title: [Analgesia for labour and delivery in a parturient with paramytonia congenita].
abstract: A patient presenting with paramyotonia congenita (Eulenburg's paramyotonia) was seen at the preanaesthetic visit during pregnancy. The underlying disease was known for years. Analysis of the literature and advice taken from specialists emphasized the safe use of regional anaesthesia and analgesia which was indeed used for labour and delivery without any complication. By contrast, the limited information available on the use of general anaesthesia suggests the risks associated with the use of succinylcholine and possibly with halogenated agents. Additional and useful factors that may limit the occurrence of myotonic crises such as maintenance of normal temperature and plasma potassium concentration, should be undertaken simultaneously.
authors: Département d'anesthésie-réanimation, hôpital Bicêtre, hôpitaux universitaires Paris-Sud, 78 rue du Général-Leclerc, Le Kremlin-Bicêtre cedex, France.
authors: B
authors: B
authors: Frossard
authors: C
authors: C
authors: Combret
authors: D
authors: D
authors: Benhamou
mesh_terms: D000328:Adult; D000577:Amides; D015360:Analgesia, Epidural / Q000379:methods*; D016362:Analgesia, Obstetrical / Q000379:methods*; D003080:Cold Temperature / Q000009:adverse effects; D000075202:Contraindications; D005260:Female; D006221:Halothane; D006801:Humans; D007008:Hypokalemia / Q000517:prevention & control; D007035:Hypothermia / Q000517:prevention & control; D020125:Mutation, Missense; D020967:Myotonic Disorders / Q000235:genetics / Q000503:physiopathology; D062553:NAV1.4 Voltage-Gated Sodium Channel / Q000235:genetics; D017354:Point Mutation; D011247:Pregnancy; D012042:Registries; D000077212:Ropivacaine; D013390:Succinylcholine; D017409:Sufentanil
chemical_list: D000577:Amides; D062553:NAV1.4 Voltage-Gated Sodium Channel; C106251:SCN4A protein, human; D000077212:Ropivacaine; D017409:Sufentanil; D013390:Succinylcholine; D006221:Halothane