title: Inherited epidermolysis bullosa: clinical and therapeutic aspects.
abstract: Inherited epidermolysis bullosa (EB) is a heterogeneous group of genetic disorders that present with skin and, in some cases, mucosal fragility, predisposing patients to the development of blisters and/or erosions after minimal trauma or friction. Children with a recurrent history of these kinds of lesions or neonates that present them in the absence of another reasonable explanation should be investigated. Diagnosis must be based on clinical and histopathological findings. To date, management of inherited EB basically consists in avoiding traumas that trigger lesions, as well as preventing infection and facilitating healing of the wounds with the systematic use of bandages.
authors.affiliation: Federal University of Bahia (UFBA), Salvador, BA, Brazil.
authors.forename: Vanessa Lys Simas Yamakawa
authors.initials: VL
authors.lastname: Boeira
authors.forename: Erica Sales
authors.initials: ES
authors.lastname: Souza
authors.forename: Bruno de Oliveira
authors.initials: Bde O
authors.lastname: Rocha
authors.forename: Pedro Dantas
authors.initials: PD
authors.lastname: Oliveira
authors.forename: Maria de Fátima Santos Paim de
authors.initials: Mde F
authors.lastname: Oliveira
authors.forename: Vitória Regina Pedreira de Almeida
authors.initials: VR
authors.lastname: Rêgo
authors.forename: Ivonise
authors.initials: I
authors.lastname: Follador
mesh_terms: D001458:Bandages; D004820:Epidermolysis Bullosa / Q000145:classification / Q000235:genetics / Q000473:pathology / Q000628:therapy; D006801:Humans; D012867:Skin / Q000473:pathology; D014945:Wound Healing