title: [A case of IgG4 associated sclerosing cholangitis without clinical manifestations of autoimmune pancreatitis].
abstract: IgG4-related systemic diseases are characterized by a diffuse or mass forming inflammatory reaction rich in lymphocytes and IgG4-positive plasma cells (lymphoplasmacytic infiltration), fibrosclerosis of variable organs and obliterative phlebitis. They usually involve various organs including the pancreas, bile duct, gallbladder, salivary gland, retroperitoneum, kidney, lung, and prostate. However, most of them are accompanied by autoimmune pancreatitis, and good response to steroid treatment is one of the hallmarks of this disease. We report a case of an 67-year-old man with IgG4 associated sclerosing cholangitis, who was diagnosed by endoscopic retrograde cholangiopancreatography and successfully treated with steroid therapy.
authors: Department of Internal Medicine, Kwandong University Myongji Hospital, Deogyang-gu, Goyang, Korea.
authors: Song Wook
authors: SW
authors: Chun
authors: Ja Sung
authors: JS
authors: Choi
authors: Beo Deul
authors: BD
authors: Kang
authors: Yu Jin
authors: YJ
authors: Kim
authors: Ki Jun
authors: KJ
authors: Han
authors: Hyeon Geun
authors: HG
authors: Cho
authors: Hwa Eun
authors: HE
authors: Oh
authors: Jae Hee
authors: JH
authors: Cho
mesh_terms: D000368:Aged; D000893:Anti-Inflammatory Agents / Q000627:therapeutic use; D001327:Autoimmune Diseases / Q000150:complications / Q000175:diagnosis; D001653:Bile Ducts, Intrahepatic / Q000000981:diagnostic imaging / Q000473:pathology; D002760:Cholangiopancreatography, Endoscopic Retrograde; D015209:Cholangitis, Sclerosing / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D003135:Common Bile Duct / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D007074:Immunoglobulin G / Q000097:blood*; D007150:Immunohistochemistry; D008297:Male; D010195:Pancreatitis / Q000150:complications / Q000175:diagnosis; D011239:Prednisolone / Q000627:therapeutic use; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography
chemical_list: D000893:Anti-Inflammatory Agents; D007074:Immunoglobulin G; D011239:Prednisolone