title: Late diagnosis of double aortic arch: consequences on long-term follow-up.
abstract: Double aortic arch is the most common congenital anomaly of the aortic arch system, in which the trachea and esophagus are completely encircled by vascular segments of the aortic arch and its branches, often resulting in variable airway compression. One case of late diagnosis of this congenital malformation and long-term consequences of late surgical treatment with persistent tracheo-broncomalacia and dynamic airway obstruction is reported. This report emphasizes the importance of an early diagnosis to minimise the progressive airways damage and subsequent respiratory symptoms, that need an accurate medical follow-up.
authors.affiliation: Respiratory Unit, "Bambino Gesù" Pediatric Hospital, IRCCS, Rome, Italy.
authors.forename: Nicola
authors.initials: N
authors.lastname: Ullmann
authors.forename: Laura
authors.initials: L
authors.lastname: Menchini
authors.forename: Teresa
authors.initials: T
authors.lastname: Salerno
authors.forename: Paolo
authors.initials: P
authors.lastname: Tomà
authors.forename: Renato
authors.initials: R
authors.lastname: Cutrera
mesh_terms: D000293:Adolescent; D001013:Aorta, Thoracic / Q000002:abnormalities* / Q000601:surgery; D001249:Asthma / Q000175:diagnosis*; D057210:Delayed Diagnosis; D003951:Diagnostic Errors; D056973:Four-Dimensional Computed Tomography; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging*; D008297:Male; D014132:Trachea / Q000000981:diagnostic imaging*; D055089:Tracheobronchomalacia / Q000150:complications / Q000175:diagnosis* / Q000000981:diagnostic imaging; D054079:Vascular Malformations / Q000150:complications / Q000175:diagnosis* / Q000601:surgery
keywords: 4D CT scan; aortic arch; bronchomalacia; dyspnoea