title: Whole-lung lavage for pediatric patients with pulmonary alveolar proteinosis.
abstract: Pulmonary alveolar proteinosis (PAP) is a chronic disorder of surfactant clearance from the alveoli. Its prevalence is rare, especially in the pediatric population. Although there is no cure for this condition, symptoms of PAP are managed most effectively through whole-lung lavage (WLL). Perioperative RNs caring for children with PAP undergoing WLL in the OR should implement patient interventions to maintain vital signs and normothermia and preserve skin integrity. Additionally, perioperative RNs often are responsible for assembling closed-drainage systems for WLL. Detailed procedural preference cards, targeted education sessions, and multidisciplinary collaboration are crucial for establishing a comprehensive plan of care for the pediatric patient with PAP undergoing WLL in the OR.
authors.affiliation: The Children's Hospital of Philadelphia, PA, USA.
authors.forename: Leigh Ann
authors.initials: LA
authors.lastname: DiFusco
authors.forename: Raj K
authors.initials: RK
authors.lastname: Verma
mesh_terms: D002648:Child; D002675:Child, Preschool; D003422:Critical Care; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D010347:Patient Care Planning; D013527:Perioperative Nursing; D011649:Pulmonary Alveolar Proteinosis / Q000175:diagnosis / Q000451:nursing / Q000628:therapy*; D019233:Retreatment; D007507:Therapeutic Irrigation / Q000295:instrumentation / Q000379:methods