title: Intrahepatic biliary intraductal papillary mucinous neoplasm with gallbladder agenesis: case report.
abstract: We report here on a case of intraductal papillary mucinous neoplasm (IPMN) of the bile duct, associated with gallbladder agenesis. A 65-year-old woman was admitted to the hospital with epigastric pain, anorexia, and nausea. Abdominal computed tomography scan and magnetic resonance imaging showed a 5 × 2.5 cm lobulated cystic lesion in the lateral lobe of the liver. The gallbladder was not seen on both imaging modalities. Endoscopic retrograde cholangiopancreatography suggested the diagnosis of biliary IPMN due to abundant mucin that protruded from the papilla and the lobulated cystic lesion. Laparoscopic wedge resection of the liver was performed. The final pathology was consistent with biliary IPMN. The specimen showed multifocal high-grade dysplasia with negative resection margins. The patient experienced no postoperative complications and was discharged 5 days after the operation.
authors.affiliation: Department of Surgery, Division of Hepatobiliary Surgery, School of Medicine, Kyung Hee University, Seoul, Korea.
authors.forename: Bum-Soo
authors.initials: BS
authors.lastname: Kim
authors.forename: Sun-Hyung
authors.initials: SH
authors.lastname: Joo
authors.forename: Sung-Jig
authors.initials: SJ
authors.lastname: Lim
authors.forename: Kwang-Ro
authors.initials: KR
authors.lastname: Joo
mesh_terms: D002288:Adenocarcinoma, Mucinous / Q000473:pathology / Q000601:surgery*; D000231:Adenocarcinoma, Papillary / Q000473:pathology / Q000601:surgery*; D000368:Aged; D001650:Bile Duct Neoplasms / Q000175:diagnosis / Q000473:pathology / Q000601:surgery*; D001653:Bile Ducts, Intrahepatic / Q000473:pathology / Q000601:surgery*; D001707:Biopsy, Needle; D002760:Cholangiopancreatography, Endoscopic Retrograde / Q000379:methods; D049448:Cholangiopancreatography, Magnetic Resonance / Q000379:methods; D005260:Female; D005500:Follow-Up Studies; D005704:Gallbladder / Q000002:abnormalities*; D006498:Hepatectomy / Q000379:methods; D006801:Humans; D007150:Immunohistochemistry; D010535:Laparoscopy / Q000379:methods; D035583:Rare Diseases; D018570:Risk Assessment; D016896:Treatment Outcome