title: Congenital pulmonary alveolar proteinosis.
abstract: Pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by pulmonary surfactant accumulation within the alveolar spaces. It occurs with a reported prevalence of 0.1 per 100,000 individuals. Two clinically different pediatric types have been defined as congenital PAP which is fatal and a late-onset PAP which is similar to the adult form and less severe. The clinical course of PAP is variable, ranging from spontaneous remission to respiratory failure. Whole-lung lavage is the current standard treatment for PAP patients. We report a new congenital case of PAP.
authors.affiliation: Pediatrics Department, University of Monastir, Faculty of Medicine, Monastir 5000, Tunisia.
authors.forename: Saber
authors.initials: S
authors.lastname: Hammami
authors.forename: Khaled
authors.initials: K
authors.lastname: Harrathi
authors.forename: Khaled
authors.initials: K
authors.lastname: Lajmi
authors.forename: Samir
authors.initials: S
authors.lastname: Hadded
authors.forename: Chebil
authors.initials: C
authors.lastname: Ben Meriem
authors.forename: Mohamed Néji
authors.initials: MN
authors.lastname: Guédiche