title: [Management of a child with Swyer-James syndrome who underwent flexible bronchoscopy under general anesthesia].
abstract: Swyer-James syndrome (SJS) is a rare syndrome characterized by hyperlucency of one or more lobes of the unilateral lung and decreased pulmonary vascularity which is considered to be secondary to the childhood obliterative bronchiolitis. We report anesthetic management of a girl with SJS who underwent flexible bronchoscopy. A 15-year-old girl weighing 47 kg was referred to our hospital with suspected SJS. She had a history of bronchiolitis in early childhood. On admission, chest radiograph showed a hyperlucent lung with diminished pulmonary vasculature on the left lung. Pulmonary function test revealed slightly restrictive pattern (%VC 69.3%, %FEVa1.0 77.9%). Ventilation and perfusion scanning demonstrated the markedly decreased ventilation (left : right, 33 : 67) and perfusion (left : right, 10 : 90) of the left lung. To rule out the foreign body and bronchial stenosis, flexible bronchoscopy under general anesthesia was planned. Anesthesia was induced with propofol and maintained with propofol and remifentanil. Spontaneous respiration was maintained by using laryngeal mask airway to prevent the pressure alveolar damage by positive pressure ventilation. Flexible bronchoscopy was performed safely by using topical laryngeal lidocaine administration and additional bolus of propofol. Her postoperative course was uncomplicated and she was discharged on the following day.
authors.affiliation: Department of Anesthesia and Intensive Care, Osaka Medical Center and Research Institute for Maternal and Child Health, Izumi 594-1101.
authors.forename: Aiko
authors.initials: A
authors.lastname: Oyamaguchi
authors.forename: Kazuya
authors.initials: K
authors.lastname: Tachibana
authors.forename: Muneyuki
authors.initials: M
authors.lastname: Takeuchi
authors.forename: Keiko
authors.initials: K
authors.lastname: Kinouchi
mesh_terms: D000293:Adolescent; D000768:Anesthesia, General / Q000379:methods*; D001980:Bronchi / Q000473:pathology; D001999:Bronchoscopy / Q000379:methods*; D005260:Female; D006801:Humans; D017214:Laryngeal Masks; D019568:Lung, Hyperlucent / Q000175:diagnosis* / Q000473:pathology*; D012119:Respiration