title: Extrarenal testicular Wilms' tumor in a 3-year-old child.
abstract: We report an extremely rare case of extrarenal testicular Wilms' tumor in a 3-year-old boy with intrabdominal undescended left testis. The patient was admitted because of pain and vomiting, with evidence of a huge abdominal mass. At surgery a large tumor arising from the intrabdominal testis was found. Histology showed the classical triphasic Wilms' tumor elements: epithelial, mesenchymal and blastemal areas. Extrarenal Wilms' tumors account for only 3% of all Wilms' tumors and just -100 cases have been reported in literature. Testicular origin is anecdotic. We present histomorphological, histogenetic, clinical, diagnostic, prognostic and therapeutic features of this rare tumor.
authors.affiliation: Department of Pediatric Surgery, FONDAZIONE IRCCS Ca' Granda Ospedale Maggiore Policlinico, Via Commenda 10, 20122 Milano, Italy. chped.articles@gmail.com
authors.forename: A
authors.initials: A
authors.lastname: Morandi
authors.forename: A M
authors.initials: AM
authors.lastname: Fagnani
authors.forename: L
authors.initials: L
authors.lastname: Runza
authors.forename: G
authors.initials: G
authors.lastname: Farris
authors.forename: A
authors.initials: A
authors.lastname: Zanini
authors.forename: F
authors.initials: F
authors.lastname: Parolini
authors.forename: G
authors.initials: G
authors.lastname: Bassi
authors.forename: V
authors.initials: V
authors.lastname: Gentilino
authors.forename: F
authors.initials: F
authors.lastname: Macchini
authors.forename: R
authors.initials: R
authors.lastname: Arnoldi
authors.forename: E
authors.initials: E
authors.lastname: Leva
mesh_terms: D002675:Child, Preschool; D003287:Contrast Media; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D011856:Radiographic Image Enhancement / Q000379:methods; D013736:Testicular Neoplasms / Q000000981:diagnostic imaging / Q000601:surgery*; D014057:Tomography, X-Ray Computed / Q000379:methods; D018608:Ultrasonography, Doppler / Q000379:methods; D009396:Wilms Tumor / Q000000981:diagnostic imaging / Q000601:surgery*
chemical_list: D003287:Contrast Media