[Malignant rhabdoid tumor of the orbit].
Malignant rhabdoid tumor is a rare and malignant tumor of childhood. Generally     it originates from the kidney and central nervous system, but occasionally it     may arise from the orbit. Differential diagnosis from other childhood soft     tissue sarcomas should be done. We report here an 8-week-old female infant with     malignant rhabdoid tumor of the orbit who was treated with chemotherapy and     surgery. The 8 week-old girl was referred to our hospital with a history of     right proptosis first noted at birth. Physical and laboratory evaluation of the     patient was normal except for right proptosis. The mass was removed surgically.     Histopathologic examination and immunohistochemical findings of the specimen     were evaluated as malignant rhabdoid tumor. Chemotherapy was administered. While     in clinical remission, she succumbed during a febrile episode. Malignant     rhabdoid tumor can rarely originate from the orbit. Malignant rhabdoid tumor     should be kept in mind in the differential diagnosis of orbital masses, and     surgery, chemotherapy and local radiotherapy should be used as combined therapy     due to the poor prognosis.
İstanbul Üniversitesi, Cerrahpaşa Tıp Fakültesi, Pediatrik Hematoloji-Onkoloji, Anabilim Dalı, İstanbul, Türkiye. drkaramans@yahoo.com
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D003131:Combined Modality Therapy; D003937:Diagnosis, Differential; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D007223:Infant; D009918:Orbital Neoplasms / Q000175:diagnosis* / Q000628:therapy; D011379:Prognosis; D018335:Rhabdoid Tumor / Q000175:diagnosis* / Q000628:therapy