title: Incidental (malignancy) and coincidental (idiopathic polydactylous longitudinal erythronychia) conditions in patients with segmental neurofibromatosis.
abstract: Segmental neurofibromatosis (SNF) is an uncommon presentation of neurofibromatosis type 1 (NF-1). Although patients with SNF are at a lower risk for developing NF-l-associated complications, the estimated occurrence of related malignancies may be approaching the frequency observed in patients with NF-1. Idiopathic polydactylous longitudinal erythronychia also may be associated with SNF, though the frequency of this association remains to be determined.
authors.affiliation: Department of Dermatology, University of Texas MD Anderson Cancer Center, Houston, USA. mitehead@gmail.com
authors.forename: Philip R
authors.initials: PR
authors.lastname: Cohen
mesh_terms: D000310:Adrenal Gland Neoplasms / Q000453:epidemiology / Q000209:etiology / Q000473:pathology; D006801:Humans; D009260:Nail Diseases / Q000209:etiology / Q000473:pathology*; D009369:Neoplasms / Q000453:epidemiology / Q000209:etiology / Q000473:pathology*; D017253:Neurofibromatoses / Q000150:complications / Q000473:pathology*