title: Issues in pediatric haemophilia care.
abstract: The hemophilias are the most common X-linked inherited bleeding disorders. The challenges in children are different from that in adults and, If not properly managed, can lead to chronic disease and lifelong disabilities. Currently, inhibitors are the most severe complication and prophylaxis is emerging as the optimal preventive care strategy. Quality of life has become in the western countries the primary objective of the process of providing care, thus all the strategies (psychotherapy, physiotherapy, community life), not just the infusion of the missing factor, should be activated for the patient and family to give them the perception of being healthy.
authors.affiliation: Dipartimento di Scienze Biomediche ed Oncologia Umana, Clinica Pediatrica, Università degli Studi di Bari Aldo Moro, Bari, Italy. paola.giordano@uniba.it
authors.forename: Paola
authors.initials: P
authors.lastname: Giordano
authors.forename: Massimo
authors.initials: M
authors.lastname: Franchini
authors.forename: Giuseppe
authors.initials: G
authors.lastname: Lassandro
authors.forename: Maria Felicia
authors.initials: MF
authors.lastname: Faienza
authors.forename: Roberto
authors.initials: R
authors.lastname: Valente
authors.forename: Angelo Claudio
authors.initials: AC
authors.lastname: Molinari
mesh_terms: D002648:Child; D003029:Coagulants / Q000008:administration & dosage*; D003695:Delivery of Health Care / Q000458:organization & administration; D019317:Evidence-Based Medicine; D005164:Factor IX / Q000008:administration & dosage*; D005169:Factor VIII / Q000008:administration & dosage*; D006467:Hemophilia A / Q000175:diagnosis / Q000188:drug therapy* / Q000453:epidemiology / Q000517:prevention & control; D002836:Hemophilia B / Q000175:diagnosis / Q000188:drug therapy* / Q000453:epidemiology / Q000517:prevention & control; D006801:Humans; D007558:Italy / Q000453:epidemiology; D009140:Musculoskeletal Diseases / Q000517:prevention & control; D011788:Quality of Life; D012307:Risk Factors; D012944:Social Support; D016896:Treatment Outcome
chemical_list: D003029:Coagulants; D005169:Factor VIII; D005164:Factor IX