title: Third Åland islands conference on von Willebrand disease, 26-28 September 2012: meeting report.
abstract: The first meeting of international specialists in the field of von Willebrand disease (VWD) was held in the Åland islands in 1998 where Erik von Willebrand had first observed a bleeding disorder in some members of a family from Föglö and a summary of the meeting was published in 1999. The second meeting was held in 2010 and a report of the meeting was published in 2012. Topics covered included progress in understanding of VWD over the last 50 years; multimers; classification of VWD; pharmacokinetics and laboratory assays; genetics; treating the paediatric patient; prophylaxis; geriatrics; gene therapy and treatment guidelines. This third meeting held over 3 days covered the structure and function of von Willebrand factor (VWF); type 1 VWD, the most common form of the disease; a lifespan of pharmacokinetics in VWD; detecting inhibitors in VWD patients; and special challenges in understanding and treating the female VWD patient.
authors: Department of Hematology and Coagulation Disorders, Lund University, Skåne University Hospital, Malmö, Sweden. erik.berntorp@med.lu.se
authors: E
authors: E
authors: Berntorp
authors: B
authors: B
authors: Fuchs
authors: M
authors: M
authors: Makris
authors: R
authors: R
authors: Montgomery
authors: V
authors: V
authors: Flood
authors: J S
authors: JS
authors: O'Donnell
authors: A B
authors: AB
authors: Federici
authors: D
authors: D
authors: Lillicrap
authors: P
authors: P
authors: James
authors: U
authors: U
authors: Budde
authors: M
authors: M
authors: Morfini
authors: P
authors: P
authors: Petrini
authors: S
authors: S
authors: Austin
authors: C
authors: C
authors: Kannicht
authors: V
authors: V
authors: Jiménez-Yuste
authors: C
authors: C
authors: Lee
mesh_terms: D000818:Animals; D005169:Factor VIII / Q000378:metabolism; D005260:Female; D006801:Humans; D014842:von Willebrand Diseases / Q000175:diagnosis* / Q000235:genetics / Q000378:metabolism / Q000628:therapy*; D014841:von Willebrand Factor / Q000378:metabolism
chemical_list: D014841:von Willebrand Factor; D005169:Factor VIII
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