title: Fatal Blastoid Variant Mantle Cell Lymphoma in a Patient with Sjögren's Syndrome.
abstract: Primary Sjögren's syndrome (pSS) is an autoimmune disorder of the exocrine glands presenting with progressive ocular and oral dryness, parotid gland enlargement, and often with extraglandular manifestations. In this group of patients the risk of development of non-Hodgkin's lymphoma is 16-fold compared to healthy population, mainly of the MALT lymphoma type. This case reports a 52-year-old woman with pSS developing a progressively growing mass at face and neck compatible with blastoid variant mantle cell lymphoma and a fatal outcome.
authors.affiliation: Rheumatology Unit, Fundación Valle del Lili, ICESI University, Cali, Colombia.
authors.forename: Fabio
authors.initials: F
authors.lastname: Bonilla-Abadía
authors.forename: Manuel A
authors.initials: MA
authors.lastname: Pérez
authors.forename: Evelyn
authors.initials: E
authors.lastname: Muñoz-Buitrón
authors.forename: Joaquín D
authors.initials: JD
authors.lastname: Rosales
authors.forename: Carlos A
authors.initials: CA
authors.lastname: Cañas
authors.forename: Gabriel J
authors.initials: GJ
authors.lastname: Tobón