title: Mayer-Rokitansky-Kuster-Hauser syndrome type II: A rare case.
abstract: Mayer-Rokitansky-Kuster-Hauser (MRKH) is a malformation complex comprising absent vagina and absent or rudimentary uterus. MRKH syndrome may be attributed to an initial affection of the intermediate mesoderm consequently leading (by the end of the 4(th) week of fetal life) to an alteration of the blastema of the cervicothoracicsomites and the pronephricducts. These latter subsequently induce the differentiation of the mesonephric and then the Wolffian and Mullerian ducts. There are very sparse such cases reported. We present a case of type II MRKH or Mullerian renal cervical somite association (i.e., Mullerian duct aplasia, renal dysplasia, and cervical somite anomalies).
authors.affiliation: Department of General Medicine, Aarupadai Veedu Medical College and Hospital, Puducherry, India.
authors.forename: Anand
authors.initials: A
authors.lastname: Pai
authors.forename: Mohammad
authors.initials: M
authors.lastname: Shakir
keywords: Dandy Walker malformation; mayer-rokitansky-kuster-hauser syndrome type II; mullerian agenesis; renal agenesis
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