title: Synchronous perivesical and renal malignant rhabdoid tumor in a 9-year-old boy: a case report and review of literature.
abstract: Pediatric extrarenal malignant rhabdoid tumors (MRTs) are rare and aggressive (20% 5-year survival). Only 2 cases of bladder MRTs have been published. We report on a 9-year-old boy presenting with gross hematuria, palpable pelvic mass, and an obstructed, nonfunctional kidney. Evaluation was consistent with a 9.7 cm extrarenal MRT invading the bladder and prostate. He underwent a cystoprostatectomy, Indiana pouch continent urinary reservoir creation, and a left nephroureterectomy. A discrete 2.5 cm focus of renal MRT was found. To our knowledge, this is the first case of simultaneous perivesical and renal MRT. We review the current management of pediatric extrarenal MRTs.
authors.affiliation: Division of Pediatric Urology, Riley Hospital for Children, Indiana University School of Medicine, Indianapolis, IN.
authors.forename: Konrad M
authors.initials: KM
authors.lastname: Szymanski
authors.forename: Christian H
authors.initials: CH
authors.lastname: Tabib
authors.forename: Muhammad T
authors.initials: MT
authors.lastname: Idrees
authors.forename: Mark P
authors.initials: MP
authors.lastname: Cain
mesh_terms: D001706:Biopsy; D001853:Bone Marrow / Q000473:pathology; D002648:Child; D006417:Hematuria / Q000150:complications; D006801:Humans; D006869:Hydronephrosis / Q000175:diagnosis / Q000473:pathology; D007668:Kidney / Q000473:pathology; D007680:Kidney Neoplasms / Q000175:diagnosis* / Q000473:pathology*; D008198:Lymph Nodes / Q000601:surgery; D008297:Male; D011468:Prostatectomy; D018335:Rhabdoid Tumor / Q000175:diagnosis* / Q000473:pathology*; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome