The peripartum management of a patient with glutaric aciduria type 1.
The management of cesarean delivery for a parturient with placenta previa at 36 weeks' gestation and glutaric aciduria type 1 is presented. The management goal was to prevent encephalopathic crisis by ensuring adequate caloric intake with dextrose infusion and to provide carnitine supplementation and adequate anesthesia.
Department of Anesthesiology, Duke University Health System, Durham, NC 27710, USA. Unyime-Ituk@Uiowa.edu
Unyime S
US
Ituk
Terrence K
TK
Allen
Ashraf S
AS
Habib
D000592:Amino Acid Metabolism, Inborn Errors / Q000628:therapy*; D000773:Anesthesia, Obstetrical / Q000379:methods; D000775:Anesthesia, Spinal / Q000379:methods; D001928:Brain Diseases, Metabolic / Q000628:therapy*; D002331:Carnitine / Q000627:therapeutic use; D002585:Cesarean Section; D005260:Female; D005947:Glucose / Q000008:administration & dosage; D050770:Glutaryl-CoA Dehydrogenase / Q000172:deficiency; D006801:Humans; D007262:Infusions, Intravenous; D019990:Perioperative Care / Q000379:methods; D010923:Placenta Previa / Q000601:surgery; D011247:Pregnancy; D011248:Pregnancy Complications / Q000628:therapy*; D011295:Prenatal Care / Q000379:methods*; D014803:Vitamin B Complex / Q000627:therapeutic use; D055815:Young Adult
D014803:Vitamin B Complex; D050770:Glutaryl-CoA Dehydrogenase; D005947:Glucose; D002331:Carnitine