title: Episodic idiopathic systemic capillary leak syndrome in a girl.
abstract: Episodic idiopathic systemic capillary leak syndrome is a rare disorder that presents with attacks of circulatory shock due to plasma leakage into the extravascular space. Reported here is the case of a girl who had recurrent circulatory shock. The diagnosis of episodic idiopathic systemic capillary leak syndrome was made following the fourth episode. The course was favorable following acute i.v. cristalloids and methylprednisolone.
authors.affiliation: Pediatric Emergency Unit, Clinica De Marchi, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy. yoyobiancorosso@hotmail.com
authors.forename: Gregorio Paolo
authors.initials: GP
authors.lastname: Milani
authors.forename: Rosa Maria
authors.initials: RM
authors.lastname: Dellepiane
authors.forename: Massimo Luca
authors.initials: ML
authors.lastname: Castellazzi
authors.forename: Marta Benedetta Maria
authors.initials: MB
authors.lastname: Mazzoni
authors.forename: Mario Giovanni
authors.initials: MG
authors.lastname: Bianchetti
authors.forename: Emilio Filippo
authors.initials: EF
authors.lastname: Fossali
mesh_terms: D019559:Capillary Leak Syndrome / Q000150:complications* / Q000628:therapy; D002675:Child, Preschool; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D012151:Resuscitation / Q000379:methods; D012769:Shock / Q000209:etiology* / Q000628:therapy
keywords: circulatory shock; episodic idiopathic systemic capillary leak syndrome