title: Unusual sudden cardiac death from an anomalous left coronary artery from the right sinus of Valsalva.
abstract: A left coronary artery arising from the right sinus of Valsalva is a rare congenital coronary anomaly. We report a case of a 5-year-old boy with an anomalous left coronary artery from the right sinus of Valsalva whose presenting sign was cardiac arrest. There is no reported instance of a child <9 years of age without other congenital cardiac defects having died suddenly with this coronary anomaly. The transthoracic echocardiogram demonstrated normal origins of the coronary arteries, but on autopsy, an anomalous origin of the left main coronary artery from the right sinus of Valsalva was found.
authors.affiliation: 1Department of Pediatric Cardiology,Johns Hopkins School of Medicine,Baltimore,Maryland,United States of America.
authors.forename: Ram N
authors.initials: RN
authors.lastname: Bishnoi
authors.affiliation: 2Department of Pediatrics and Department of Anesthesiology and Critical Care Medicine,Johns Hopkins School of Medicine,Baltimore,Maryland,United States of America.
authors.forename: Kristen N
authors.initials: KN
authors.lastname: McMillan
authors.affiliation: 1Department of Pediatric Cardiology,Johns Hopkins School of Medicine,Baltimore,Maryland,United States of America.
authors.forename: William R
authors.initials: WR
authors.lastname: Thompson
mesh_terms: D002675:Child, Preschool; D003330:Coronary Vessel Anomalies / Q000150:complications*; D016757:Death, Sudden, Cardiac / Q000209:etiology*; D006801:Humans; D008297:Male; D012850:Sinus of Valsalva / Q000002:abnormalities*