title: Orocraniofacial findings and dental management of a pediatric patient with Dubowitz syndrome.
abstract: Dubowitz syndrome is a rare genetic condition characterized by microcephaly, dysmorphic facial features and delayed general growth. It is transmitted through autosomal recessive inheritance. The purpose of this report is to describe the oral, craniofacial and systemic characteristics of a 7-year 11-month-old boy with Dubowitz syndrome and the dental management provided. The pediatric dentist should possess the ability to recognize this rare alteration, to provide dental treatment and to refer for the necessary medical and multidisciplinary treatment.
authors.affiliation: Pediatric Dentistry Posgraduate Program, Facultad de Estomatología, Universidad Autónoma de San Luis Potosí, México.
authors.forename: J Arturo
authors.initials: JA
authors.lastname: Garrocho-Rangel
authors.forename: Gloria A
authors.initials: GA
authors.lastname: Bueno-Rubio
authors.forename: Beatriz
authors.initials: B
authors.lastname: Martínez-Sandoval
authors.forename: Ma Socorro
authors.initials: MS
authors.lastname: Ruiz-Rodríguez
authors.forename: Miguel A
authors.initials: MA
authors.lastname: Santos-Diaz
authors.forename: Amaury J
authors.initials: AJ
authors.lastname: Pozos-Guillén
mesh_terms: D000402:Airway Obstruction / Q000209:etiology; D002508:Cephalometry; D002648:Child; D003731:Dental Caries / Q000209:etiology / Q000628:therapy*; D003793:Dental Restoration, Permanent / Q000379:methods*; D004485:Eczema / Q000150:complications*; D005147:Facial Bones / Q000002:abnormalities; D019066:Facies; D006130:Growth Disorders / Q000150:complications*; D006801:Humans; D006972:Hypertelorism / Q000209:etiology; D008607:Intellectual Disability / Q000150:complications*; D008297:Male; D008310:Malocclusion / Q000209:etiology; D008831:Microcephaly / Q000150:complications*; D008844:Micrognathism / Q000209:etiology; D024343:Open Bite / Q000209:etiology; D010895:Pit and Fissure Sealants / Q000627:therapeutic use; D063173:Retrognathia / Q000209:etiology; D013577:Syndrome
chemical_list: D010895:Pit and Fissure Sealants