title: Progressive symmetrical erythrokeratodermia -- case report.
abstract: Progressive symmetrical erythrokeratodermia is a rare autosomal dominant genodermatosis with variable penetrance described by Darier in 1911. It is characterized by erythematous and keratotic plaques, sharply defined and symmetrically distributed along the extremities, buttocks and, more rarely, on the face. We report a case of a 55-year-old patient with lesions on the dorsum of the hands, interphalangeal pads, wrists, groin and back feet. This case demonstrates a rare and late diagnosis, clinical profusion and presence of familiar involvement.
authors.affiliation: Naval Hospital Marcílio Dias (Hospital Naval Marcílio Dias - HNMD), Rio de Janeiro (RJ), Brazil. biaguaraldi@hotmail.com
authors.forename: Bianca de Mello
authors.initials: Bde M
authors.lastname: Guaraldi
authors.forename: Thaís Jerez
authors.initials: TJ
authors.lastname: Jaime
authors.forename: Rafael de Mello
authors.initials: Rde M
authors.lastname: Guaraldi
authors.forename: Daniel Fernandes
authors.initials: DF
authors.lastname: Melo
authors.forename: Osvania Maris
authors.initials: OM
authors.lastname: Nogueira
authors.forename: Nilton
authors.initials: N
authors.lastname: Rodrigues
mesh_terms: D017255:Acitretin / Q000627:therapeutic use; D056266:Erythrokeratodermia Variabilis / Q000188:drug therapy / Q000473:pathology*; D005260:Female; D006801:Humans; D007645:Keratoderma, Palmoplantar / Q000188:drug therapy / Q000473:pathology*; D007641:Keratolytic Agents / Q000627:therapeutic use; D008875:Middle Aged
chemical_list: D007641:Keratolytic Agents; D017255:Acitretin
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