title: Immunoglobulin g4-related systemic sclerosing disease: a case involving the ureter and kidney.
abstract: Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids.
authors.affiliation: Department of Urology, Kyung Hee University Hospital at Gangdong, Seoul, Korea.
authors.forename: Sunchan
authors.initials: S
authors.lastname: Kim
authors.forename: Tae Gu
authors.initials: TG
authors.lastname: Kim
authors.forename: Seung-Kwon
authors.initials: SK
authors.lastname: Choi
authors.forename: Myung Joon
authors.initials: MJ
authors.lastname: Kim
authors.forename: Gyeong Eun
authors.initials: GE
authors.lastname: Min
authors.forename: Hyung-Lae
authors.initials: HL
authors.lastname: Lee
authors.forename: Koo Han
authors.initials: KH
authors.lastname: Yoo
keywords: Immunoglobulin G; Sclerosis; Ureter