title: Ovarian steroid cell tumor, not otherwise specified, associated with congenital adrenal hyperplasia: rare tumors of an endocrine disease.
abstract: Ovarian steroid cell tumors, not otherwise specified (OSCTs), are extremely rare and present a diagnostic challenge when evaluating an ovarian mass. We present a case of such a tumor in a patient with known Congenital Adrenal Hyperplasia (CAH), secondary to 21-hydroxylase deficiency, who was noncompliant with her medications. The workup, diagnosis, and treatment of this rare condition are described.
authors.affiliation: Department of Pediatric Surgery, Connecticut Children's Medical Center, Hartford, CT, USA. tithomas@resident.uchc.edu
authors.forename: Tina T
authors.initials: TT
authors.lastname: Thomas
authors.forename: Kimberly R
authors.initials: KR
authors.lastname: Ruscher
authors.forename: Srinivas
authors.initials: S
authors.lastname: Mandavilli
authors.forename: Fabiola
authors.initials: F
authors.lastname: Balarezo
authors.forename: Christine M
authors.initials: CM
authors.lastname: Finck
mesh_terms: D000293:Adolescent; D000312:Adrenal Hyperplasia, Congenital / Q000150:complications*; D000314:Adrenal Rest Tumor / Q000175:diagnosis* / Q000209:etiology; D005260:Female; D006801:Humans; D010051:Ovarian Neoplasms / Q000175:diagnosis* / Q000209:etiology
keywords: Congenital adrenal hyperplasia; Endocrine tumors; Ovarian adrenal rest tumors; Ovarian steroid cell tumors; Ovarian tumor