Prosthodontic management of patients with amelogenesis imperfecta.
BACKGROUND
Amelogenesis Imperfecta (AI) is an heterogenous genetic disorder that disturbs the developing enamel structure. This rare ectodermal defect leads to a variety of clinical manifestations due to agenesis, hypoplasia, and/or hypomineralisation of the enamel.


OBJECTIVE
To describe the prosthodontic management of dental anomalies commonly associated with AI.


METHODS
By using the classification of Witkop and Rao (1971), the variation in clinical presentation of the different Types of AI are illustrated and discussed, in particular Type I AI and Type 4 AI.


CONCLUSIONS
Early diagnosis and prosthodontic management as part of a multidisciplinary, patient-centred approach are key factors to treatment success. Treatment options to address the oral complications are influenced by modifying factors including age, socioeconomic status, type and severity of the disorder, and intraoral status at the time of treatment planning. Ultimately, management includes pain and infection control, provision of aesthetics and restoration of function which may lead to patient satisfaction, psychological well-being and an improved quality of life.
Department of Prosthodontics, School of Oral Health Science, Faculty of Health Sciences, University of the Witwatersrand. Vyonne.Hoods-Moonsammy@wits.ac.za
V J
VJ
Hoods-Moonsammy
M M
MM
Mothopi
A K
AK
Taruvingira
C P
CP
Owen
D G
DG
Howes
D000293:Adolescent; D000328:Adult; D000367:Age Factors; D000567:Amelogenesis Imperfecta / Q000145:classification / Q000628:therapy*; D000848:Anodontia / Q000628:therapy; D002648:Child; D003442:Crowns; D003743:Dental Enamel / Q000002:abnormalities; D017266:Dental Prosthesis; D019094:Dental Prosthesis, Implant-Supported; D003824:Denture, Complete; D003830:Denture, Partial, Fixed; D004955:Esthetics, Dental; D006801:Humans; D008310:Malocclusion / Q000628:therapy; D010347:Patient Care Planning; D010348:Patient Care Team; D017060:Patient Satisfaction; D011788:Quality of Life; D012390:Root Canal Therapy / Q000379:methods; D014716:Vertical Dimension; D055815:Young Adult