title: Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature.
abstract: Klippel-Trenaunay syndrome (KTS) is a rare congenital syndrome of vascular malformations and soft tissue and bone hypertrophy. Vascular malformations can affect multiple organ systems. Involvement of the gastrointestinal (GI) tract is uncommon in KTS, but it can be a source of life-threatening bleeding. We report a case of a 32-year-old male with a known diagnosis of KTS who presented with a life-threatening rectal bleeding and was treated with proctosigmoidectomy and massive blood products transfusion. He expired after a long hospitalization. We then review the literature on KTS and management of some of its complications.
authors.affiliation: Department of Internal Medicine, Division of Gastroenterology, Saint Francis Hospital Evanston Program, University of Illinois at Chicago, 355 Ridge Avenue, Evanston, IL 60202, USA.
authors.forename: Salih
authors.initials: S
authors.lastname: Samo
authors.forename: Muhammed
authors.initials: M
authors.lastname: Sherid
authors.forename: Husein
authors.initials: H
authors.lastname: Husein
authors.forename: Samian
authors.initials: S
authors.lastname: Sulaiman
authors.forename: Margaret
authors.initials: M
authors.lastname: Yungbluth
authors.forename: John A
authors.initials: JA
authors.lastname: Vainder