title: Immunoglobulin G4-related sclerosing disease invading the trachea and superior vena cava in mediastinum.
abstract: It is well known that immunoglobulin G4 (IgG4)-related sclerosing disease usually occurs in the pancreas, bile duct and gall bladder, but not in the mediastinum, trachea or superior vena cava (SVC). In this case, a patient underwent mediastinal mass excision and trachea resection and repair for a mediastinal and intratracheal mass 15 years ago. This mass was diagnosed postoperatively as an inflammatory pseudotumour (plasma cell granuloma). Subsequently, a mass was found to have recurred in the SVC. We performed a mass excision and innominate vein to the right atrium auricle bypass operation. The mass was diagnosed as IgG4-related sclerosing disease. This patient is now disease and recurrence free.
authors.affiliation: Department of Thoracic and Cardiovascular Surgery, School of Medicine, Keimyung University, Dae-gu, Republic of Korea.
authors.forename: Dongsub
authors.initials: D
authors.lastname: Noh
authors.forename: Chang-Kwon
authors.initials: CK
authors.lastname: Park
authors.forename: Sun-Young
authors.initials: SY
authors.lastname: Kwon
mesh_terms: D000368:Aged; D005260:Female; D006801:Humans; D007074:Immunoglobulin G; D008479:Mediastinal Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D008482:Mediastinum / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D011859:Radiography; D012598:Sclerosis / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D014132:Trachea / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D014683:Vena Cava, Superior / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery
chemical_list: D007074:Immunoglobulin G
keywords: Immunoglobulin G4-related sclerosing disease; Superior vena cava; Trachea