title: Individualized approach in the management of patients with hypoplastic left heart syndrome (HLHS).
abstract: Over the past decade new variations on the "classic" first stage palliation (the Norwood/BT shunt) for patients with Hypoplastic Left Heart Syndrome have emerged and been vetted by the medical community. A "one size fits all" approach may not be adequate anymore. In this review, the optimal indications for the various palliative options (Norwood/BT shunt, Norwood/RV-PA conduit, Hybrid Stage I with or without ductal stenting, heart transplantation) are reviewed from a standpoint of the initial anatomy and physiology of the patient, letting it guide clinical management. Current knowledge useful for decision-making is also reviewed as objectively as possible.
authors.affiliation: Division of Cardiothoracic Surgery, Columbia University Medical Center, New York-Presbyterian, Morgan Stanley Children's Hospital, New York, NY 10032, USA. eb2709@columbia.edu
authors.forename: Emile A
authors.initials: EA
authors.lastname: Bacha
mesh_terms: D006348:Cardiac Surgical Procedures / Q000379:methods* / Q000401:mortality; D005260:Female; D016027:Heart Transplantation / Q000379:methods / Q000401:mortality; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000175:diagnosis / Q000401:mortality* / Q000601:surgery*; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D058327:Norwood Procedures / Q000379:methods / Q000401:mortality; D010166:Palliative Care / Q000379:methods; D057285:Precision Medicine / Q000379:methods*; D011379:Prognosis; D018570:Risk Assessment; D015607:Stents; D016019:Survival Analysis; D016896:Treatment Outcome