title: Case reports of incontinentia pigmenti in males.
abstract: Incontinentia pigmenti is an X-linked dominant disorder, which is fatal in males, and majority of cases reported are in females. Here, we report 2 cases of males with incontinentia pigmenti. Case 1 has progressed through the classical stages of IP, giving history of vesicular and verrucous lesions and has presented with hyperpigmentation in whorled pattern. Case 2 has vesicular lesions in a linear distribution on the legs along with classical histopathological findings.
authors.affiliation: theDepartment of Dermatology, Venerology and Leprology, B. J. Medical College, Ahmedabad, Gujarat, India.
authors.forename: Khushboo D
authors.initials: KD
authors.lastname: Gupta
authors.forename: Bela B
authors.initials: BB
authors.lastname: Padhiar
authors.forename: Umesh K
authors.initials: UK
authors.lastname: Karia
authors.forename: Bela J
authors.initials: BJ
authors.lastname: Shah
keywords: Findings; X-linked dominant; incontinentia pigmenti; males
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