title: Left main coronary artery atresia and associated cardiac defects: report on concomitant surgical treatment.
abstract: A 9-year-old boy with congenital atresia of the left main coronary artery underwent myocardial revascularization. Coarctation of the aorta and ventricular septal defect were diagnosed at the age of 1 year. At age 7 years, the child presented with syncope while exercising. Preoperative evaluation included cardiac catheterization which revealed the unexpected finding of congenital atresia of the left main coronary artery with origin of the circumflex artery from the right coronary artery. Surgical correction included myocardial revascularization by means of left internal mammary artery graft to the anterior descending coronary artery, coarctation resection, and ventricular septal defect repair. The patient recovered uneventfully. We report the details of this extremely rare case with successful concomitant surgical management of the congenital coronary artery anomaly and the associated structural heart disease.
authors.affiliation: Heart Institute, University of São Paulo, São Paulo, Brazil.
authors.forename: Marcelo
authors.initials: M
authors.lastname: Jatene
authors.forename: Ignacio
authors.initials: I
authors.lastname: Juaneda
authors.forename: Rogerio Dos Anjos
authors.initials: Rdos A
authors.lastname: Miranda
authors.forename: Rafaella
authors.initials: R
authors.lastname: Gato
authors.forename: Miguel Lorenzo Barbero
authors.initials: ML
authors.lastname: Marcial
keywords: congenital heart disease; congenital heart surgery; coronary artery anomaly; coronary artery surgery