title: Frontonasal and fibrous dysplasia in a patient with unilateral cleft lip and palate.
abstract: Frontonasal dysplasia is a rare entity. It has characteristic physical deformities: hypertelorism, broad nasal root, median facial cleft of the upper lip or palate, clefting of the nasal alae, poorly formed nasal tip, cranium bifidum occultum, and a widow's peak hairline. Fibrous dysplasia is a benign bone tumor in which normal bone is replaced by fibrous, poorly formed osseus tissues. We present a patient with frontonasal dysplasia who desired correction of her hypertelorism. Incidentally, fibrous dysplasia was found in her left orbit complicating surgical correction. In addition, the patient has velopharyngeal insufficiency and a class III malocclusion. The interplay of all these craniofacial defects makes the sequencing and timing of surgery important in this unique patient.
authors.affiliation: Division of Plastic Surgery, Baylor College of Medicine Houston, TX 77030-2399, USA. William.weathers@bcm.edu
authors.forename: William M
authors.initials: WM
authors.lastname: Weathers
authors.forename: Erik M
authors.initials: EM
authors.lastname: Wolfswinkel
authors.forename: Steven B
authors.initials: SB
authors.lastname: Albright
authors.forename: Larry H
authors.initials: LH
authors.lastname: Hollier
authors.forename: Edward P
authors.initials: EP
authors.lastname: Buchanan
mesh_terms: D000015:Abnormalities, Multiple; D000293:Adolescent; D002971:Cleft Lip / Q000601:surgery*; D002972:Cleft Palate / Q000601:surgery*; D019465:Craniofacial Abnormalities / Q000175:diagnosis*; D005145:Face / Q000002:abnormalities*; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000175:diagnosis; D006801:Humans; D006972:Hypertelorism / Q000175:diagnosis; D008313:Malocclusion, Angle Class III / Q000175:diagnosis; D009916:Orbital Diseases / Q000175:diagnosis; D014681:Velopharyngeal Insufficiency / Q000175:diagnosis