Peliosis hepatis in a child with myotubular myopathy: successful treatment using hepatic artery embolization.
Peliosis hepatis (PH) is a rare condition characterized by multiple blood-filled spaces within the hepatic parenchyma that can lead to fatal hemorrhage. There is no consensus on the best treatment algorithm for PH, and therapy is directed at removing the potential causative agent with operative intervention when necessary. Here we present the first known case of PH in a child with myotubular myopathy who was successfully treated with angiography and hepatic artery embolization as a first line therapy, without the need for operative intervention. Awareness of this condition and the available treatment modalities may lead to favorable outcomes in future cases.
Department of Surgery, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA. terlizjp@umdnj.edu
Joseph P
JP
Terlizzi
Robert
R
Azizi
Monica D
MD
Chow
Sharon
S
Underberg-Davis
John L
JL
Nosher
Perry W
PW
Stafford
Joelle
J
Pierre
D000792:Angiography; D002648:Child; D004621:Embolization, Therapeutic; D004630:Emergencies; D017707:Erythrocyte Transfusion; D040181:Genetic Diseases, X-Linked / Q000150:complications*; D006470:Hemorrhage / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy; D006499:Hepatic Artery / Q000000981:diagnostic imaging; D006801:Humans; D008107:Liver Diseases / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy; D008297:Male; D020914:Myopathies, Structural, Congenital / Q000150:complications*; D010382:Peliosis Hepatis / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy*; D010949:Plasma; D012151:Resuscitation; D012769:Shock / Q000209:etiology / Q000628:therapy; D014057:Tomography, X-Ray Computed
Hepatic artery embolization; Hepatic hemorrhage; Myotubular myopathy; Peliosis hepatis