title: [Congenital bile duct hypoplasia (Alagille-Watson syndrome)--a rare cause of biliary cirrhosis in adults].
abstract: A case of a rare hereditary disease, Alagille-Watson syndrome, is reported. It most frequently affects liver and cardiovascular system which leads to biliary cirrhosis and cardiovascular catastrophe in young patients. Pathogenesis and clinical variants of the disease are described.
authors.forename: É Z
authors.initials: ÉZ
authors.lastname: Burnevich
authors.forename: I A
authors.initials: IA
authors.lastname: Lopatina
authors.forename: E A
authors.initials: EA
authors.lastname: Arion
authors.forename: A V
authors.initials: AV
authors.lastname: Odintsov
mesh_terms: D000328:Adult; D016738:Alagille Syndrome / Q000150:complications / Q000188:drug therapy / Q000473:pathology*; D005260:Female; D006801:Humans; D008105:Liver Cirrhosis, Biliary / Q000188:drug therapy / Q000209:etiology* / Q000473:pathology; D055815:Young Adult