Malignant peripheral nerve sheath tumor of the small bowel: an unusual presentation with fatal outcome.
Malignant peripheral nerve sheath tumor of the small bowel is an extremely rare disease. Histologic distinction from other types of soft tissue sarcoma especially fibrosarcoma and leiomyosarcoma requires electron microscopy. Complete surgery remains the only curative treatment. However, late diagnosis makes curative surgery more difficult. The contribution of chemotherapy to incomplete surgery has been proved without controlled studies. We report a case of this type of lesion discovered following a small bowel perforation.
Department of Medical Oncology, National Institute of Oncology, Rabat, Morocco.
Amina
A
Mohtaram
Siham
S
Mesmoudi
Hind
H
M'rabti
Amal
A
Rami
Rachida
R
Latib
Zakia
Z
Bernoussi
Imane
I
Aaribi
Meryam
M
Ben Ameur El Youbi
Hassan
H
Errihani