:complications* / Q000175:diagnosis; D012859:Sjogren's Syndrome / Q000150:complications* / Q000175:diagnosis; D014057:Tomography, X-Ray Computed