title: Orbital cavitary rhabdomyosarcoma: case report and literature review.
abstract: Orbital cavitary rhabdomyosarcoma has been previously reported in 2 cases. The case presented here was a 15-year-old boy who had proptosis, pain, periorbital hyperemia, and visual loss in his OD, which progressed in 6 weeks. Radiologic studies demonstrated a well-demarcated, multilobulated, large mass with cavities, extending from the anterior orbit to the apex, suggesting a diagnosis of venolymphatic malformation with an intrinsic hemorrhage. On surgery, a multilobular, hemorrhagic cystic mass was almost completely excised. Histologic examination revealed a diagnosis of embryonal rhabdomyosarcoma. After postoperative chemotherapy and radiotherapy, the tumor did not recur during a follow-up period of 45 months. This case, together with the previous ones, suggests that cavitary orbital rhabdomyosarcomas may have some distinct clinical, radiologic, and surgical characteristics.
authors.affiliation: Departments of *Ophthalmology and †Radiology, Uludag University, Bursa, Turkey.
authors.forename: Bülent
authors.initials: B
authors.lastname: Yazıcı
authors.forename: Huri
authors.initials: H
authors.lastname: Sabur
authors.forename: Zeynep
authors.initials: Z
authors.lastname: Yazıcı
mesh_terms: D000293:Adolescent; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009801:Oculomotor Muscles / Q000473:pathology; D009918:Orbital Neoplasms / Q000473:pathology* / Q000532:radiotherapy / Q000601:surgery; D018232:Rhabdomyosarcoma, Alveolar / Q000473:pathology* / Q000532:radiotherapy / Q000601:surgery; D014057:Tomography, X-Ray Computed; D014792:Visual Acuity