title: Crouzon syndrome: clinico-radiological illustration of a case.
abstract: Crouzon syndrome, also called craniofacial dysostosis, is an autosomal dominant disorder with complete penetrance and variable expressivity. Described by a French neurosurgeon in 1912, it is a rare genetic disorder characterized by premature closure of cranial sutures, midfacial hypoplasia, and orbital defects. Here, we report a case of this rare entity. The patient presented with brachycephaly, maxillary hypoplasia, exophthalmos, mandibular prognathism, along with dental and orbital abnormalities.
authors: Department of Oral Medicine Diagnosis and Radiology, Kothiwal Dental College and Research Centre, Mora Mustaqueem, Moradabad, Uttar Pradesh, India.
authors: Raviprakash Sasankoti
authors: RS
authors: Mohan
authors: Naveen Shanker
authors: NS
authors: Vemanna
authors: Sankalp
authors: S
authors: Verma
authors: Neha
authors: N
authors: Agarwal
keywords: Craniofacial dysostosis; copper beaten appearance; crouzon syndrome; exophthalmos
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