title: Primary pediatric endobronchial Ewing sarcoma family of tumors.
abstract: BACKGROUND
  Ewing sarcoma family of tumors is the second most common primary bone tumor of childhood. Extraosseous Ewing sarcoma family of tumors is rare. We present a pediatric case of primary endobronchial Ewing sarcoma family of tumors.
  
  
  METHODS
  A 12-year-old boy presented with dyspnea and chest radiography showed right pulmonary atelectasis. Chest computed tomography demonstrated tumor in the right main bronchus. Histopathological examination of the resected tumor demonstrated Ewing sarcoma family of tumors. No other lesions were detected throughout the body and the right main bronchus was thought to be the primary site. As of 1 year and 6 months after further resection of residual tumor followed by chemotherapy and radiotherapy, the patient remains disease-free.
  
  
  CONCLUSIONS
  Extraosseous Ewing sarcoma family of tumors arises in soft tissues of the trunk or extremities, but primary endobronchial Ewing sarcoma family of tumors has rarely been reported. Although quite rare, Ewing sarcoma family of tumors should be considered among the differential diagnoses for pediatric bronchial tumor.
authors.affiliation: Department of Pediatrics, Kobe University Graduate School of Medicine, Kobe, Japan.
authors.forename: Akira
authors.initials: A
authors.lastname: Hayakawa
authors.forename: Satoshi
authors.initials: S
authors.lastname: Hirase
authors.forename: Natsuki
authors.initials: N
authors.lastname: Matsunoshita
authors.forename: Nobuyuki
authors.initials: N
authors.lastname: Yamamoto
authors.forename: Ikuko
authors.initials: I
authors.lastname: Kubokawa
authors.forename: Takeshi
authors.initials: T
authors.lastname: Mori
authors.forename: Tomoko
authors.initials: T
authors.lastname: Yanai
authors.forename: Yoshimasa
authors.initials: Y
authors.lastname: Maniwa
authors.forename: Kazumoto
authors.initials: K
authors.lastname: Iijima
keywords: Ewing sarcoma family of tumors; atelectasis; pediatric endobronchial tumor