title: [Primitive neuroectodermal tumor of kidney : a case report].
abstract: A 16-year-old man was referred to our hospital for asymptomatic gross hematuria. The findings of abdominal ultrasonography were normal. A month later, gross hematuria disappeared, and he was not followed after that. A month later, the patient was taken to our hospital in an ambulance for severe back pain and recurring gross hematuria. Computed tomography (CT) revealed a large right renal tumor with tumor thrombus penetrating inside the inferior vena cava. The patient underwent radical nephrectomy and embolectomy. The pathological diagnosis of the tumor was diagnosed as primitive neuroectodermal tumor (PNET) of kidney by immunostaining and gene analysis. We started adjuvant chemotherapy soon after the operation. However, at 10 months after, multiple pulmonary metastases were detected. The patient was treated with salvage chemotherapy, surgery and irradiation therapy as combined modality therapy. Nevertheless, he died 18 months after the diagnosis.
authors.affiliation: The Department of Urology, Osaka Red Cross Hospital, Japan.
authors.forename: Naofumi
authors.initials: N
authors.lastname: Tsutsumi
authors.forename: Takayuki
authors.initials: T
authors.lastname: Sumiyoshi
authors.forename: Motohiro
authors.initials: M
authors.lastname: Okamura
authors.forename: Yoshiharu
authors.initials: Y
authors.lastname: Nakashima
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Iwamura
authors.forename: Kenji
authors.initials: K
authors.lastname: Mitsumori
authors.forename: Kazuo
authors.initials: K
authors.lastname: Nishimura
authors.forename: Masayuki
authors.initials: M
authors.lastname: Shintaku
authors.forename: Takashi
authors.initials: T
authors.lastname: Koyama
authors.forename: Yusuke
authors.initials: Y
authors.lastname: Matsui
authors.forename: Mitsumasa
authors.initials: M
authors.lastname: Watanabe
mesh_terms: D000293:Adolescent; D006801:Humans; D007680:Kidney Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000628:therapy; D008297:Male; D018242:Neuroectodermal Tumors, Primitive / Q000175:diagnosis / Q000473:pathology* / Q000628:therapy