title: Ebstein's anomaly with subpulmonary obstruction--a rare association.
abstract: Ebstein's anomaly comprises a wide spectrum of congenital cardiac abnormalities involving the tricuspid valve (TV) apparatus and the architecture of the morphological right ventricle (RV). We report a case of Ebstein's anomaly in a 3-year-old boy having a unique association with severe subpulmonic obstruction caused by tethered and dysplastic anterior tricuspid leaflet (ATL), and a large ventricular septal defect. In view of poorly functioning RV, the baby was planned for a bidirectional Glenn shunt with subsequent Fontan completion.
authors.affiliation: Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences and Research, Bangalore, Karnataka, India. dr_bhupinders@yahoo.in
authors.forename: Bhupinder
authors.initials: B
authors.lastname: Singh
authors.forename: Anand
authors.initials: A
authors.lastname: Subramanyan
authors.forename: M
authors.initials: M
authors.lastname: Jayaranganath
authors.forename: C N
authors.initials: CN
authors.lastname: Manjunath
mesh_terms: D002675:Child, Preschool; D003937:Diagnosis, Differential; D004437:Ebstein Anomaly / Q000150:complications* / Q000000981:diagnostic imaging*; D004452:Echocardiography / Q000379:methods*; D006801:Humans; D008297:Male; D011662:Pulmonary Subvalvular Stenosis / Q000150:complications* / Q000000981:diagnostic imaging*
keywords: Ebstein's anomaly; pulmonary valve; ventricular septal defect