title: The orthodontic and surgical management of Zimmerman-Laband syndrome.
abstract: Zimmermann-Laband syndrome (ZLS) is a rare autosomal disorder characterized by gingival fibromatosis, abnormalities of the nose and/or ears, hypoplasia of the nails or terminal phalanges of the hands and feet, hyperextensibility of joints, hepatosplenomegaly, hirsutism, and intellectual disability. The characteristics of the syndrome are highly variable and complicated. This paper reports a case of ZLS and the clinical manifestations encountered in relation to the current available literature. The comprehensive management of the patient's dentition is described, focusing on the orthodontic and surgical considerations clinicians should be aware of when treating patients with the syndrome.
authors: Department of Orthodontics, University Dental Hospital, Health Park, Cardiff, United Kingdom.
authors: Teleri
authors: T
authors: Perks
authors: Hashmat
authors: H
authors: Popat
authors: Andrew J
authors: AJ
authors: Cronin
authors: Peter
authors: P
authors: Durning
authors: Roger
authors: R
authors: Maggs
mesh_terms: D000015:Abnormalities, Multiple / Q000601:surgery / Q000628:therapy*; D002508:Cephalometry / Q000379:methods; D019465:Craniofacial Abnormalities / Q000601:surgery / Q000628:therapy*; D005260:Female; D005351:Fibromatosis, Gingival / Q000601:surgery / Q000628:therapy*; D005500:Follow-Up Studies; D006228:Hand Deformities, Congenital / Q000601:surgery / Q000628:therapy*; D006801:Humans; D007180:Incisor / Q000473:pathology; D008310:Malocclusion / Q000601:surgery / Q000628:therapy*; D008312:Malocclusion, Angle Class II / Q000628:therapy; D008437:Maxilla / Q000002:abnormalities; D063166:Maxillary Osteotomy / Q000379:methods; D024343:Open Bite / Q000601:surgery / Q000628:therapy; D009971:Orthodontics, Corrective / Q000379:methods*; D056948:Orthognathic Surgical Procedures / Q000379:methods*; D010347:Patient Care Planning; D011862:Radiography, Panoramic; D063173:Retrognathia / Q000601:surgery / Q000628:therapy; D014716:Vertical Dimension; D055815:Young Adult