title: Hybrid procedures for an infant with hypoplastic left heart syndrome with intact atrial septum.
abstract: A boy, prenatally diagnosed as hypoplastic left heart syndrome (HLHS) with intact atrial septum (IAS) was successfully treated by hybrid procedures. He underwent emergent catheter atrial septostomy and stent insertion in the atrial septum on Day 1 and then underwent bilateral pulmonary artery banding, ductal stent insertion, modified Norwood operation, bidirectional Glenn's operation and finally Fontan type operation at 2 years of age. Considering the presence of decompression pathway from the left atrium in HLHS with IAS, we should organize a treatment team for collaborative work and plan an appropriate treatment strategy before delivery. Although his clinical course has been uneventful until now, closer medical observation is warranted because he may have coexisting pulmonary disease.
authors.affiliation: Department of Surgery, University of Yamanashi, 1110 Shimokato, Chuo-City, Yamanashi, 409-3898, Japan, ssuzuki@yamanashi.ac.jp.
authors.forename: Shoji
authors.initials: S
authors.lastname: Suzuki
authors.forename: Hiroaki
authors.initials: H
authors.lastname: Kise
authors.forename: Shigeaki
authors.initials: S
authors.lastname: Kaga
authors.forename: Minako
authors.initials: M
authors.lastname: Hoshiai
authors.forename: Keiichi
authors.initials: K
authors.lastname: Koizumi
authors.forename: Yohei
authors.initials: Y
authors.lastname: Hasebe
authors.forename: Shinya
authors.initials: S
authors.lastname: Motohashi
authors.forename: Masahiko
authors.initials: M
authors.lastname: Matsumoto
mesh_terms: D054087:Atrial Septum / Q000601:surgery; D006328:Cardiac Catheterization / Q000379:methods; D002675:Child, Preschool; D019299:Decompression, Surgical / Q000379:methods; D018729:Fontan Procedure / Q000379:methods; D006325:Heart Atria / Q000601:surgery; D006801:Humans; D018636:Hypoplastic Left Heart Syndrome / Q000601:surgery*; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D058327:Norwood Procedures / Q000379:methods*; D011651:Pulmonary Artery / Q000601:surgery; D012086:Reoperation
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