title: Management of aortic aneurysms in patients with connective tissue disease.
abstract: Acute dissection and rupture of aortic aneurysms comprise for 1-2% of all deaths in developed countries. Dilation of the aorta is caused by several different mechanisms including inherited disorders of connective tissue. Recent reports estimate that 20% of patients presenting with thoracic aortic disease do have an underlying genetic basis of disease.
authors: Department of Cardiovascular Surgery, University Hospital Berne, Berne, Switzerland.
authors: F
authors: F
authors: Schoenhoff
authors: J
authors: J
authors: Schmidli
authors: M
authors: M
authors: Czerny
authors: T P
authors: TP
authors: Carrel
mesh_terms: D000328:Adult; D000368:Aged; D001014:Aortic Aneurysm / Q000000981:diagnostic imaging / Q000235:genetics / Q000601:surgery*; D001027:Aortography / Q000379:methods; D019917:Blood Vessel Prosthesis Implantation / Q000009:adverse effects; D003240:Connective Tissue Diseases / Q000150:complications* / Q000175:diagnosis / Q000235:genetics; D004535:Ehlers-Danlos Syndrome / Q000150:complications; D057510:Endovascular Procedures / Q000009:adverse effects; D005260:Female; D020022:Genetic Predisposition to Disease; D006801:Humans; D055947:Loeys-Dietz Syndrome / Q000150:complications; D008297:Male; D008382:Marfan Syndrome / Q000150:complications; D008875:Middle Aged; D018579:Patient Selection; D010641:Phenotype; D011247:Pregnancy; D018570:Risk Assessment; D012307:Risk Factors; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome