title: Congenital portosystemic venous shunt in a preterm Rh-isoimmunized infant.
abstract: The authors report a preterm infant with Rh-isoimmunization, who had persistent hepato-splenomegaly with conjugated hyperbilirubinemia, transaminitis, and hyperammonemia. Ultrasound abdomen revealed an intrahepatic portosystemic venous shunt (PSVS). The child was managed conservatively. On follow up at 2.4 y of age, the child is having normal growth and development, but with persisting shunt. Severe Rh-isoimmunisation in a neonate can sometimes share some of the features of congenital PSVS and delay the diagnosis of the latter. The index case had shunt ratio >80 % during the neonatal period but did not require any intervention.
authors: Division of Neonatology, Department of Pediatrics, All India Institute of Medical Sciences, Newborn Health Knowledge Centre, WHO Collaborating Centre for Training and Research in Neonatal Care, ICMR Centre for Advanced Research in Newborn Health, New Delhi, India.
authors: Anu
authors: A
authors: Thukral
authors: Kamaldeep
authors: K
authors: Arora
authors: Rashmi Ranjan
authors: RR
authors: Das
authors: Arundeep
authors: A
authors: Arora
authors: Shivanand
authors: S
authors: Gamanagatti
authors: Ramesh K
authors: RK
authors: Agarwal
mesh_terms: D002675:Child, Preschool; D006801:Humans; D007234:Infant, Premature; D008297:Male; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D012203:Rh Isoimmunization; D014463:Ultrasonography; D054079:Vascular Malformations / Q000150:complications / Q000000981:diagnostic imaging
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