title: Intra-abdominal primary monophasic synovial sarcoma with hemangiopericytoma-like areas.
abstract: We report a case of retroperitoneal intra-abdominal primary monophasic synovial sarcoma (SS) with hemangiopericytomatous (HPC) pattern in a 25-year-old male arising from the triangular ligament on the superior surface of liver encasing the inferior vena cava (IVC) and masquerading as a hepatic tumor. A large heterogeneously enhancing, well defined, lobulated, exophytic lesion was seen involving segment VIII of the liver with foci of calcification in the periphery. A biopsy, followed by total resection of the tumor, showed a spindle cell sarcoma with HPC pattern, which was consistent with monophasic SS on histology and immunohistochemistry. The unusual clinical presentation, radiology, pathology, and differential diagnosis will be discussed in detail.
authors.affiliation: Department of Pathology, Basic Sciences Block, Manipal, Karnataka, India.
authors.forename: Lakshmi
authors.initials: L
authors.lastname: Rao
authors.forename: Padmapriya
authors.initials: P
authors.lastname: Jaiprakash
authors.forename: Nagaraj
authors.initials: N
authors.lastname: Palankar
authors.forename: Vinay
authors.initials: V
authors.lastname: Gowda
mesh_terms: D000328:Adult; D001706:Biopsy; D006393:Hemangiopericytoma / Q000473:pathology*; D006801:Humans; D007150:Immunohistochemistry; D008297:Male; D012187:Retroperitoneal Space / Q000473:pathology*; D013584:Sarcoma, Synovial / Q000175:diagnosis*; D014057:Tomography, X-Ray Computed