title: Progressive hemifacial atrophy.
abstract: Progressive hemifacial atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive but self-limited atrophy affecting one side of the face. The incidence and the cause of this alteration are unknown. A cerebral disturbance of fat metabolism has been proposed as a primary cause. Possible factors that are involved in the pathogenesis include trauma, viral infections, heredity, endocrine disturbances and auto-immunity. The most common complications that appear in association to this disorder are: trigeminal neuralgia, facial paresthesia, severe headache and epilepsy. Characteristically, the atrophy progresses slowly for several years and, it becomes stable. The objective of this work is, through the presentation of a clinical case, to accomplish a literature review concerning general characteristics, etiology, physiopathology and treatment of progressive hemifacial atrophy.
authors.affiliation: Department of Oral Medicine and Radiology, Vasantdada Patil Dental College and Hospital, Sangli, India.
authors.forename: Abhijeet
authors.initials: A
authors.lastname: Sande
authors.forename: Mukund
authors.initials: M
authors.lastname: Risbud
authors.forename: Avinash
authors.initials: A
authors.lastname: Kshar
authors.forename: Arati Oka
authors.initials: AO
authors.lastname: Paranjpe
keywords: Parry-Romberg Syndrome; Progressive hemifacial atrophy; Romberg's disease