title: Video-assisted thoracoscopic surgery for recurrent pneumothorax in pulmonary lymphangioleimyomatosis with tuberous sclerosis complex.
abstract: Pneumothorax in pulmonary lymphangioleiomyomatosis (LAM) with tuberous sclerosis complex (TSC) is a difficult condition to manage. Video-assisted thoracoscopic surgery (VATS) may play a role in diagnosis and treatment of this situation. We present a case of right recurrent pneumothorax due to LAM with TSC in whom VATS was performed for pathological diagnosis and mechanical pleurodesis. The unique presentation of LAM in TSC was also discussed.
authors.affiliation: Department of Dermatology, National Taiwan University Hospital and National Taiwan University College of Medicine, Taipei, Taiwan.
authors.forename: Chia-Fen
authors.initials: CF
authors.lastname: Tsai
authors.forename: Chen-Hao
authors.initials: CH
authors.lastname: Hsiao
authors.forename: Jang-Ming
authors.initials: JM
authors.lastname: Lee
authors.forename: Ke-Cheng
authors.initials: KC
authors.lastname: Chen
authors.forename: Ming-Jium
authors.initials: MJ
authors.lastname: Shieh
authors.forename: Hong-Shiee
authors.initials: HS
authors.lastname: Lai
authors.forename: Jin-Shing
authors.initials: JS
authors.lastname: Chen
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D008171:Lung Diseases / Q000150:complications*; D018192:Lymphangioleiomyomatosis / Q000150:complications*; D011030:Pneumothorax / Q000150:complications* / Q000601:surgery*; D012008:Recurrence; D020775:Thoracic Surgery, Video-Assisted / Q000379:methods*; D014402:Tuberous Sclerosis / Q000150:complications*