title: Generalized lymphatic malformation with chylothorax: long-term management of a highly morbid condition in a pediatric patient.
abstract: Generalized lymphatic malformation (GLM) often causes chylothorax, which can be a highly morbid condition. Chylothorax in a pediatric patient with a lymphangiogenic disorder may be especially resistant to therapy, requiring more aggressive measures. We discuss the complex ongoing long-term management of a pediatric patient with GLM who presented with massive, persistent left chylothorax, which resolved by surgical ligation of the thoracic duct and medical management.
authors.affiliation: Department of Pediatric General and Thoracic Surgery, Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.
authors.forename: Wendy
authors.initials: W
authors.lastname: Chen
authors.forename: Denise
authors.initials: D
authors.lastname: Adams
authors.forename: Manish
authors.initials: M
authors.lastname: Patel
authors.forename: Anita
authors.initials: A
authors.lastname: Gupta
authors.forename: Roshni
authors.initials: R
authors.lastname: Dasgupta
mesh_terms: D000293:Adolescent; D002916:Chylothorax / Q000209:etiology* / Q000628:therapy*; D005260:Female; D006801:Humans; D044148:Lymphatic Abnormalities / Q000150:complications*; D013997:Time Factors