title: Vogt-Koyanagi-Harada syndrome presenting with encephalopathy.
abstract: VogtKoyanagi-Harada (VKH) is a rare syndrome affecting tissues with melanocytes. The possibility that VKH syndrome has an autoimmune pathogenesis is supported by the high frequency of human leukocyte antigen-DR4 commonly associated with other autoimmune diseases. Eyes are the main affected organ, resulting in blindness. Brain disease as a late onset event is extremely rare. Here, we are reporting a 57-year-old woman with previously diagnosed VKH syndrome, presenting with a late-onset brain encephalopathy. She was treated with corticosteroids and discharged from hospital with good general condition.
authors: Department of Infectious and Tropical Diseases, Isfahan University of Medical Sciences, Isfahan, Iran.
authors: Alireza E
authors: AE
authors: Naeini
authors: Dana
authors: D
authors: Daneshmand
authors: Farzin
authors: F
authors: Khorvash
authors: Ahmad
authors: A
authors: Chitsaz
keywords: Autoimmunity; Vogt-Koyanagi-Harada syndrome; encephalopathy; human leukocyte antigen (HLA)
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