title: Pulmonary Arterial Hypertension-A Deadly Complication of Systemic Sclerosis.
abstract: Pulmonary arterial hypertension (PAH) is a devastating disease with limited therapeutic options. Moreover, when PAH occurs in patients diagnosed with systemic sclerosis, worse outcomes are observed. The purpose of this review is to discuss the etiologies of PAH found in the systemic sclerosis patient, limitations of current medical therapies, and, finally, potential therapies for patients with this combination.
authors.affiliation: Department of Pharmacology, Tulane University School of Medicine, New Orleans, LA, USA.
authors.forename: Edward A
authors.initials: EA
authors.lastname: Pankey
authors.forename: Matthew
authors.initials: M
authors.lastname: Epps
authors.forename: Bobby D
authors.initials: BD
authors.lastname: Nossaman
authors.forename: Albert L
authors.initials: AL
authors.lastname: Hyman
authors.forename: Philip J
authors.initials: PJ
authors.lastname: Kadowitz
keywords: connective tissue disease; pulmonary arterial hypertension; pulmonary hypertension; systemic sclerosis