title: Repair of a complex thoracic aneurysm from relapsing polychondritis.
abstract: A 29-year-old female with a history of relapsing polychondritis (RP) and open repair of a proximal descending thoracic aneurysm presented with 2 areas of asymptomatic thoracic aortic aneurysmal dilatation. The patient returned 3 months later with symptomatic aneurysm expansion, and she underwent ascending aortic arch replacement. She subsequently underwent staged endovascular repair of the distal descending thoracic aorta. RP is a rare disorder with an incidence of 3.5 per million persons annually, 4% to 7% of whom develop aneurysmal disease. Because of the aneurysmal potential of this disease, it is important for vascular surgeons to be aware of its presentation and treatment. To our knowledge, this is the first reported case describing endovascular technique to treat such a patient.
authors: Division of Vascular Surgery, Rush University Medical Center, Chicago, IL 60612, USA. chad_jacobs@rush.edu
authors: Chad E
authors: CE
authors: Jacobs
authors: Robert J
authors: RJ
authors: March
authors: Peter J
authors: PJ
authors: Hunt
authors: Aksim G
authors: AG
authors: Rivera
authors: Sherry
authors: S
authors: Cavanagh
authors: Walter J
authors: WJ
authors: McCarthy
mesh_terms: D000328:Adult; D017545:Aortic Aneurysm, Thoracic / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D001027:Aortography / Q000379:methods; D019917:Blood Vessel Prosthesis Implantation; D057510:Endovascular Procedures; D005260:Female; D006801:Humans; D011081:Polychondritis, Relapsing / Q000150:complications*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
keywords: endovascular repair; relapsing polychondritis; thoracic aortic aneurysm