Juvenile xanthogranuloma: diverse presentations of noncutaneous disease.
Juvenile xanthogranulomas (JXGs) are benign cutaneous lesions of childhood that often spontaneously involute. They rarely present as a noncutaneous tumors. However, JXG tumors have been described in numerous noncutaneous anatomic sites, presenting with a variety of symptoms. The severity of symptoms and accurate preoperative diagnosis of JXG should determine operative and nonoperative treatment options of these uncommon, benign, and self-limiting tumors. We report 3 cases of symptomatic, noncutaneous JXG from disparate anatomic sites all treated with aggressive surgical resection.
*Department of Pediatric Surgery, Children's Medical Center, University of Texas Southwestern Medical Center, Dallas †Baylor College of Medicine, Baylor University School of Medicine, Houston, TX ‡Department of Pediatric Surgery, University of Miami, Coral Gables, FL.
Joseph T
JT
Murphy
Tim
T
Soeken
Steve
S
Megison
Eduardo
E
Perez
D000293:Adolescent; D002648:Child; D005260:Female; D006801:Humans; D007223:Infant; D008171:Lung Diseases / Q000000981:diagnostic imaging* / Q000601:surgery; D008279:Magnetic Resonance Imaging; D008297:Male; D010182:Pancreatic Diseases / Q000000981:diagnostic imaging* / Q000601:surgery; D012720:Severity of Illness Index; D014057:Tomography, X-Ray Computed; D020433:Trigeminal Nerve Diseases / Q000473:pathology* / Q000601:surgery; D014972:Xanthogranuloma, Juvenile / Q000000981:diagnostic imaging* / Q000473:pathology* / Q000601:surgery