title: Rehabilitation of medically complex ectodermal dysplasia with novel surgical and prosthodontic protocols.
abstract: The functional and aesthetic needs of a 17-year-old patient afflicted with ectodermal dysplasia, chronic long-term immunosuppression, cleft palate, velopharyngeal insufficiency, hypernasality, maxillary hypoplasia, and oligodontia were met with a multidisciplinary team approach. Predictable functional and aesthetic outcomes were obtained with a combination of injection augmentation of the soft palate and nasopharynx and rigid fixation maxillary external distraction with immediate placement and immediate load protocols. No biological or prosthetic complications were noted after definitive rehabilitation with a mandibular implant-retained fixed prosthesis and a maxillary implant-retained detachable prosthesis.
authors.affiliation: Department of Dental Specialties, Division of Prosthetic and Esthetic Dentistry, Mayo Clinic College of Medicine, Rochester, Minnesota, USA. Electronic address: dhima.matilda@mayo.edu.
authors.forename: M
authors.initials: M
authors.lastname: Dhima
authors.affiliation: Department of Dental Specialties, Division of Prosthetic and Esthetic Dentistry, Mayo Clinic College of Medicine, Rochester, Minnesota, USA.
authors.forename: T J
authors.initials: TJ
authors.lastname: Salinas
authors.affiliation: Department of Otorhinolaryngology, Division of Pediatric Otorhinolaryngology, Mayo Clinic College of Medicine, Rochester, Minnesota, USA.
authors.forename: S A
authors.initials: SA
authors.lastname: Cofer
authors.affiliation: Department of Surgery, Division of Oral and Maxillofacial Surgery, Mayo Clinic College of Medicine, Rochester, Minnesota, USA.
authors.forename: K L
authors.initials: KL
authors.lastname: Rieck
mesh_terms: D000293:Adolescent; D002508:Cephalometry; D003758:Dental Implantation, Endosseous / Q000379:methods*; D019094:Dental Prosthesis, Implant-Supported; D004476:Ectodermal Dysplasia / Q000000981:diagnostic imaging / Q000601:surgery*; D004954:Esthetics; D006801:Humans; D008297:Male; D008334:Mandible / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D008437:Maxilla / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D011859:Radiography
keywords: chronic immune suppression; cleft palate; distraction osteogenesis; ectodermal dysplasia; immediate implant load; immediate implant placement; maxillary hypoplasia; oligodontia; treatment outcome; young adult