title: Dental Findings and Management in a Mucopolysaccharidosis Type IIIB Patient.
abstract: Mucopolysaccharidosis type IIIB (MPS IIIB) is an autosomal recessive disorder caused by deficiency of the lysosomal enzyme a-N-acetylglucosaminidase. Affected subjects present developmental delay, attention deficit disorder, uncontrollable hyperactivity, and aggressive behavior, followed  by progressive dementia and death in late adolescence. The purpose of this paper is to report the dental findings and treatment in a child with MPS IIIB. His primary molars and permanent mandibular incisors presented obliterated pulp chambers and root canals, which may be a clinical manifestation  of this disorder.
authors: School of Dentistry, University of São Paulo at Ribeirão Preto, Brazil.
authors: Talitha de Siqueira
authors: Tde S
authors: Mellara
authors: Danielle Torres
authors: DT
authors: Azevedo
authors: Gisele
authors: G
authors: Faria
authors: Paulo
authors: P
authors: Nelson Filho
authors: Alexandra Mussolino de
authors: AM
authors: Queiroz
authors: Luiz Guilherme
authors: LG
authors: Brentegani
mesh_terms: D002648:Child; D003730:Dental Care for Persons with Disabilities; D003731:Dental Caries / Q000175:diagnosis / Q000628:therapy; D003786:Dental Pulp Cavity / Q000002:abnormalities; D003803:Dentigerous Cyst / Q000000981:diagnostic imaging; D005500:Follow-Up Studies; D006801:Humans; D007180:Incisor / Q000002:abnormalities; D008297:Male; D008336:Mandibular Diseases / Q000000981:diagnostic imaging; D008963:Molar / Q000002:abnormalities; D008964:Molar, Third / Q000002:abnormalities; D009084:Mucopolysaccharidosis III / Q000473:pathology*; D011859:Radiography; D014076:Tooth Diseases / Q000175:diagnosis* / Q000628:therapy; D014083:Tooth Germ / Q000002:abnormalities; D014094:Tooth, Deciduous / Q000002:abnormalities