title: Vulvar "proximal-type" epithelioid sarcoma: report of a case and review of the literature.
abstract: BACKGROUND
  The "proximal-type" epithelioid sarcoma is a very rare kind of mesenchimal tumor characterized by the difficulty in histological diagnosis and the very aggressive biological behavior.
  
  
  METHODS
  We report of a case of a 63 years old woman with a vulvar "proximal-type" epithelioid sarcoma that underwent a radical surgical staging followed by an adjuvant radiotherapy. She is on follow-up care for 14 months and there is no clinical evidence of disease.
  
  
  CONCLUSIONS
  Even if quite rare the proximal type epithelioid sarcoma should be regarded as a separate entity of particularly aggressive biologic behaviour. Its diagnosis attracts controversies and criticism related to the surgical approach and the choice of an adjuvant therapy.
  The virtual slide(s) for this article can be found here: http://www.diagnosticpathology.diagnomx.eu/vs/1508554852942125.
authors.affiliation: Surgery Department, Gynecology Section and Obstetrics, Tor Vergata University, Rome, Italy.
authors.forename: Lodovico
authors.initials: L
authors.lastname: Patrizi
authors.forename: Giacomo
authors.initials: G
authors.lastname: Corrado
authors.forename: Maria
authors.initials: M
authors.lastname: Saltari
authors.forename: Letizia
authors.initials: L
authors.lastname: Perracchio
authors.forename: Chiara
authors.initials: C
authors.lastname: Scelzo
authors.forename: Emilio
authors.initials: E
authors.lastname: Piccione
authors.forename: Enrico
authors.initials: E
authors.lastname: Vizza
mesh_terms: D014408:Biomarkers, Tumor / Q000032:analysis; D001706:Biopsy; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D008875:Middle Aged; D009367:Neoplasm Staging; D018714:Radiotherapy, Adjuvant; D012509:Sarcoma / Q000737:chemistry / Q000473:pathology* / Q000628:therapy; D013997:Time Factors; D016896:Treatment Outcome; D014846:Vulvar Neoplasms / Q000737:chemistry / Q000473:pathology* / Q000628:therapy
chemical_list: D014408:Biomarkers, Tumor