title: A case report of an intraabdominal microcystic and pseudopapillary spindle and round cell neoplasm and a comparison to other intraabdominal mesenchymal tumors.
abstract: OBJECTIVE
  We present a case of a new mesenchymal tumor entity named 'distinctive microcystic and pseudopapillary spindle and round cell neoplasm', of which only 30 cases have been reported worldwide.
  
  
  METHODS
  A fifty-two-year-old woman presented in January 2012 with epigastric pain of changing character and weight loss. Examinations revealed a tumor 10×6.8×9.8 cm in diameter showing infiltration in the surrounding organs. A Whipple procedure and a right hemicolectomy were necessary to achieve free resection margins. At the last follow-up in November 2012 the patient was well and there were no signs of recurrence or metastatic spread. Intra-abdominal mesenchymal tumors cause unspecific abdominal symptoms. Local recurrence and metastatic spread can occur. The main prognostic factors for survival are a free margin after resection and the histological subtype of the tumor. Behavioral prediction is not possible in every case and the treatment has to be individualized for every patient.
  
  
  CONCLUSIONS
  This case represents a new entity of mesenchymal tumor. It was treated according to the guidelines for intra-abdominal sarcomas. Further investigation of this kind of tumor is necessary to define therapeutic guidelines.
authors.affiliation: Universitätsklinik für Chirurgie, Klin. Abteilung für Allgemeinchirurgie, Auenbruggerplatz 29, A-8036 Graz, Austria. andrea.bradatsch@medunigraz.at
authors.forename: Andrea
authors.initials: A
authors.lastname: Bradatsch
authors.forename: Peter
authors.initials: P
authors.lastname: Kornprat
authors.forename: Johannes
authors.initials: J
authors.lastname: Haybaeck
authors.forename: Hans-Jörg
authors.initials: HJ
authors.lastname: Mischinger
mesh_terms: D000008:Abdominal Neoplasms / Q000473:pathology*; D005260:Female; D046152:Gastrointestinal Stromal Tumors / Q000473:pathology; D006801:Humans; D008637:Mesenchymoma / Q000473:pathology; D008875:Middle Aged; D012509:Sarcoma / Q000473:pathology; D014057:Tomography, X-Ray Computed