Primary Ewings sarcoma of cavernous sinus in an infant: a case report and review of literature.
Ewing's / peripheral primitive neuroectodermal tumor (pPNET) of the cavernous     sinus are extremely uncommon. We present clinical, radiological, pathological     findings of Ewing's / pPNET involving the cavernous sinus in an eleven-month-old     infant presenting with proptosis and 6th nerve palsy. MRI Contrast scans showed     a well-defined, homogenously enhancing mass involving the right cavernous sinus     location. Histopathology and immunohistochemical features were consistent with     Ewing's/pPNET. The patient succumbed to disease in spite of starting     chemotherapy. The clinical, radiological and pathological findings of previously     reported cases of Ewing's sarcoma / pPNET involving the cavernous sinus are     summarized. The histological differential diagnosis of primary intracranial     Ewing's sarcoma / pPNET are discussed.
Nizam's Institute of Medical Sciences, Department of Neurosurgery, Hyderabad, India.
Mohana Rao
MR
Patibandla
Shantveer G
SG
Uppin
Amit Kumar
AK
Thotakura
Manas K
MK
Panigrahi
Sundaram
S
Challa
D001859:Bone Neoplasms / Q000473:pathology*; D002426:Cavernous Sinus / Q000473:pathology*; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007223:Infant; D008279:Magnetic Resonance Imaging; D008297:Male; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000473:pathology*; D012512:Sarcoma, Ewing / Q000473:pathology*