title: Successful treatment of heart failure in an adult patient with Prader-Willi syndrome.
abstract: Prader-Willi Syndrome (PWS) is a rare genetic disorder characterized by physical, psychological and physiological abnormalities. Obesity and related cardiovascular diseases are a common problem in adult patients with PWS. This report describes a case of adult PWS with heart failure associated with marked obesity and sleep-disordered breathing that was successfully treated with oxygen therapy, adaptive servoventilation, medications, diet therapy and rehabilitation.
authors.affiliation: Department of Cardiovascular Medicine, Nagasaki University Graduate School of Biomedical Sciences, Japan. hkawano@nagasaki-u.ac.jp
authors.forename: Hiroaki
authors.initials: H
authors.lastname: Kawano
authors.forename: Tooru
authors.initials: T
authors.lastname: Ikeda
authors.forename: Koichi
authors.initials: K
authors.lastname: Shimazaki
authors.forename: Shuji
authors.initials: S
authors.lastname: Arakawa
authors.forename: Yuji
authors.initials: Y
authors.lastname: Matsumoto
authors.forename: Motonobu
authors.initials: M
authors.lastname: Hayano
authors.forename: Koji
authors.initials: K
authors.lastname: Maemura
mesh_terms: D000328:Adult; D004035:Diet Therapy / Q000379:methods; D005081:Exercise Therapy / Q000379:methods; D005260:Female; D006333:Heart Failure / Q000150:complications* / Q000175:diagnosis / Q000628:therapy*; D006801:Humans; D011218:Prader-Willi Syndrome / Q000150:complications* / Q000175:diagnosis / Q000628:therapy*; D016896:Treatment Outcome