title: Intraorbital arteriovenous fistula with thrombosed varix: Diagnosis and treatment without catheter angiography in a developing country.
abstract: BACKGROUND
  Pure intraorbital arteriovenous fistula (AVF) that do not connect to the cavernous sinus are quite rare. Presence of thrombosed varix in association with a spontaneous onset pure orbital AVF is even rarer.
  
  
  METHODS
  We report an interesting case of a 50-year-old female with pure intraorbital AVF of spontaneous onset with thrombosed varicose superior ophthalmic vein (SOV). She presented with 18 months history of right eye proptosis, upper lid swelling, and conjunctival chemosis with recent onset of retro-orbital pain and decreased vision. Computed tomography (CT) and angiography revealed thrombosed varicose SOV in association with pure intraorbital AVF. Direct surgical exposure of the thrombosed SOV through right fronto-orbital approach followed by excision of the fistulous lesion resulted in complete orbital decompression with disappearance of all symptoms by 2 months.
  
  
  CONCLUSIONS
  Spontaneous onset pure intraorbital AVF in association with thrombosed varicose SOV is extremely rare. In such cases, direct surgical exposure of the SOV followed by excision may accomplish complete closure of the fistula without significant risk for iatrogenic injury.
authors.affiliation: Department of Neurosurgery, S.C.B. Medical college and Hospital, Cuttack, Odisha, India.
authors.forename: Sudhansu Sekhar
authors.initials: SS
authors.lastname: Mishra
authors.forename: Souvagya
authors.initials: S
authors.lastname: Panigrahi
authors.forename: Pratap Chandra
authors.initials: PC
authors.lastname: Satpathy
authors.forename: Deepak
authors.initials: D
authors.lastname: Das
keywords: Direct surgical exposure; pure intraorbital arteriovenous fistula; spontaneous onset; thrombosed varix
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