title: Potts shunt and atrial septostomy in pulmonary hypertension caused by left ventricular disease.
abstract: We report a 20-year-old patient with Shone's complex and severe diastolic dysfunction of his small left ventricle (LV) in whom severe pulmonary hypertension and biventricular failure developed while he was awaiting combined heart-lung transplantation. We performed a percutaneous balloon atrial septostomy and a modified Potts shunt (13-mm graft from left pulmonary artery to descending aorta), with the aim of decompressing the hypertensive right ventricle (RV) by reducing left ventricular preload and left atrial hypertension. The procedures were uneventful. The patient's condition improved rapidly and biventricular function was restored. In contrast to a Potts shunt in other conditions, patients with pulmonary hypertension caused by left ventricular disease may benefit from an additional atrial left-to-right shunt.
authors.affiliation: Pediatric Heart Center, Justus-Liebig University Hospital, Giessen, Germany.
authors.forename: Heiner
authors.initials: H
authors.lastname: Latus
authors.forename: Christian
authors.initials: C
authors.lastname: Apitz
authors.forename: Dorle
authors.initials: D
authors.lastname: Schmidt
authors.forename: Christian
authors.initials: C
authors.lastname: Jux
authors.forename: Matthias
authors.initials: M
authors.lastname: Mueller
authors.forename: Juergen
authors.initials: J
authors.lastname: Bauer
authors.forename: Hakan
authors.initials: H
authors.lastname: Akintuerk
authors.forename: Martin
authors.initials: M
authors.lastname: Schneider
authors.forename: Dietmar
authors.initials: D
authors.lastname: Schranz
mesh_terms: D000714:Anastomosis, Surgical / Q000379:methods; D054087:Atrial Septum / Q000601:surgery; D006348:Cardiac Surgical Procedures / Q000379:methods*; D003937:Diagnosis, Differential; D004452:Echocardiography; D005500:Follow-Up Studies; D006325:Heart Atria / Q000000981:diagnostic imaging / Q000503:physiopathology / Q000601:surgery*; D006344:Heart Septal Defects, Atrial / Q000150:complications* / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis / Q000209:etiology / Q000601:surgery*; D019028:Magnetic Resonance Imaging, Cine; D008297:Male; D011652:Pulmonary Circulation; D055815:Young Adult