title: Surgical treatment of congenital rhabdoid tumor in a 10-day-old newborn.
abstract: BACKGROUND
  Malignant rhabdoid tumors are rare and aggressive tumors of pediatric age. The primary tumor can occur in different localizations, but it mainly involves kidney, soft tissue, or central nervous system. It has been associated to a poor diagnosis.
  
  
  METHODS
  The authors present the case of a 10-day-old newborn affected by a bulky nasofronto-orbitary neoplasm. The patient underwent radical surgical treatment and further excision of a preauricular metastasis combined with postoperative chemotherapy treatment.
  
  
  RESULTS
  The authors adopted a diagnostic and therapeutic protocol according to international guidelines, not without difficulty because the first histological report showed esthesioneuroblastoma. The rarity and aggresivity of rhabdoid tumor and the precocity of onset in our patient presented a difficulty to define prognostic factors and survival rates, as well as therapeutic plan of treatment.
  
  
  CONCLUSIONS
  The authors underline the importance of a correct prenatal diagnosis and an early surgical treatment to reach the complete healing of the patient.
authors.affiliation: Unit of Maxillo-Facial Surgery, Universitá "Sapienza" I Facoltá di Medicina e Chirurgia, Roma, Italy.
authors.forename: Valerio
authors.initials: V
authors.lastname: Ramieri
authors.forename: Emanuela
authors.initials: E
authors.lastname: Basile
authors.forename: Nikhil Carlo
authors.initials: NC
authors.lastname: Cascone
authors.forename: Paolo
authors.initials: P
authors.lastname: Arangio
authors.forename: Claudio
authors.initials: C
authors.lastname: Ungari
authors.forename: Paolo
authors.initials: P
authors.lastname: Gennaro
authors.forename: Andrea
authors.initials: A
authors.lastname: Di Cataldo
authors.forename: Angela
authors.initials: A
authors.lastname: Sementa
authors.forename: Mario Giuseppe
authors.initials: MG
authors.lastname: Romeo
authors.forename: Anna
authors.initials: A
authors.lastname: Clerico
authors.forename: Milena
authors.initials: M
authors.lastname: La Spina
authors.forename: Salvatore
authors.initials: S
authors.lastname: D'Amico
authors.forename: Maria
authors.initials: M
authors.lastname: Licciardello
authors.forename: Pietro
authors.initials: P
authors.lastname: Milone
authors.forename: Piero
authors.initials: P
authors.lastname: Cascone
mesh_terms: D006258:Head and Neck Neoplasms / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008279:Magnetic Resonance Imaging; D008297:Male; D011296:Prenatal Diagnosis; D018335:Rhabdoid Tumor / Q000175:diagnosis / Q000601:surgery*; D014057:Tomography, X-Ray Computed