title: Hypocomplementemic Urticarial Vasculitis Syndrome in an 8-year-old Boy: A Case Report and Review of Literature.
abstract: Hypocomplementemic urticarial vasculitis syndrome is an immune complex-mediated disease of unknown etiology. The clinical course is characterized by urticaria, conjunctivitis, joint pain, and hypocomplementemia. We here report a case of a child with hypocomplementemic urticarial vasculitis syndrome that progressed to nephritis. Renal biopsy was consistent with diffuse proliferative glomerulonephritis with diffuse subendothelial immune deposits. He responded well to a combination of steroid and mofetil micofenolate.
authors.affiliation: MBBCh, ABMS-Pediatric, Pediatric Rheumatologist, Salmaniya Medical Complex, Kingdom of Bahrain. ;
authors.forename: Zakiya Saleh Adnan
authors.initials: ZS
authors.lastname: Al Mosawi
authors.forename: Badriya Ebrahim Ahmed
authors.initials: BE
authors.lastname: Al Hermi
keywords: Children; HUVS; Nephritis
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