title: Epithelioid hemangioma of the orbit or angiolymphoid hyperplasia with eosinophilia.
abstract: A patient was referred to the department for an incidentally discovered right orbital mass on MRI. After surgical excision, histopathologic examination led to the diagnosis of epithelioid hemangioma, a tumor rarely located in the orbit, whose main histopathologic feature is an exuberant proliferation of small vascular channels lined by enlarged endothelial cells. The clinical characteristics and histopathology of epithelioid hemangioma allow differentiation with Kimura disease, angiosarcoma, intravascular papillary endothelial hyperplasia, and other vascular tumors that share the common feature of an abnormal proliferation of endothelial cells. Although epithelioid hemangioma is extremely rare, it should be considered in the differential diagnosis of orbital tumors.
authors.affiliation: *Oculoplastic and Orbital Service, †Ophthalmology Service, and ‡Pathology Service, University Hospital La Paz, Madrid, Spain.
authors.forename: Margarita
authors.initials: M
authors.lastname: Sánchez-Orgaz
authors.forename: Alfredo
authors.initials: A
authors.lastname: Insausti-García
authors.forename: Laura Yébenes
authors.initials: LY
authors.lastname: Gregorio
authors.forename: Alvaro Arbizu
authors.initials: AA
authors.lastname: Duralde
authors.forename: Ricardo
authors.initials: R
authors.lastname: Romero-Martín
mesh_terms: D000368:Aged; D000796:Angiolymphoid Hyperplasia with Eosinophilia / Q000175:diagnosis* / Q000601:surgery; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D009916:Orbital Diseases / Q000175:diagnosis* / Q000601:surgery; D014792:Visual Acuity