title: Isolated interrupted aortic arch in an 18-year-old man.
abstract: Isolated interrupted aortic arch, a congenital malformation, is very rarely reported in adults. Most adult patients have presented with type A interruption (interruption just beyond the left subclavian artery) and without an associated ventricular septal defect. Conventional surgical repair is typically a challenge because of the extent of collateral circulation in patients who have survived to adulthood. We describe the successful, single-staged, extra-anatomic ventral aortic repair of type A interrupted aortic arch in an 18-year-old man, and we discuss the pathogenesis of the so-called adult form of the condition.
authors: Department of Cardiothoracic & Vascular Surgery, Postgraduate Institute of Medical Education & Research and Dr Ram Manohar Lohia Hospital, New Delhi 110001, India. shyamadeep1976@gmail.com
authors: Shyamadeep
authors: S
authors: Borgohain
authors: Anubhav
authors: A
authors: Gupta
authors: Vijay
authors: V
authors: Grover
authors: Vijay Kumar
authors: VK
authors: Gupta
mesh_terms: D000293:Adolescent; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery; D001027:Aortography / Q000379:methods; D019917:Blood Vessel Prosthesis Implantation; D003097:Collateral Circulation; D006801:Humans; D008297:Male; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome; D054079:Vascular Malformations / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery
keywords: Anastomosis, surgical; aorta, thoracic/abnormalities/surgery; collateral circulation; heart defects, congenital/complications; treatment outcome