title: A rare case of accessory maxilla and bilateral Tessier no. 7 clefts, a 10-year follow-up.
abstract: A Tessier no. 7 cleft is a lateral facial cleft which originates from the oral cavity and extends towards the tragus, involving both soft-tissue and skeletal components. A male patient presenting with both maxillary jaw duplication and bilateral Tessier no. 7 clefts, which has been reported only twice in the literature, is described. Bilateral facial clefts, macrostomia and chondro-cutaneous remnants were noted, which were repaired and resected. With further growth, facial asymmetry and asymmetric facial nerve dysfunction became apparent. Radiographic examination showed an accessory maxillary jaw and a flattened and hypoplastic right coronoid process. A maxillary alveolar cleft was also present between the left second bicuspid and the second permanent molar. This case may represent an under-recognized phenotype with an unusual combination of maxillary jaw duplication, macrostomia, Tessier no. 7 clefts, and chondro-cutaneous remnants. A long-term follow-up of these patients is recommended as they often develop craniofacial deformities later in life.
authors: Warwick Dentistry, Warwick Medical School, University of Warwick, Coventry, UK.
authors: Ali
authors: A
authors: Borzabadi-Farahani
authors: Stephen L-K
authors: SL
authors: Yen
authors: Cameron
authors: C
authors: Francis
authors: Pedro A
authors: PA
authors: Lara-Sanchez
authors: Jeffrey
authors: J
authors: Hammoudeh
mesh_terms: D000293:Adolescent; D000539:Alveolar Process / Q000002:abnormalities*; D019465:Craniofacial Abnormalities / Q000175:diagnosis*; D005064:Eustachian Tube / Q000002:abnormalities; D005146:Facial Asymmetry / Q000175:diagnosis; D006801:Humans; D008265:Macrostomia / Q000175:diagnosis*; D008297:Male; D008312:Malocclusion, Angle Class II / Q000175:diagnosis; D008437:Maxilla / Q000002:abnormalities*; D015050:Zygoma / Q000002:abnormalities
keywords: Accessory maxilla; Bilateral Tessier no. 7 cleft; Macrostomia; Maxillary duplication