title: A 17-year-old girl with Klippel-Weber syndrome complicated with a pulmonary thromboembolism and RV thrombus.
abstract: A 17-year-old girl with multiple areas of skin hemangiomas that had been present since birth was referred to our institution complaining of sudden onset of dyspnea. Enhanced CT demonstrated a pulmonary thromboembolism and transthoracic echocardiogram showed a thrombus-like echo in the right ventricle. CT further revealed thrombi in the inferior vena cava (IVC) and peripheral vein. The thrombi, especially those in the RV, were highly life-threatening; therefore, immediate thrombectomy was performed and an IVC filter was placed. Because no major complications occurred, the patient was discharged 34 days after admission. In such young women, carefully using anticoagulation therapy and planning pregnancy are recommended.
authors.affiliation: Division of Cardiology, Nippon Medical School Chiba Hokusoh Hospital, Japan.
authors.forename: Toshimasa
authors.initials: T
authors.lastname: Yamada
authors.forename: Takayoshi
authors.initials: T
authors.lastname: Ohba
authors.forename: Teppei
authors.initials: T
authors.lastname: Yamamoto
authors.forename: Nakahisa
authors.initials: N
authors.lastname: Kimata
authors.forename: Toru
authors.initials: T
authors.lastname: Inami
authors.forename: Ryo
authors.initials: R
authors.lastname: Munakata
authors.forename: Daisuke
authors.initials: D
authors.lastname: Murakami
authors.forename: Mitsunori
authors.initials: M
authors.lastname: Maruyama
authors.forename: Masamichi
authors.initials: M
authors.lastname: Takano
authors.forename: Chikao
authors.initials: C
authors.lastname: Ibuki
authors.forename: Noritake
authors.initials: N
authors.lastname: Hata
authors.forename: Yoshihiko
authors.initials: Y
authors.lastname: Seino
authors.forename: Kyoichi
authors.initials: K
authors.lastname: Mizuno
mesh_terms: D000293:Adolescent; D000925:Anticoagulants / Q000627:therapeutic use; D003328:Coronary Thrombosis / Q000150:complications* / Q000628:therapy; D005260:Female; D006352:Heart Ventricles; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D011247:Pregnancy; D011248:Pregnancy Complications / Q000628:therapy; D011655:Pulmonary Embolism / Q000150:complications* / Q000628:therapy; D017131:Thrombectomy; D016306:Vena Cava Filters; D014682:Vena Cava, Inferior; D020246:Venous Thrombosis / Q000150:complications / Q000628:therapy
chemical_list: D000925:Anticoagulants