title: Uncommon of the uncommon: malignant perivascular epithelioid cell tumor of the lung.
abstract: A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant pulmonary PEC tumor with lung to lung metastases was established. Herein, the difficulties of diagnosis and management we confronted are described.
authors.affiliation: Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul 135-710, Korea.
authors.forename: Hyun-Ju
authors.initials: HJ
authors.lastname: Lim
authors.forename: Ho Yun
authors.initials: HY
authors.lastname: Lee
authors.forename: Joungho
authors.initials: J
authors.lastname: Han
authors.forename: Yong Soo
authors.initials: YS
authors.lastname: Choi
authors.forename: Kyung Soo
authors.initials: KS
authors.lastname: Lee
mesh_terms: D003937:Diagnosis, Differential; D005500:Follow-Up Studies; D006801:Humans; D008175:Lung Neoplasms / Q000175:diagnosis* / Q000601:surgery; D008297:Male; D008875:Middle Aged; D054973:Perivascular Epithelioid Cell Neoplasms / Q000175:diagnosis* / Q000601:surgery; D011013:Pneumonectomy; D049268:Positron-Emission Tomography / Q000379:methods*; D020775:Thoracic Surgery, Video-Assisted / Q000379:methods; D014057:Tomography, X-Ray Computed / Q000379:methods*
keywords: Clear cell sugar tumor; Lung tumor; Pecoma; Perivascular epithelioid cell
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