title: Coincidence of congenital agenesis of left lung and common atrium: a very rare case.
abstract: Pulmonary agenesis is characterized by undeveloped pulmonary vessels, bronchi as well as lung parenchyma and is a rare congenital anomaly with unknown etiology. It is usually diagnosed during childhood. Nearly, one third of these patients have concomitant congenital heart diseases. While more than 50% of these patients die before the age of 5 years, some other patients may be asymptomatic throughout their life. On the other hand, common atrium, another rare congenital anomaly, is characterized by complete absence of the atrial septum and is usually accompanied by atrioventricular valve malformations. An 18-year-old male presented with concomitant pulmonary agenesis and common atrium and had not undergone surgery due to high risk for mortality.
authors.affiliation: Department of Cardiology, Faculty of Medicine, Mazandaran University of Medical Sciences, Sari, Iran. Dr.Mr.Nabati@Gmail.com
authors.forename: Maryam
authors.initials: M
authors.lastname: Nabati
authors.forename: Babak
authors.initials: B
authors.lastname: Bagheri
authors.forename: Valiolla
authors.initials: V
authors.lastname: Habibi
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis* / Q000000981:diagnostic imaging; D000293:Adolescent; D000367:Age Factors; D015150:Echocardiography, Doppler / Q000379:methods*; D004562:Electrocardiography / Q000379:methods; D006325:Heart Atria / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006330:Heart Defects, Congenital / Q000175:diagnosis* / Q000000981:diagnostic imaging; D006343:Heart Septal Defects / Q000175:diagnosis / Q000000981:diagnostic imaging; D006801:Humans; D007492:Iran; D008168:Lung / Q000002:abnormalities / Q000000981:diagnostic imaging; D008171:Lung Diseases / Q000175:diagnosis* / Q000000981:diagnostic imaging; D008297:Male; D008991:Monitoring, Physiologic; D035583:Rare Diseases; D018570:Risk Assessment