title: Dandy Walker Syndrome with Tessier 7 Cleft-a Rare Case Report and a Surgical Note on the Use of Vermilion Flap and Lazy W-Plasty.
abstract: The Dandy-Walker syndrome is a malformation of the brain that involves the mal-development of the cerebellum, associated with a cystic enlargement of this area, and frequently hydrocephalus. This malformation occurs in ~1 in 30,000 babies. It is seen mostly in females. Developmental anomalies like cleft lip, cleft palate, and cardiac malformation, orthopaedic and urinary structural abnormalities may also occur in 30% of the individuals. We report a case of Dandy Walker syndrome with Tessier 7 facial cleft with paramedian cleft palate in a 6 month old child. Surgical methods used to correct this anomaly include commissuroplasty, myoplasty of the orbicularis oris, and closure of the cleft cheek. Authors report a vermilion square flap technique that combines a lower lip mucocutaneous vermilion border flap with a lazy W-plasty to ensure a natural commissure and skin closure.
authors.affiliation: Department of OMFS, Goa Dental College and Hospital, Bambolim, Goa, 403002 India.
authors.forename: Vikas
authors.initials: V
authors.lastname: Dhupar
authors.forename: Praveen
authors.initials: P
authors.lastname: Kumar
authors.forename: Francis
authors.initials: F
authors.lastname: Akkara
authors.forename: Ananth
authors.initials: A
authors.lastname: Kumar
keywords: Dandy-Walker syndrome (DWS); Tessier 7 malformation