title: Retinoblastoma with unusual association of postaxial polydactyly.
abstract: BACKGROUND
  Retinoblastoma is the most common primary intraocular malignancy of childhood, arising from retinal progenitor cells. The most common presenting feature is leucocoria, followed by strabismus, defective vision, and rarely nystagmus. The unusual associations reported with retinoblastoma are well-differentiated liposarcoma and lipomatous tissues, chromosome breakage syndromes, and the myriad findings of rare 13q deletion syndrome.
  
  
  METHODS
  Case report.
  
  
  RESULTS
  An 8-year-old boy presented with features of retinoblastoma, having leucocoria in the left eye and an unusual association of postaxial polydactyly in the left hand.
  
  
  CONCLUSIONS
  Postaxial polydactyly should be considered as an association of retinoblastoma.
authors: Regional Institute of Ophthalmology, Indira Gandhi Institute of Medical Sciences, Sheikhpura, Patna, India. drdmishra12@yahoo.com
authors: Deepak
authors: D
authors: Mishra
authors: Pratyush
authors: P
authors: Ranjan
authors: Bibhuti P
authors: BP
authors: Sinha
authors: Vijay
authors: V
authors: Baijal
authors: Madhu
authors: M
authors: Bhadauria
mesh_terms: D002648:Child; D002882:Chromosomes, Human, Pair 13 / Q000235:genetics; D005385:Fingers / Q000002:abnormalities*; D006801:Humans; D008297:Male; D017689:Polydactyly / Q000175:diagnosis* / Q000235:genetics; D019572:Retinal Neoplasms / Q000175:diagnosis*; D012175:Retinoblastoma / Q000175:diagnosis*; D013577:Syndrome; D014034:Toes / Q000002:abnormalities*