title: Gastaut type idiopathic childhood occipital epilepsy.
abstract: Gastaut type idiopathic childhood occipital epilepsy is an uncommon epileptic syndrome characterised by frequent seizures, most commonly presenting as elementary visual hallucinations or blindness. Other occipital (non-visual) symptoms may also occur. Interictal EEG typically shows occipital paroxysms, often with fixation-off sensitivity. Ictal EEG is usually characterised by interruption by paroxysms and sudden appearance of low-voltage, occipital, fast rhythm and/or spikes. Despite well described clinical and EEG patterns, to our knowledge, there are very few reports in the literature with video-EEG recording of either seizure semiology or fixation-off phenomena. We present a video-EEG recording of a 12-year-old girl with Gastaut type epilepsy, illustrating the interictal and ictal aspects of this syndrome. Our aim was to demonstrate the clinical and neurophysiological pattern of a typical seizure of Gastaut type epilepsy, as well as the fixation-off phenomena, in order to further clarify the typical presentation of this syndrome. [Published with video sequences].
authors.affiliation: Department of Neurology and Neurosurgery, Hospital São Paulo, Universidade Federal de São Paulo, Brazil. taissaferrari@yahoo.com.br
authors.forename: Taissa
authors.initials: T
authors.lastname: Ferrari-Marinho
authors.forename: Eugenia Fialho
authors.initials: EF
authors.lastname: Macedo
authors.forename: Rafael Scarpa
authors.initials: RS
authors.lastname: Costa Neves
authors.forename: Lívia Vianez
authors.initials: LV
authors.lastname: Costa
authors.forename: Ivanda S S
authors.initials: IS
authors.lastname: Tudesco
authors.forename: Kelly C
authors.initials: KC
authors.lastname: Carvalho
authors.forename: Henrique
authors.initials: H
authors.lastname: Carrete
authors.forename: Luis Otavio
authors.initials: LO
authors.lastname: Caboclo
authors.forename: Elza Marcia
authors.initials: EM
authors.lastname: Yacubian
authors.forename: Ana Paula
authors.initials: AP
authors.lastname: Hamad
mesh_terms: D002648:Child; D004569:Electroencephalography; D004828:Epilepsies, Partial / Q000503:physiopathology*; D005260:Female; D006801:Humans; D009778:Occipital Lobe / Q000503:physiopathology*
keywords: Gastaut type epilepsy; idiopathic childhood epilepsy; video-EEG