Combination of left ventricular noncompaction and partial atrioventricular canal defect in a 21-year-old male: a case report.
BACKGROUND
Left ventricular noncompaction (LVNC) is classified as a genetic cardiomyopathy characterized by a progressive systolic dysfunction. It may occur alone or in association with congenital cardiac anomalies. The combination of left ventricular noncompaction with partial atrioventricular canal defect is rare and has not, to our knowledge, been described previously.


METHODS
A 21-year-old male who traveled to our center from a neighboring country presented with signs of heart failure. Transthorarcic echocardiography showed prominent trabeculations in the left ventricle predominantly in the left ventricle involving the apical lateral and mid anterolateral segments associated with a partial atrioventricular canal defect. There was a biventricular systolic dysfunction. There was good response to medical treatment.


CONCLUSIONS
This case stresses the importance of maintaining a high degree of suspicion for this rare cardiomyopathy and the need to systematically look for other associated anomalies in order to institute proper short- and long-term managements.
Department of Cardiology, Aristide Le Dantec Teaching Hospital, Dakar, Senegal.
Malick
M
Bodian
Modou
M
Jobe
Mohamed
M
Lèye
Mouhamadou Bamba
MB
Ndiaye
Adama
A
Kane
Simon Antoine
SA
Sarr
Alassane
A
Mbaye
Maboury
M
Diao
Fatimata Gatta
FG
Ba
Aliou Alassane
AA
Ngaïde
Sarah Mouna
SM
Coly
Anna
A
Thiam
Moustapha
M
Sarr
Serigne Abdou
SA
Bâ
atrioventricular canal defect; left ventricular; noncompaction