title: Cogan's syndrome: achievement of complete resolution of auditory deficit with steroids.
abstract: Cogan's syndrome is a rare inflammatory disorder predominantly affecting ocular and audiovestibular apparatus. The typical ocular picture is that of a non-syphilitic interstitial keratitis, while audiovestibular features resemble Meniere's disease. The hearing deficit often does not adequately respond to systemic steroids, which are the mainstay of therapy. Cochlear implants may ameliorate this deficit, but may not be readily available because of financial constraints in the Indian subcontinent. A high index of suspicion and multispecialty coordination will help in the early initiation of therapy and reduce long-term morbidity. We report a case of this rare entity where the recovery of deficits was dramatic on initiation of high-dose steroids.
authors.affiliation: Department of Medicine, Government Medical College and Hospital, Chandigarh, India.
authors.forename: Pritam
authors.initials: P
authors.lastname: Singh
authors.forename: Monica
authors.initials: M
authors.lastname: Gupta
authors.forename: S S
authors.initials: SS
authors.lastname: Lehl
authors.forename: Kamal
authors.initials: K
authors.lastname: Singh
mesh_terms: D000293:Adolescent; D019929:Cochlear Implantation; D003054:Cochlear Implants; D055952:Cogan Syndrome / Q000188:drug therapy*; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000188:drug therapy* / Q000209:etiology; D006801:Humans; D013256:Steroids / Q000627:therapeutic use*; D016896:Treatment Outcome; D014722:Vestibule, Labyrinth
chemical_list: D013256:Steroids