title: Unusual variant of scimitar syndrome associated with an absent right pulmonary artery, stenosis of the inferior vena cava, hemi-azygous continuation and the VACTERL association.
abstract: We report on a two-month-old infant with an unusual form of scimitar syndrome, associated with an absent right pulmonary artery, obstructed inferior vena cava, hemi-azygous continuation and the VACTERL association. The infant posed a major management problem and eventually died from a lower respiratory tract infection.
authors.affiliation: Steve Biko Academic Hospital and Department of Paediatric Cardiology, University of Pretoria, South Africa. fari.takawira@up.ac.za
authors.forename: Farirai F
authors.initials: FF
authors.lastname: Takawira
authors.forename: Fareed
authors.initials: F
authors.lastname: Omar
mesh_terms: D000015:Abnormalities, Multiple; D001003:Anal Canal / Q000002:abnormalities*; D001401:Azygos Vein / Q000002:abnormalities*; D003251:Constriction, Pathologic; D004562:Electrocardiography; D004947:Esophagus / Q000002:abnormalities*; D017809:Fatal Outcome; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D007223:Infant; D007668:Kidney / Q000002:abnormalities*; D017880:Limb Deformities, Congenital / Q000175:diagnosis / Q000628:therapy; D010690:Phlebography; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging; D012587:Scimitar Syndrome / Q000175:diagnosis / Q000628:therapy; D013131:Spine / Q000002:abnormalities*; D014132:Trachea / Q000002:abnormalities*; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging