title: Double-chambered right ventricle: a review.
abstract: A double-chambered right ventricle is a rare heart defect in which the right ventricle is separated into a high-pressure proximal and low-pressure distal chamber. This defect is considered to be congenital and typically presents in infancy or childhood but has been reported to present rarely in adults. It can be caused by the presence of anomalous muscle tissue, hypertrophy of the endogenous trabecular bands, or an aberrant moderator band; all of which will typically result in progressive obstruction of the outflow tract. In this paper, we will discuss the general anatomy of the right ventricle, the relevant embryology of the heart, and the presentation, diagnosis, and treatment of a double-chambered right ventricle.
authors.affiliation: Department of Anatomical Sciences, School of Medicine, St George's University, Grenada, West Indies. Electronic address: mloukas@sgu.edu.
authors.forename: Marios
authors.initials: M
authors.lastname: Loukas
authors.forename: Brian
authors.initials: B
authors.lastname: Housman
authors.forename: Christa
authors.initials: C
authors.lastname: Blaak
authors.forename: Sarah
authors.initials: S
authors.lastname: Kralovic
authors.forename: R Shane
authors.initials: RS
authors.lastname: Tubbs
authors.forename: Robert H
authors.initials: RH
authors.lastname: Anderson
mesh_terms: D017023:Coronary Angiography; D018450:Disease Progression; D018618:Echocardiography, Doppler, Color; D006330:Heart Defects, Congenital / Q000150:complications / Q000473:pathology* / Q000503:physiopathology / Q000628:therapy; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D006984:Hypertrophy; D008279:Magnetic Resonance Imaging; D011237:Predictive Value of Tests; D011379:Prognosis; D016278:Ventricular Function, Right; D014694:Ventricular Outflow Obstruction / Q000209:etiology; D017725:Ventricular Pressure
keywords: Anomalous muscle band; Congenital heart disease; Crista supraventricularis; Heart defect; Moderator band; Septoparietal trabeculations; Subinfundibular pulmonary stenosis