title: [Fronto-ethmoidal fibrous dysplasia: a case-report].
abstract: OBJECTIVE
  Fibrous dysplasia is a congenital bone disease, where normal bone is replaced by a fibrous-like tissue with immature osteogenesis. The cephalic extremity is affected in one out of three cases. The aim of this study was to describe a case of fibrous dysplasia and review workup and management of this pathology.
  
  
  METHODS
  We reviewed relevant publications using the Medline database and presented a case of isolated paranasal sinus fibrous dysplasia to illustrate this disease.
  
  
  RESULTS
  The clinical onset was headache and left palpebral oedema in a twelve-year old. Imaging showed a left fronto-ethmoidal bone lesion with epidural empyema. No other radiological anomaly or phosphor-calcic disorder was present. The clinical course was positive using intravenous antibiotics, with a two-year follow-up.
  
  
  CONCLUSIONS
  Fibrous dysplasia is diagnosed using CT-scan, without the need for histologic confirmation in most cases. Initial workup includes axial skeleton X-rays and hormonal dosages. The efficiency of biphosphonates drugs has significally reduced the number of surgical procedures.
  
  
  CONCLUSIONS
  Fibrous dysplasia is often a multifocal disease and should be treated medically first. Management requires a multi-disciplinary team.
authors: CHU A. Michallon, Clinique ORL, Pôle Tête et Cou et Chirurgie Réparatrice, 38043 Grenoble cedex 9, France.
authors: F
authors: F
authors: Hoareau-Gruchet
authors: M
authors: M
authors: Nils
authors: L
authors: L
authors: Spinato
authors: M
authors: M
authors: Rabeyrin
authors: C A
authors: CA
authors: Righini
mesh_terms: D002648:Child; D004487:Edema / Q000175:diagnosis / Q000209:etiology; D005004:Ethmoid Bone / Q000000981:diagnostic imaging / Q000473:pathology*; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging / Q000473:pathology; D005358:Fibrous Dysplasia, Monostotic; D005624:Frontal Bone / Q000000981:diagnostic imaging / Q000473:pathology*; D006261:Headache / Q000175:diagnosis / Q000209:etiology; D006801:Humans; D014057:Tomography, X-Ray Computed