title: Pentalogy of Cantrell; complete expression in a nine-month-old-boy.
abstract: Pentalogy of Cantrell is a rare congenital malformation whose exact cause is not completely understood; it is characterized by defects in the anterior abdominal and thoracic walls consisting of omphalocoele, diaphragmatic defect, ectopia cordis, intracardiac defects and sternal clefts. The complex has variable clinical expression with complete and incomplete expressions reported. We, therefore, report a case of complete manifestation of the pentad in a 9-month-old boy.
authors.affiliation: Department of Paediatrics, Aminu Kano Teaching Hospital/Bayero University, Kano, Nigeria.
authors.forename: Ibrahim
authors.initials: I
authors.lastname: Aliyu
authors.forename: Mohammad Aminu
authors.initials: MA
authors.lastname: Mohammad
keywords: Cantrell; ectopia cordis; omphalocoele; pentalogy; sternal cleft
references.citation: Arq Bras Cardiol. 2000 Oct;75(4):323-8
references.pmid: 11058929
references.citation: Niger J Clin Pract. 2011 Jan-Mar;14(1):106-8
references.pmid: 21494004
references.citation: Am J Med Genet. 1988 Oct;31(2):391-4
references.pmid: 3232702
references.citation: Eur J Pediatr. 2008 Jan;167(1):29-35
references.pmid: 17674044
references.citation: Am J Med Genet. 1994 Feb 15;49(4):431-4
references.pmid: 7909197
references.citation: Surg Gynecol Obstet. 1958 Nov;107(5):602-14
references.pmid: 13592660
references.citation: Am J Med Genet. 1992 Jan 1;42(1):90-5
references.pmid: 1308371
references.citation: J Surg Tech Case Rep. 2010 Jan;2(1):20-3
references.pmid: 22091325
references.citation: Pediatr Pathol. 1986;5(3-4):481-3
references.pmid: 3537999
references.citation: Pediatr Dev Pathol. 2004 Nov-Dec;7(6):649-52
references.pmid: 15630538
references.citation: Ann Thorac Surg. 2000 Jul;70(1):111-4
references.pmid: 10921692