title: Atrioventricular septal defect with an imperforate right-sided component of the common atrioventricular valve: anatomic and embryologic considerations.
abstract: We describe an atypical case of an atrioventricular septal defect with a common atrioventricular junction in which the right-sided component of the common atrioventricular valve was imperforate, producing tricuspid atresia with a severely hypoplastic right ventricle and an ostium primum defect. We discuss the implications of the anatomic findings with regard to concepts of cardiac development, drawing a comparison with similar cases previously reported.
authors.affiliation: 1 Department of Pediatrics, Amplatz Children's Hospital, University of Minnesota, Minneapolis, Minnesota, United States of America.
authors.forename: Lazaro E
authors.initials: LE
authors.lastname: Hernandez
authors.affiliation: 1 Department of Pediatrics, Amplatz Children's Hospital, University of Minnesota, Minneapolis, Minnesota, United States of America.
authors.forename: Lazaros K
authors.initials: LK
authors.lastname: Kochilas
authors.affiliation: 2 Department of Pediatrics, Institute of Medical Genetics, Newcastle University, Newcastle-upon-Tyne, United Kingdom.
authors.forename: Robert H
authors.initials: RH
authors.lastname: Anderson
mesh_terms: D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000196:embryology; D006343:Heart Septal Defects / Q000150:complications / Q000000981:diagnostic imaging / Q000196:embryology; D006801:Humans; D007223:Infant; D008297:Male; D018785:Tricuspid Atresia / Q000150:complications / Q000000981:diagnostic imaging / Q000196:embryology; D014463:Ultrasonography