title: Tetralogy of Fallot with absent pulmonary valve syndrome, right aortic arch, and disconnected left pulmonary artery.
abstract: We present a rare case of a two-week-old infant with tetralogy of Fallot , absent pulmonary valve syndrome , right aortic arch, and disconnected left pulmonary artery (LPA) whose origin was from ductal ligament adjacent to the left subclavian artery. One-stage surgical correction, including closure of ventricular septal defect (VSD), LPA reconstruction and reconnection to the pulmonary trunk, reduction in size of the right pulmonary artery (RPA), and right ventricular outflow tract reconstruction with valved conduit, was successfully performed with good clinical mid-term outcome.
authors.affiliation: Department of Paediatric Cardiology, Freeman Hospital, High Heaton, Newcastle upon Tyne, UK. ruth.solana@salud.madrid.org
authors.forename: Ruth
authors.initials: R
authors.lastname: Solana-Gracia
authors.forename: David
authors.initials: D
authors.lastname: Crossland
authors.forename: Leslie
authors.initials: L
authors.lastname: Mitchell
authors.forename: Christopher
authors.initials: C
authors.lastname: Wren
authors.forename: Massimo
authors.initials: M
authors.lastname: Griselli
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000601:surgery; D006348:Cardiac Surgical Procedures; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000601:surgery; D018633:Pulmonary Atresia / Q000209:etiology* / Q000601:surgery; D019651:Plastic Surgery Procedures / Q000379:methods; D013771:Tetralogy of Fallot / Q000209:etiology* / Q000601:surgery; D016896:Treatment Outcome
keywords: bronchoscopy/bronchus; congenital heart surgery; great vessel anomaly; neonate; pulmonary arteries; pulmonary stenosis