title: Dermatofibrosarcoma protuberans: an unusual case of neck swelling.
abstract: Dermatofibrosarcoma protuberans (DFSP) is a relatively intermediate to low grade malignant tumour with high proclivity for local recurrence if excised inadequately. It is a locally aggressive tumour and despite sharing some histological features with fibrohistiocytic tumours, it tends to grow in a more infiltrative manner. We are reporting this rare tumour in a 30-year-old woman where the diagnosis of DFSP was confirmed histologically and by positive immunomarkers at immunohistochemistry.
authors.affiliation: Department of Otorhinolaryngology-Head & Neck Surgery, Aga Khan University Hospital, Karachi.
authors.forename: Naeem Sultan
authors.initials: NS
authors.lastname: Ali
authors.forename: Maliha
authors.initials: M
authors.lastname: Kazi
authors.forename: Beena
authors.initials: B
authors.lastname: Umar
authors.forename: Mumtaz Jamshed
authors.initials: MJ
authors.lastname: Khan
mesh_terms: D000328:Adult; D044963:Biopsy, Fine-Needle; D018223:Dermatofibrosarcoma / Q000175:diagnosis* / Q000532:radiotherapy; D003937:Diagnosis, Differential; D005260:Female; D006258:Head and Neck Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000532:radiotherapy; D006801:Humans; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000473:pathology / Q000532:radiotherapy