title: Fibrocartilaginous intramedullary bone forming tumor of the distal femur mimicking osteosarcoma.
abstract: Fibrocartilaginous dysplasia (FCD) has occasionally led to a misdiagnosis and wrong decision which can significantly alter the outcome of the patients. A 9-yr-old boy presented with pain on his left distal thigh for 6 months without any trauma history. Initial radiographs showed moth eaten both osteolytic and osteosclerotic lesions and biopsy findings showed that the lesion revealed many irregular shaped and sclerotic mature and immature bony trabeculae. Initial diagnostic suggestions were varied from the conventional osteosarcoma to low grade central osteosarcoma or benign intramedullary bone forming lesion, but close observation was done. This study demonstrated a case of unusual fibrocartilaginous intramedullary bone forming tumor mimicking osteosarcoma, so that possible misdiagnosis might be made and unnecessary extensive surgical treatment could be performed. In conclusion, the role of orthopaedic oncologist as a decision maker is very important when the diagnosis is uncertain.
authors.affiliation: Department of Orthopaedic Surgery, Soonchunhyang University Bucheon Hospital, Bucheon, Korea.
authors.forename: Sang-Heon
authors.initials: SH
authors.lastname: Song
authors.forename: Hanna
authors.initials: H
authors.lastname: Lee
authors.forename: Hae-Ryong
authors.initials: HR
authors.lastname: Song
authors.forename: Myo-Jong
authors.initials: MJ
authors.lastname: Kim
authors.forename: Jong-Hoon
authors.initials: JH
authors.lastname: Park
mesh_terms: D001842:Bone and Bones / Q000000981:diagnostic imaging*; D002648:Child; D003937:Diagnosis, Differential; D005269:Femur / Q000000981:diagnostic imaging; D051445:Fibrocartilage / Q000000981:diagnostic imaging*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D012516:Osteosarcoma / Q000175:diagnosis / Q000000981:diagnostic imaging; D011859:Radiography
keywords: Diagnosis; Fibrocartilaginous Dysplasia; Orthopaedic Oncologist; Osteosarcoma