title: Diverse manifestations and management options in Klippel-Trenaunay syndrome: a single centre 10-year experience.
abstract: Klippel-Trenaunay syndrome is a well-known conglomeration of capillary malformations, bony or soft tissue hypertrophy, and abnormal deep or superficial veins. Although it generally presents with grossly enlarged limbs, it can present with more serious features like haematuria, haematochezia, and seizures. This retrospective study included patients admitted with the diagnosis of Klippel-Trenaunay syndrome in this institute from 2001-2010. The patients' demographic data, clinical features, associated findings, and treatments given were tabulated. A total of 19 patients were included in the study. Two patients presented with haematocezia and had to undergo bowel resection. Five presented with bleeding and ulceration. Debulking surgery was done in three of them. Patients also presented with abdominal distension, jaundice, seizures, and haematuria. Although the common presentation of varicose veins was treated with sclerotherapy, the treatment was tailored to each patient. Klippel-Trenaunay syndrome is a multifaceted disorder which can manifest in a number of different ways. These features may be missed by an unwary plastic surgeon treating them only for the limb hypertrophy.
authors.affiliation: Plastic and Reconstructive Surgery, Christian Medical College Vellore, India. drsreekarh@yahoo.com
authors.forename: Harinatha
authors.initials: H
authors.lastname: Sreekar
authors.forename: Sandeep
authors.initials: S
authors.lastname: Dawre
authors.forename: Kiran S
authors.initials: KS
authors.lastname: Petkar
authors.forename: Rahul B
authors.initials: RB
authors.lastname: Shetty
authors.forename: Shashank
authors.initials: S
authors.lastname: Lamba
authors.forename: Sukriya
authors.initials: S
authors.lastname: Naik
authors.forename: Ashish K
authors.initials: AK
authors.lastname: Gupta
mesh_terms: D000293:Adolescent; D000328:Adult; D000367:Age Factors; D001165:Arteriovenous Malformations / Q000000981:diagnostic imaging / Q000601:surgery*; D002648:Child; D002675:Child, Preschool; D015331:Cohort Studies; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000175:diagnosis / Q000601:surgery; D006503:Hepatic Veins / Q000000981:diagnostic imaging / Q000601:surgery; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis* / Q000628:therapy*; D008206:Lymphatic Diseases / Q000175:diagnosis / Q000628:therapy; D018810:Magnetic Resonance Angiography; D008297:Male; D008875:Middle Aged; D011379:Prognosis; D011859:Radiography; D012189:Retrospective Studies; D018570:Risk Assessment; D015911:Sclerotherapy / Q000379:methods; D012720:Severity of Illness Index; D012737:Sex Factors; D016896:Treatment Outcome; D014648:Varicose Veins / Q000503:physiopathology / Q000628:therapy*; D055815:Young Adult