title: A girl with sternal malformation/vascular dysplasia association.
abstract: Sternal malformation/vascular dysplasia association is a rare congenital dysmorphology, which has not yet been reported in Korea. Its typical clinical features include a sternal cleft covered with atrophic skin, a median abdominal raphe extending from the sternal defect to the umbilicus, and cutaneous craniofacial hemangiomata. We report a case of a full-term newborn who presented with no anomalies at birth, except for a skin defect over the sternum and a supraumbilical raphe. Multiple hemangiomas appeared subsequently on her chin and upper chest wall, and respiratory distress due to subglottic hemangioma developed during the first 2 months of life. Her symptoms were controlled with oral prednisolone administration. No respiratory distress have recurred during the 3-year follow-up period.
authors.affiliation: Department of Pediatrics, Ewha Womans University School of Medicine, Seoul, Korea.
authors.forename: Na Yong
authors.initials: NY
authors.lastname: Lee
authors.forename: Hye Kyung
authors.initials: HK
authors.lastname: Cho
authors.forename: Kyung-Hyo
authors.initials: KH
authors.lastname: Kim
authors.forename: Eun Ae
authors.initials: EA
authors.lastname: Park
keywords: Hemangioma; Malformation; Sternum
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