title: Anesthetic management of a patient with Huntington's chorea -A case report-.
abstract: Huntington's chorea is a rare hereditary disorder of the nervous system. It is inherited as an autosomal dominant disorder and is characterized by progressive chorea, dementia and psychiatric disturbances. The best anesthetic technique is yet to be established for these patients with increased risk of aspiration due to involvement of pharyngeal muscles and an exaggerated response to sodium thiopental and succinylcholine. The primary goal in general anesthesia for these patients is to provide airway protection and a rapid and safe recovery. We report the anesthetic management of a 51-year-old patient with Huntington's chorea admitted for an emergency operation.
authors.affiliation: Department of Anesthesiology and Pain Medicine, Kyung Hee University Hospital at Gangdong, College of Medicine, Kyung Hee University, Seoul, Korea.
authors.forename: Jong-Man
authors.initials: JM
authors.lastname: Kang
authors.forename: Jun-Young
authors.initials: JY
authors.lastname: Chung
authors.forename: Jin Hee
authors.initials: JH
authors.lastname: Han
authors.forename: Yung-Suk
authors.initials: YS
authors.lastname: Kim
authors.forename: Bong Jae
authors.initials: BJ
authors.lastname: Lee
authors.forename: Jae-Woo
authors.initials: JW
authors.lastname: Yi
keywords: Bronchoscope; Huntington disease; Intubation
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