title: Combined Bentall and modified Ravitch procedures in a patient with Marfan syndrome.
abstract: Marfan syndrome is an inherited, connective-tissue disorder transmitted as an autosomal dominant trait. Cardinal features of the disorder include tall stature, ectopia lentis, mitral valve prolapse, aortic root dilatation, and aortic dissection. Pectus excavatum may exist as an isolated lesion or in association with a genetic syndrome such as Marfan syndrome. We report the successful management of a simultaneous correction of pectus excavatum and the underlying cardiovascular diseases.
authors.affiliation: Department of Anesthesiology, Escorts Heart Institute and Research Centre Ltd., New Delhi, India.
authors.forename: Bhuvnesh
authors.initials: B
authors.lastname: Kansara
authors.forename: Ajmer
authors.initials: A
authors.lastname: Singh
authors.forename: Samir
authors.initials: S
authors.lastname: Girotra
authors.forename: K S
authors.initials: KS
authors.lastname: Iyer
keywords: Aortic aneurysm; Marfan syndrome; pectus excavatum