title: Renal rhabdomyosarcoma in a pancake kidney.
abstract: Renal rhabdomyosarcoma (RMS) is a rare pediatric tumor. Pancake kidneys are unusual anatomic anomalies resulting when both upper and lower poles of the embryonic kidney become fused. We report on a 4-year-old boy who was discovered to have a stage 4, group IV renal embryonal RMS arising from a pancake kidney with metastases to the lung, pelvis, and bone marrow. Treatment included multimodal therapy, consisting of neoadjuvant chemotherapy, complete surgical resection, and adjuvant chemotherapy. He remains in clinical remission 7 months after resection.
authors: Division of Pediatric Surgery of Cincinnati Children's Hospital Medical Center, Cincinnati, OH, USA.
authors: Ashley
authors: A
authors: Walther
authors: Nicholas G
authors: NG
authors: Cost
authors: Aaron P
authors: AP
authors: Garrison
authors: James I
authors: JI
authors: Geller
authors: Shumyle
authors: S
authors: Alam
authors: Gregory M
authors: GM
authors: Tiao
mesh_terms: D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D019046:Bone Marrow Neoplasms / Q000556:secondary / Q000628:therapy; D017024:Chemotherapy, Adjuvant; D002675:Child, Preschool; D006801:Humans; D007668:Kidney / Q000002:abnormalities*; D007680:Kidney Neoplasms / Q000473:pathology* / Q000601:surgery / Q000628:therapy*; D008175:Lung Neoplasms / Q000601:surgery / Q000628:therapy; D008297:Male; D020360:Neoadjuvant Therapy; D010386:Pelvic Neoplasms / Q000556:secondary / Q000628:therapy; D012208:Rhabdomyosarcoma / Q000556:secondary* / Q000601:surgery / Q000628:therapy*