title: Functional pulmonary atresia in newborn with normal intracardiac anatomy: Successful treatment with inhaled nitric oxide and pulmonary vasodilators.
abstract: Functional pulmonary atresia is characterized by a structurally normal pulmonary valve that does not open during right ventricular ejection. It is usually associated with Ebstein's anomaly, Uhl's anomaly, neonatal Marfan syndrome and tricuspid valve dysplasia. However, functional pulmonary atresia is rarely reported in newborn with anatomically normal heart. We report a newborn with functional pulmonary atresia who had normal intracardiac anatomy, who responded to treatment with nitric oxide and other vasodilator therapy successfully.
authors.affiliation: Department of Pediatric Cardiology, Kocaeli University, Medical Faculty, Kocaeli, Turkey.
authors.forename: Gürkan
authors.initials: G
authors.lastname: Altun
authors.forename: Kadir
authors.initials: K
authors.lastname: Babaoğlu
authors.forename: Köksal
authors.initials: K
authors.lastname: Binnetoğlu
authors.forename: Nazan
authors.initials: N
authors.lastname: Kavas
authors.forename: Ayşe Engin
authors.initials: AE
authors.lastname: Arısoy
keywords: Echocardiography; functional pulmonary atresia; nitric oxide