title: Total hip arthroplasty in a 17-year-old girl with progressive pseudorheumatoid dysplasia.
abstract: Progressive pseudorheumatoid dysplasia is an autosomal recessively inherited skeletal disease. Progressive pseudorheumatoid dysplasia can involve multiple synovial joints, which then develop structural deformity and articular dysfunction. We report a case of progressive pseudorheumatoid dysplasia with polyarthropathy in a 17-year-old girl. Total hip arthroplasty was performed to treat persistent pain and stiffness by reconstructing a functional joint. Although we found arthroplasty to be an effective way of reconstructing a functional joint, treatment of the underlying cause is urgently required for this disease in the future.
authors.affiliation: Department of Orthopedic Surgery, Shanghai Sixth People's Hospital, Shanghai Jiao Tong University, Shanghai, China.
authors.forename: You-Shui
authors.initials: YS
authors.lastname: Gao
authors.forename: Hao
authors.initials: H
authors.lastname: Ding
authors.forename: Chang-Qing
authors.initials: CQ
authors.lastname: Zhang
mesh_terms: D000293:Adolescent; D001177:Arthropathy, Neurogenic / Q000601:surgery*; D019644:Arthroplasty, Replacement, Hip; D005260:Female; D006621:Hip Joint / Q000601:surgery; D006801:Humans; D007592:Joint Diseases / Q000151:congenital; D016896:Treatment Outcome