title: Klüver-Bucy syndrome after unilateral frontotemporal resection in a child with tuberous sclerosis.
abstract: Klüver-Bucy syndrome (KBS) is a behavioral phenotype that appears most often after bilateral temporal damage. The main features of KBS are compulsion to examine objects orally, increased sexual activity, placidity, hypermetamorphosis (irresistible impulse to notice and react to everything within sight), visual agnosia, and problems with memory. It is more rarely reported in children than in adults. We present a case of KBS in a 2-year-old boy with tuberous sclerosis complex (TSC) after left frontotemporal resection for refractory epilepsy. This is the first KBS after unilateral temporal resection in a child, although it has already been reported in two adult cases. It also is the first case reported in a TSC patient.
authors: Department of Neurology, Massachusetts General Hospital, Boston, USA. susboronat@gmail.com
authors: Susana
authors: S
authors: Boronat
authors: Peter
authors: P
authors: Newberry
authors: William
authors: W
authors: Mehan
authors: Elizabeth Anne
authors: EA
authors: Thiele
authors: Ann-Christine
authors: AC
authors: Duhaime
mesh_terms: D002675:Child, Preschool; D004827:Epilepsy / Q000209:etiology / Q000601:surgery; D005625:Frontal Lobe / Q000601:surgery; D007839:Functional Laterality; D006801:Humans; D020232:Kluver-Bucy Syndrome / Q000209:etiology*; D008297:Male; D059906:Neuroimaging; D019635:Neurosurgical Procedures / Q000009:adverse effects*; D011183:Postoperative Complications / Q000209:etiology*; D013702:Temporal Lobe / Q000601:surgery; D014402:Tuberous Sclerosis / Q000150:complications
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