title: Fluorescein angiography findings in phacomatosis pigmentovascularis.
abstract: The authors report the fluorescein angiography findings in a 3-month-old patient with phacomatosis cesioflammea, which revealed venous-venous anastomoses in addition to previously undescribed features of peripheral retinal vascular nonperfusion. The authors encourage physicians to consider phacomatosis pigmentovascularis in the differential diagnosis of patients presenting with facial port-wine stain and to screen these patients for peripheral retinal avascularity in addition to glaucoma and primary uveal melanoma.
authors: Bascom Palmer Eye Institute, Department of Ophthalmology, University of Miami Miller School of Medicine, Miami, FL 33136, USA. chenry2@med.miami.edu
authors: Christopher R
authors: CR
authors: Henry
authors: Elizabeth
authors: E
authors: Hodapp
authors: Ditte J
authors: DJ
authors: Hess
authors: Lauren S
authors: LS
authors: Blieden
authors: Audina M
authors: AM
authors: Berrocal
mesh_terms: D002830:Choroid Neoplasms / Q000473:pathology*; D005260:Female; D005451:Fluorescein Angiography; D006391:Hemangioma / Q000473:pathology*; D006801:Humans; D007223:Infant; D020752:Neurocutaneous Syndromes / Q000175:diagnosis*; D019339:Port-Wine Stain / Q000175:diagnosis*; D012169:Retinal Vein / Q000002:abnormalities*; D016157:Vascular Fistula / Q000175:diagnosis*; D014792:Visual Acuity