title: Congenital ectropion uveae presenting as acute glaucoma in a 3-year-old child.
abstract: Congenital ectropion uveae is a rare anomaly commonly associated with neurofibromatosis and occasionally with other ocular abnormalities. Glaucoma related with this condition may be present in infancy, or may develop later in life, and is thought to be due to an associated angle dysgenesis. Diagnosis is frequently delayed due to the subtle signs and the absence of symptoms and management is primarily surgical. We report an unusual case of unilateral congenital ectropion uveae in a 3-year-old child, with no evidence of neurofibromatosis, presenting as acute glaucoma, which was successfully managed by topical treatment only, avoiding surgical intervention.
authors: 1st Department of Ophthalmology, Aristotle University of Thessaloniki, AHEPA Hospital, 3 Pl. Ippodromiou Street, 54621, Thessaloniki, Greece.
authors: N G
authors: NG
authors: Ziakas
authors: A
authors: A
authors: Chranioti
authors: A
authors: A
authors: Malamas
authors: O
authors: O
authors: Leliopoulou
authors: A
authors: A
authors: Mataftsi
mesh_terms: D000208:Acute Disease; D002675:Child, Preschool; D004483:Ectropion / Q000151:congenital*; D005901:Glaucoma / Q000175:diagnosis*; D006801:Humans; D007498:Iris / Q000002:abnormalities; D008297:Male; D010857:Pigment Epithelium of Eye / Q000002:abnormalities; D014602:Uvea / Q000002:abnormalities*
references: Ophthalmic Surg Lasers. 1999 Jul-Aug;30(7):567-70
references: 10929982
references: J Pediatr Ophthalmol Strabismus. 2009 Jan-Feb;46(1):35-7
references: 19213275
references: Ophthalmology. 1985 Jul;92(7):912-21
references: 4022577
references: Ophthalmology. 1984 Apr;91(4):326-31
references: 6425761