Multidisciplinary staged surgical management of bifrontal meningoencephalocele with long-term follow-up.
The authors report on an infant with a bifrontal encephalocele that was associated with multisuture craniosynostosis, spasticity, and a progressively severe epilepsy. They describe the initial presentation, genetic screening results, staged multidisciplinary operative plans, clinical course, complications, and long-term surgical and developmental follow-up. To their knowledge, the comprehensive surgical management of this type of complicated congenital cranial anomaly has not been previously described. Surgical management was staged and multidisciplinary and required careful attention to all 3 components of the condition: 1) hydrocephalus, 2) frontal meningoencephalocele, and 3) epilepsy.
Divisions of Neurosurgery, Children's of Alabama, University of Alabama at Birmingham, Alabama 35233, USA. jeffrey.blount@childrensal.org
Jeffrey P
JP
Blount
Amber S
AS
Gordon
Paul M
PM
Foreman
John H
JH
Grant
D003398:Craniosynostoses / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D004677:Encephalocele / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D004827:Epilepsy / Q000175:diagnosis / Q000209:etiology / Q000517:prevention & control; D006801:Humans; D006849:Hydrocephalus / Q000175:diagnosis / Q000209:etiology / Q000517:prevention & control; D007231:Infant, Newborn; D008297:Male; D008588:Meningocele / Q000150:complications / Q000175:diagnosis / Q000601:surgery*