Supracardiac total anomalous pulmonary venous connection with bilateral (right and left) vertical veins and bilateral obstruction.
This report describes a rare form of obstructed supracardiac total anomalous pulmonary venous connection with two vertical veins (right and left) draining the right- and the left-sided pulmonary veins respectively without formation of a common chamber and with bilateral obstruction. Surgery for these patients is technically challenging due to the absence of a common chamber, and the prognosis is worse than for patients with a common chamber. Also, it is important to be aware of this entity so that an accurate noninvasive preoperative diagnosis by echocardiography alone without invasive cardiac catheterization is possible. This facilitates emergency surgical repair without delay, which is crucial to improvement of the outcome.
Department of Cardiology, KEM Hospital, Room No 403, 4th Floor, CVTC Building, Acharya Donde Marg, Parel, Mumbai, 400012, India, seemasaregamasmailbox@rediffmail.com.
Seema A
SA
Gavali
Milind S
MS
Phadke
Prafulla G
PG
Kerkar
D006328:Cardiac Catheterization; D006348:Cardiac Surgical Procedures / Q000379:methods; D003937:Diagnosis, Differential; D015150:Echocardiography, Doppler / Q000379:methods*; D017809:Fatal Outcome; D006801:Humans; D007231:Infant, Newborn; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging* / Q000601:surgery