title: Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis -- case report.
abstract: Behçet's disease is a chronic inflammatory disease of unknown aetiology, characterized by recurrent oral and genital aphthous ulcerations, uveitis, skin lesions and other multisystem affections associated with vasculitis. Different types of vessels, predominantly veins, can be affected in Behçet's disease. The frequency of vascular lesions in Behçet's disease, such as superficial and deep venous thromboses, arterial aneurysms and occlusions, ranges between 7-29%. Budd-Chiari syndrome is a rare and serious complication of Behçet's disease and implies thrombosis of the hepatic veins and/or the intrahepatic or suprahepatic inferior vena cava. We report a case of a 25-year-old man with Behçet's disease that developed Budd-Chiari syndrome. The correlation of dermatological, pathological and imaging studies confirmed the diagnosis.
authors.affiliation: School of Medicine, Federal University of Pará, Belém, PA, Brazil. marayabittencourt@hotmail.com
authors.forename: Maraya de Jesus Semblano
authors.initials: Mde J
authors.lastname: Bittencourt
authors.forename: Carolina Moraes
authors.initials: CM
authors.lastname: Dias
authors.forename: Thaiane Lima
authors.initials: TL
authors.lastname: Lage
authors.forename: Renata Silva
authors.initials: RS
authors.lastname: Barros
authors.forename: Otávio Augusto Gomes
authors.initials: OA
authors.lastname: Paz
authors.forename: Waldonio de Brito
authors.initials: Wde B
authors.lastname: Vieira
mesh_terms: D000328:Adult; D001528:Behcet Syndrome / Q000150:complications*; D006502:Budd-Chiari Syndrome / Q000209:etiology*; D017809:Fatal Outcome; D005832:Genital Diseases, Male / Q000209:etiology / Q000473:pathology; D006801:Humans; D008297:Male; D012883:Skin Ulcer / Q000209:etiology / Q000473:pathology