title: Von Hippel Lindau disease [VHL]: magnetic resonance imaging spectrum in a single patient.
abstract: In this case, we describe the wide magnetic resonance imaging (MRI) spectrum in a single patient who had multi organ involvement. Von Hippel Lindau Disease is a rare inherited autosomal dominant disorder characterized by development of benign and malignant lesions involving multiple organs.  Imaging plays a vital role in the diagnosis and surveillance of VHL as it can differentiate benign from malignant lesions. The median life expectancy of VHL is 49 years and the commonest cause of death in patients with VHL is renal cell carcinoma and neurologic complication from cerebellar hemangioblastomas.
authors: Department of Radiology, B Y L Nair Charitable Hospital and T N Medical College, Dr A R Nair Road, Mumbai Central, Mumbai, Maharashtra, India-400008. drsandeepjakhere@gmail.com
authors: Sandeep G
authors: SG
authors: Jakhere
authors: Bhakti
authors: B
authors: Yeragi
authors: Darshan G
authors: DG
authors: Jain
mesh_terms: D000328:Adult; D002528:Cerebellar Neoplasms / Q000473:pathology; D018325:Hemangioblastoma / Q000473:pathology; D006801:Humans; D052177:Kidney Diseases, Cystic / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D010181:Pancreatic Cyst / Q000473:pathology; D013120:Spinal Cord Neoplasms / Q000473:pathology; D006623:von Hippel-Lindau Disease / Q000473:pathology*