title: [Quality of life in Hungarian patients with cystic fibrosis].
abstract: BACKGROUND
  Cystic fibrosis is a progressive multisystemic disease which affects the quality of life of patients.
  
  
  OBJECTIVE
  The aim of the study was to evaluate quality of life in Hungarian patients with cystic fibrosis.
  
  
  METHODS
  Validated Hungarian translation of The Cystic Fibrosis Questionnaire - Revised was used to measure quality of life. Clinical severity was determined on the basis of Shwachman-Kulczycki score. Lung function was measured using spirometry.
  
  
  RESULTS
  59 patients were included from five centres in Hungary. The relationships between 8-13 year-old children self-report and parent proxy report was 0.77 (p<0.001) in physical functioning, 0.07 (p<0.001) in emotional functioning, 0.51 (p<0.001) in eating, 0.21 (p<0.001) in treatment burden, 0.54 (p<0.001) in body image, 0.49 (p<0.001) in respiratory symptoms and 0.40 (p<0.001) in digestive symptoms domains.
  
  
  CONCLUSIONS
  In contrast to physical domains weak correlations were observed between answers obtained from children and their parents in psychosocial domains. The perception of both patients and their parents should be assessed when measuring quality of life in paediatric patients with cystic fibrosis.
authors.affiliation: Semmelweis Egyetem Egyetemi Gyógyszertár Gyógyszerügyi Szervezési Intézet Budapest Üllői út 86. 1089. rekabodnar@ymail.com
authors.forename: Réka
authors.initials: R
authors.lastname: Bodnár
authors.forename: Klára
authors.initials: K
authors.lastname: Holics
authors.forename: Rita
authors.initials: R
authors.lastname: Ujhelyi
authors.forename: László
authors.initials: L
authors.lastname: Kádár
authors.forename: Lajos
authors.initials: L
authors.lastname: Kovács
authors.forename: Katalin
authors.initials: K
authors.lastname: Bolbás
authors.forename: Gyöngyi
authors.initials: G
authors.lastname: Székely
authors.forename: Kálmán
authors.initials: K
authors.lastname: Gyurkovits
authors.forename: Enikő
authors.initials: E
authors.lastname: Sólyom
authors.forename: Agnes
authors.initials: A
authors.lastname: Mészáros
mesh_terms: D000293:Adolescent; D000328:Adult; D000367:Age Factors; D002648:Child; D002675:Child, Preschool; D003550:Cystic Fibrosis / Q000503:physiopathology* / Q000523:psychology*; D005260:Female; D006304:Health Status; D006801:Humans; D006814:Hungary; D008176:Lung Volume Measurements; D008297:Male; D010290:Parents; D012123:Pulmonary Ventilation; D011788:Quality of Life; D013147:Spirometry; D011795:Surveys and Questionnaires; D055815:Young Adult