title: Marfan's syndrome: pre-pubertal aortic rupture with left coronary artery aneurysms and fistulas.
abstract: Aortic dissection and rupture occur in 20-40% of patients with Marfan's syndrome. This occurs predominantly in the third and fourth decade of life, contributing to the increased morbidity and mortality of this specific group of patients. This is the first known documented case report of prepubertal left coronary sinus rupture with left coronary artery aneurysms with fistulous communication to both the superior vena cava and right superior pulmonary vein, presenting with a continuous murmur
authors.affiliation: Andrews Memorial Hospital, TAI Wing, 27 Hope Road, Kingston 10, Jamaica. sandrap@cwjamaica.com
authors.forename: S
authors.initials: S
authors.lastname: Williams-Phillips
mesh_terms: D000028:Abortion, Induced; D000293:Adolescent; D000783:Aneurysm / Q000175:diagnosis*; D001019:Aortic Rupture / Q000175:diagnosis*; D001164:Arteriovenous Fistula / Q000175:diagnosis*; D002648:Child; D003323:Coronary Aneurysm / Q000175:diagnosis*; D017023:Coronary Angiography; D003324:Coronary Artery Disease / Q000175:diagnosis*; D004452:Echocardiography; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007090:Image Interpretation, Computer-Assisted; D021621:Imaging, Three-Dimensional; D007563:Jamaica; D008382:Marfan Syndrome / Q000175:diagnosis*; D061330:Multidetector Computed Tomography; D011247:Pregnancy; D011249:Pregnancy Complications, Cardiovascular / Q000175:diagnosis*; D011667:Pulmonary Veins; D012850:Sinus of Valsalva; D014683:Vena Cava, Superior