title: Limb salvage treatment for Gollop-Wolfgang complex (femoral bifurcation, complete tibial hemimelia, and hand ectrodactyly).
abstract: We reported the findings from three patients with Gollop-Wolfgang complex and demonstrated the results of five limb salvage treatments for this condition. All three femoral bifurcations were accompanied by ipsilateral complete tibial hemimelia. Two patients showed contralateral complete or partial tibial hemimelia, and one patient had hand ectrodactyly. The five limb salvage treatments included resection of the anteromedial bifurcated femur in three limbs, foot centralization in five limbs, tibiofibular fusion in one limb with partial tibial hemimelia, fibular transfer (Brown's procedure) in three limbs with complete tibial hemimelia, and callus distraction lengthening in one limb. The duration from the first operation to the final follow-up ranged from 3.5 to 5.4 years. None of the three knees treated by fibular transfer achieved a successful functional result, but all of the knees were ultimately able to withstand weight bearing. Early knee disarticulation and resection of the protruded bifurcated femur, followed by fitting of a modern prosthesis is likely to be the best treatment for patients with Gollop-Wolfgang syndrome. We note that limb salvage treatment is an alternative in patients who opt to retain their feet and refuse amputation.
authors: Department of Orthopaedic Surgery, Saga Handicapped Children's Hospital, Saga, Japan. ssgwada@vip.saganet.ne.jp
authors: Akifusa
authors: A
authors: Wada
authors: Tomoyuki
authors: T
authors: Nakamura
authors: Toshio
authors: T
authors: Fujii
authors: Noriko
authors: N
authors: Urano
authors: Haruhisa
authors: H
authors: Yanagida
authors: Kazuyuki
authors: K
authors: Takamura
authors: Mayuki
authors: M
authors: Taketa
authors: Yutaka
authors: Y
authors: Oketani
authors: Hideaki
authors: H
authors: Kubota
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000601:surgery*; D002675:Child, Preschool; D005260:Female; D005269:Femur / Q000002:abnormalities* / Q000601:surgery*; D005360:Fibula / Q000601:surgery*; D005500:Follow-Up Studies; D006228:Hand Deformities, Congenital / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D007223:Infant; D023821:Limb Salvage / Q000379:methods*; D008297:Male; D010027:Osteotomy / Q000379:methods*; D012189:Retrospective Studies; D013977:Tibia / Q000002:abnormalities* / Q000601:surgery; D013997:Time Factors; D016896:Treatment Outcome