title: Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born.
abstract: Prune belly syndrome (PBS) is a rare congenital anomaly of uncertain etiology. Many associations of PBS with other malformations were previously reported, but only few cases of the association with VACTERL have been described. We report a rare case of a Moroccan new born with PBS and complete VACTERL association. The cause of this association is still unknown, but a common etiology is possible, especially when for the two syndromes, a defect in mesodermal differentiation, in early first trimester, has been suggested.
authors.affiliation: Department of Anesthesia & Critical Care, Mother and Child Hospital, Mohammed VI University Hospital of Marrakech, Morocco.
authors.forename: Said
authors.initials: S
authors.lastname: Younous
authors.forename: Youssef
authors.initials: Y
authors.lastname: Zarrouki
authors.forename: Mustapha
authors.initials: M
authors.lastname: Boutbaoucht
authors.forename: Youssef
authors.initials: Y
authors.lastname: Mouaffak
authors.forename: Kawtar Ennour
authors.initials: KE
authors.lastname: El Idrissi
authors.forename: Nissrine
authors.initials: N
authors.lastname: Aboussair
authors.forename: Mohammed O
authors.initials: MO
authors.lastname: Saiad
keywords: Esophageal atresia; Prune belly syndrome; VACTERL association; new born
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