title: Degos' syndrome complicated by bowel perforation: focus on radiological findings.
abstract: We describe a 50-year-old man who first presented with multiple skin lesions which were characteristic of Degos' syndrome. The patient developed multiple episodes of abdominal pain. Some episodes resolved with conservative management, for others he underwent urgent operations for bowel perforations. The patient subsequently underwent extensive small bowel resection, but further systemic deterioration ensued and he died. The imaging findings of Degos' syndrome and the implications of pneumatosis intestinalis and pneumoperitoneum are discussed.
authors.affiliation: Department of Diagnostic Radiology, Princess Margaret Hospital, Laichikok, Hong Kong. jezzyeung@gmail.com
authors.forename: Jessie T H
authors.initials: JT
authors.lastname: Yeung
authors.forename: Johnny K F
authors.initials: JK
authors.lastname: Ma
authors.forename: Alfred W T
authors.initials: AW
authors.lastname: Yung
mesh_terms: D015746:Abdominal Pain / Q000175:diagnosis / Q000209:etiology; D018450:Disease Progression; D017809:Fatal Outcome; D006801:Humans; D007416:Intestinal Perforation / Q000000981:diagnostic imaging* / Q000209:etiology / Q000601:surgery; D008297:Male; D054853:Malignant Atrophic Papulosis / Q000150:complications* / Q000175:diagnosis; D008875:Middle Aged; D011027:Pneumoperitoneum / Q000000981:diagnostic imaging* / Q000209:etiology / Q000601:surgery*; D012008:Recurrence; D018570:Risk Assessment; D012720:Severity of Illness Index; D014057:Tomography, X-Ray Computed / Q000379:methods
keywords: Intestinal perforation; Malignant atrophic papulosis; Pneumatosis cystoides intestinalis; Pneumoperitoneum; Skin diseases, vascular