title: Moyamoya syndrome as an unusual presenting manifestation of systemic lupus erythematosus in a young woman.
abstract: OBJECTIVE
  To describe a rare case of moyamoya syndrome associated with systemic lupus erythematosus (SLE).
  A 22-year-old woman presented with left-sided hemiparesis in addition to fever, fatigue and malar rash. Brain magnetic resonance imaging revealed acute infarction in the right middle cerebral artery territory. Cerebral angiography showed features of moyamoya syndrome. Brain biopsy showed evidence of vasculitis. She responded well to steroid therapy.
  
  
  CONCLUSIONS
  This case represented a rare co-occurrence of SLE-related vasculitis and moyamoya syndrome. Early vascular imaging is critical in patients with SLE and suspected ischemic stroke.
authors.affiliation: Department of Neurology, Tianjin Huanhu Hospital, Tianjin, China.
authors.forename: Guanen
authors.initials: G
authors.lastname: Zhou
authors.forename: Zhongping
authors.initials: Z
authors.lastname: An
authors.forename: Sankalp
authors.initials: S
authors.lastname: Gokhale
mesh_terms: D000328:Adult; D002533:Cerebral Angiography; D005260:Female; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000453:epidemiology*; D008279:Magnetic Resonance Imaging; D008775:Methylprednisolone / Q000627:therapeutic use; D020768:Middle Cerebral Artery; D009072:Moyamoya Disease / Q000175:diagnosis* / Q000188:drug therapy / Q000453:epidemiology*
chemical_list: D008775:Methylprednisolone