title: Normalisation of left ventricular systolic function after change from VVI pacing to biventricular pacing in a child with congenital complete atrioventricular block, long-QT syndrome, and congenital muscular dystrophy: a 10-year follow-up.
abstract: Development of dilated cardiomyopathy in patients with congenital complete atrioventricular block with or without pacemaker is well described. We report a case of dilated cardiomyopathy in a child with congenital complete atrioventricular block, long-QT syndrome, and VVI pacemaker. Temporary pacing in the right ventricular outflow tract demonstrated a 63% increase in cardiac output. After change to biventricular DDD pacing, left ventricular systolic function and diastolic dimensions normalised.
authors.affiliation: 1 Department of Disease Systems Biology, University of Copenhagen, Denmark.
authors.forename: Sabrina G
authors.initials: SG
authors.lastname: Ellesøe
authors.affiliation: 2 Deptartment of Cardiology, Rigshospitalet, Copenhagen, Denmark.
authors.forename: Jesper I
authors.initials: JI
authors.lastname: Reimers
authors.affiliation: 3 Deptartment of Cardio Thoracic Surgery, Rigshospitalet, Copenhagen, Denmark.
authors.forename: Henrik Ø
authors.initials: HØ
authors.lastname: Andersen
mesh_terms: D058406:Cardiac Resynchronization Therapy; D002311:Cardiomyopathy, Dilated / Q000150:complications / Q000503:physiopathology*; D005500:Follow-Up Studies; D006327:Heart Block / Q000150:complications / Q000151:congenital* / Q000503:physiopathology / Q000628:therapy; D006801:Humans; D007231:Infant, Newborn; D008133:Long QT Syndrome / Q000150:complications / Q000503:physiopathology*; D008297:Male; D009136:Muscular Dystrophies / Q000150:complications / Q000503:physiopathology*; D020127:Recovery of Function; D013599:Systole; D013997:Time Factors; D016277:Ventricular Function, Left