title: Surgery for congenital aortic stenosis in children with left ventricular noncompaction.
abstract: Left ventricular noncompaction (LVNC) is an uncommon genetic disorder of endocardial morphogenesis, which carries a high mortality from heart failure or sudden cardiac death. This condition is often first diagnosed in adults, but it has also been described in children with other cardiac anomalies. We discuss the management of a 10-year-old female with congenital aortic stenosis associated with LVNC.
authors.affiliation: Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing, China.
authors.forename: Chao
authors.initials: C
authors.lastname: Wang
authors.forename: Qi
authors.initials: Q
authors.lastname: Miao
authors.forename: Xingrong
authors.initials: X
authors.lastname: Liu
authors.forename: Xiaofeng
authors.initials: X
authors.lastname: Li
mesh_terms: D000818:Animals; D001020:Aortic Stenosis, Subvalvular / Q000151:congenital* / Q000000981:diagnostic imaging / Q000601:surgery*; D001021:Aortic Valve / Q000601:surgery*; D058385:Cardiac Valve Annuloplasty / Q000379:methods*; D002417:Cattle; D002648:Child; D017548:Echocardiography, Transesophageal; D005260:Female; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging; D006801:Humans; D007432:Intraoperative Period; D010496:Pericardium / Q000637:transplantation; D016896:Treatment Outcome; D014656:Vascular Surgical Procedures / Q000379:methods; D018487:Ventricular Dysfunction, Left / Q000151:congenital* / Q000000981:diagnostic imaging