title: Advanced hepatocellular carcinoma in adolescence associated with congenital cholestasis: a case description.
abstract: This case describes the clinical course and treatment of a 17-year-old male patient with advanced hepatocellular carcinoma (HCC) arising in a non-cirrhotic liver. The disease was thought to be caused by a congenital cholestatic syndrome associated with intermittent oedema in childhood, resembling the rare Aagenaes syndrome. Treatment choices in advanced HCC arising in adolescence are discussed.
authors.affiliation: Department of Oncology, Aarhus University Hospital, Aarhus, Denmark, Norway.
authors.forename: Morten
authors.initials: M
authors.lastname: Ladekarl
authors.forename: Gerda Elisabeth
authors.initials: GE
authors.lastname: Villadsen
authors.forename: Anne Roed
authors.initials: AR
authors.lastname: Rudbeck
authors.forename: Oystein
authors.initials: O
authors.lastname: Aagenæs
authors.forename: Jens Erik
authors.initials: JE
authors.lastname: Nielsen
authors.forename: Stephen
authors.initials: S
authors.lastname: Hamilton-Dutoit
authors.forename: Marianne
authors.initials: M
authors.lastname: Nordsmark
keywords: Adolescence; Chemotherapy; Congenital cholestasis syndrome; Hepatocellular carcinoma; Juvenile; Treatment