title: Giant Sporadic Low Grade Malignant Peripheral Nerve Sheath (MPNST) of Left Thigh.
abstract: Malignant Peripheral Nerve Sheath Tumours (MPNST) are rare spindle- cell sarcomas which are derived from the schwann cells or the pleuripotent cells of the neural crest. MPNSTs are usually located in the peripheral nerve trunk roots, extremities and in the head and neck region. These tumours may arise as sporadic variants or in patients with neurofibromatosis1 (NF1). The estimated incidence of MPNSTs in the patients with NF1is 2-5% as compared to a 0.001% incidence in the general population. Herein, we are reporting a case of a giant sporadic (NF1 independent) low grade MPNST of the left thigh in 65 year female patient, which had a good prognosis.
authors.affiliation: Associate Professor, Department of Pathology, JMF's ACPM Medical College and Hospital , Dhule, Maharashtra, India .
authors.forename: Dhiraj B
authors.initials: DB
authors.lastname: Nikumbh
authors.forename: K H
authors.initials: KH
authors.lastname: Suryawanshi
authors.forename: N V
authors.initials: NV
authors.lastname: Dravid
authors.forename: T B
authors.initials: TB
authors.lastname: Patil
authors.forename: C M
authors.initials: CM
authors.lastname: Rokade
keywords: Malignant Peripheral Nerve Sheet Tumour (MPNST); Neurofibromatosis 1 (NF1); Sporadic
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