title: Palmoplantar contractures in childhood: a rare complication of vascular Ehlers-Danlos syndrome.
abstract: Although catastrophic vascular complications in vascular Ehlers-Danlos Syndrome (EDS) are well recognized, other complications such as flexion contractures and tendon nodules are rarely reported and poorly characterized. We report a young man with vascular EDS, who developed flexion contractures and tendon nodules, causing considerable disability. Limited management strategies are available for these complications, which have continued to prove a challenge to management.
authors.affiliation: Department of Dermatology, Royal Victoria Infirmary, Newcastle upon Tyne, UK. amy.foulkes@manchester.ac.uk
authors.forename: A C
authors.initials: AC
authors.lastname: Foulkes
authors.forename: R
authors.initials: R
authors.lastname: Pollitt
authors.forename: G
authors.initials: G
authors.lastname: Sobey
authors.forename: F M
authors.initials: FM
authors.lastname: Pope
authors.forename: A E M
authors.initials: AE
authors.lastname: Taylor
mesh_terms: D000293:Adolescent; D003286:Contracture / Q000209:etiology*; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D005531:Foot Deformities, Acquired / Q000209:etiology*; D006227:Hand Deformities, Acquired / Q000209:etiology*; D006801:Humans; D008297:Male