title: Erythrocytosis in children and adolescents-classification, characterization, and consensus recommendations for the diagnostic approach.
abstract: During recent years, the increasing knowledge of genetic and physiological changes in polycythemia vera (PV) and of different types of congenital erythrocytosis has led to fundamental changes in recommendations for the diagnostic approach to patients with erythrocytosis. Although widely accepted for adult patients this approach may not be appropriate with regard to children and adolescents affected by erythrocytosis. The "congenital erythrocytosis" working group established within the framework of the MPN&MPNr-EuroNet (COST action BM0902) addressed this question in a consensus finding process and developed a specific algorithm for the diagnosis of erythrocytosis in childhood and adolescence which is presented here.
authors.affiliation: Department of Pediatrics and Adolescent Medicine, University Medical Center Ulm, Ulm, Germany.
authors.forename: Holger
authors.initials: H
authors.lastname: Cario
authors.forename: Mary Frances
authors.initials: MF
authors.lastname: McMullin
authors.forename: Celeste
authors.initials: C
authors.lastname: Bento
authors.forename: Dagmar
authors.initials: D
authors.lastname: Pospisilova
authors.forename: Melanie J
authors.initials: MJ
authors.lastname: Percy
authors.forename: Kais
authors.initials: K
authors.lastname: Hussein
authors.forename: Jiri
authors.initials: J
authors.lastname: Schwarz
authors.forename: Maria
authors.initials: M
authors.lastname: Aström
authors.forename: Sylvie
authors.initials: S
authors.lastname: Hermouet
mesh_terms: D000293:Adolescent; D000328:Adult; D000465:Algorithms; D002648:Child; D006801:Humans; D011086:Polycythemia / Q000145:classification* / Q000175:diagnosis*
keywords: adolescents; children; congenital erythrocytosis; diagnostic algorithm; polycythemia vera