title: Caesarean section in a parturient with Carpenter syndrome and corrected Tetralogy of Fallot.
abstract: Carpenter syndrome is an extremely rare congenital disorder characterized by craniofacial malformations, syndactyly, cardiac defects and obesity. Even after surgical correction of cardiac abnormalities, intrapartum care of a parturient with this condition can be challenging because of progression of residual cardiac defects compounded by the haemodynamic changes of pregnancy. We describe the anaesthetic management for caesarean section of a parturient with Carpenter syndrome and corrected Tetralogy of Fallot. Additional complicating issues included worsening cardiac function, asthma, needle-phobia and osteoarthritis.
authors.affiliation: Nuffield Department of Anaesthetics, John Radcliffe Hospital, Oxford, UK. manishb13@yahoo.com
authors.forename: M
authors.initials: M
authors.lastname: Bhardwaj
authors.forename: C
authors.initials: C
authors.lastname: Grange
mesh_terms: D000168:Acrocephalosyndactylia / Q000150:complications*; D000769:Anesthesia, Inhalation; D000773:Anesthesia, Obstetrical; D001034:Apgar Score; D002585:Cesarean Section / Q000379:methods*; D004452:Echocardiography; D005260:Female; D006801:Humans; D016343:Monitoring, Intraoperative; D009765:Obesity / Q000150:complications; D010149:Postoperative Pain / Q000188:drug therapy; D010347:Patient Care Planning; D010348:Patient Care Team; D011182:Postoperative Care; D011247:Pregnancy; D011256:Pregnancy Outcome; D011665:Pulmonary Valve Insufficiency / Q000150:complications / Q000000981:diagnostic imaging; D013771:Tetralogy of Fallot / Q000503:physiopathology* / Q000601:surgery; D055815:Young Adult