title: Role of home monitoring in children with implantable cardioverter defibrillators for Brugada syndrome.
abstract: OBJECTIVE
  Implementation of remote home monitoring systems (HM) in clinical practice has become undoubtedly an added value for all patients with implantable cardiac devices. The aim of this study was to investigate the impact of HM in a population of children with Brugada syndrome (BS) who received an implantable cardioverter defibrillator (ICD).
  
  
  RESULTS
  Eleven children (age between 6 months and 18 years) implanted with an ICD were followed either by means of HM and with conventional in-hospital visits in our centre. Alerts and/or device-related clinical events were recorded, analysed, and subsequent clinical decisions were made if needed. During an average observation time of 26 months a total of 16 relevant alerts (13 pre-emptive alerts) were recorded in seven patients of our population. One patient experienced appropriate therapies for life-threatening ventricular arrhythmias. Three patients experienced inappropriate therapies due to supraventricular tachycardia and lead dislodgement. By means of HM two patients were discovered to have lead problems because of dislodgement or lead fracture. Mean anticipation of treatment based on the alerts was 76 ± 59 days.
  
  
  CONCLUSIONS
  Remote monitoring systems substantially improve the proper management of children with BS.
authors.affiliation: Heart Rhythm Management Centre, Cardiovascular Division, Universitair Ziekenhuis Brussel, Vrije Universiteit Brussel, Laarbeeklaan 101, 1090 Brussels, Belgium. carlodeasmundis@me.com
authors.forename: Carlo
authors.initials: C
authors.lastname: de Asmundis
authors.forename: Danilo
authors.initials: D
authors.lastname: Ricciardi
authors.forename: Mehdi
authors.initials: M
authors.lastname: Namdar
authors.forename: Gian-Battista
authors.initials: GB
authors.lastname: Chierchia
authors.forename: Andrea
authors.initials: A
authors.lastname: Sarkozy
authors.forename: Pedro
authors.initials: P
authors.lastname: Brugada
mesh_terms: D000293:Adolescent; D053840:Brugada Syndrome / Q000175:diagnosis* / Q000517:prevention & control*; D002648:Child; D002675:Child, Preschool; D017147:Defibrillators, Implantable; D003936:Diagnosis, Computer-Assisted / Q000379:methods*; D015716:Electrocardiography, Ambulatory / Q000379:methods*; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D017216:Telemedicine / Q000379:methods*; D013813:Therapy, Computer-Assisted / Q000379:methods*; D016896:Treatment Outcome
keywords: Brugada syndrome; Home monitoring; ICD; Telemedicine