title: The Right Heart in Congenital Heart Disease, Mechanisms and Recent Advances.
abstract: In patients with congenital heart disease, the right heart may support the pulmonary or the systemic circulation. Several congenital heart diseases primarily affect the right heart including Tetralogy of Fallot, transposition of great arteries, septal defects leading to pulmonary vascular disease, Ebstein anomaly and arrhythmogenic right ventricular cardiomyopathy. In these patients, right ventricular dysfunction leads to considerable morbidity and mortality. In this paper, our objective is to review the mechanisms and management of right heart failure associated with congenital heart disease. We will outline pearls and pitfalls in the management of congenital heart disease affecting the right heart and highlight recent advances in the field.
authors.affiliation: Cardiac Surgeon, Universite Paris-Sud, Laboratory of Surgical Research, Marie Lannelongue Surgical Center, France.
authors.forename: Julien
authors.initials: J
authors.lastname: Guihaire
authors.forename: François
authors.initials: F
authors.lastname: Haddad
authors.forename: Olaf
authors.initials: O
authors.lastname: Mercier
authors.forename: Daniel J
authors.initials: DJ
authors.lastname: Murphy
authors.forename: Joseph C
authors.initials: JC
authors.lastname: Wu
authors.forename: Elie
authors.initials: E
authors.lastname: Fadel
keywords: Congenital heart disease; Right heart