title: Cardiac resynchronisation therapy associated with pulmonary artery banding in an adult with severe right ventricular dysfunction after Mustard repair for complete transposition of the great arteries: results after 2 years of follow-up.
abstract: Late dysfunction of the systemic right ventricle in patients with complete transposition of the great arteries after Mustard or Senning procedures and progressive deterioration of the clinical status has been demonstrated. However, evidence-based data on the effective therapy for systemic right ventricular dysfunction in these patients are yet to be defined. Our patient shows an improvement in the right ventricular systolic function, with a reduction in tricuspid regurgitation and a consequent better exercise tolerance after a hybrid approach consisting of an upgrading of a previous transvenous-implanted dual-chamber Implantable Cardiac Defibrillator to biventricular pacing associated with pulmonary artery banding via an anterior thoracotomy.
authors: 1 Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy.
authors: Luca
authors: L
authors: Donazzan
authors: 2 Pediatric and Congenital Cardiac Surgical Unit, University of Padua, Padua, Italy.
authors: Giovanni
authors: G
authors: Stellin
authors: 1 Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy.
authors: Werner Guenther
authors: WG
authors: Rauhe
authors: 3 Department of Pneumology, San Maurizio Regional Hospital, Bolzano, Italy.
authors: Lucio
authors: L
authors: Bonazza
authors: 4 Service of Radiology, San Maurizio Regional Hospital, Bolzano, Italy.
authors: Josef
authors: J
authors: Stuefer
authors: 1 Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy.
authors: Cristina
authors: C
authors: Romeo
authors: 1 Department of Cardiology, San Maurizio Regional Hospital, Bolzano, Italy.
authors: Roberto
authors: R
authors: Crepaz
mesh_terms: D000328:Adult; D016757:Death, Sudden, Cardiac / Q000517:prevention & control*; D017147:Defibrillators, Implantable; D015150:Echocardiography, Doppler; D006801:Humans; D019028:Magnetic Resonance Imaging, Cine; D008297:Male; D011651:Pulmonary Artery / Q000601:surgery*; D012720:Severity of Illness Index; D014188:Transposition of Great Vessels / Q000150:complications / Q000601:surgery*; D016896:Treatment Outcome; D014262:Tricuspid Valve Insufficiency / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D018497:Ventricular Dysfunction, Right / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*