title: Acute brain ischemia as a complication of the Ehlers-Danlos syndrome, the case series.
abstract: Vascular type of Ehlers-Danlos syndrome involves many severe complications leading not only to organ-specific symptoms but often ends in a sudden death. The aim of this paper was to present a diagnostic possibilities and its efficiency rate in patients with vascular complications of Ehlers-Danlos syndrome who suffered from artery dissection resulting in acute brain or limb ischemia. We analysed three patients with diagnosed Ehlers-Danlos syndrome who were referred to radiology department for diagnostic imaging of affected vascular beds, each experienced brain ischemia. The paper also aims at offering some general recommendations for patients suffering from possible complications of type IV Ehlers-Danlos syndrome basing on our own experience and available literature data.
authors.affiliation: Department of Radiology and Imaging Diagnostic, Medical University of Lodz, Poland mike.pajak@gmail.com.
authors.forename: Michal
authors.initials: M
authors.lastname: Pajak
authors.affiliation: Department of Radiology and Imaging Diagnostic, Medical University of Lodz, Poland.
authors.forename: Marcin A
authors.initials: MA
authors.lastname: Majos
authors.affiliation: Department of Radiology and Imaging Diagnostic, Medical University of Lodz, Poland.
authors.forename: Wojciech
authors.initials: W
authors.lastname: Szubert
authors.affiliation: Department of Radiology and Imaging Diagnostic, Medical University of Lodz, Poland.
authors.forename: Ludomir
authors.initials: L
authors.lastname: Stefanczyk
authors.affiliation: Department of Radiology and Imaging Diagnostic, Medical University of Lodz, Poland.
authors.forename: Agata
authors.initials: A
authors.lastname: Majos
mesh_terms: D000208:Acute Disease; D000293:Adolescent; D000328:Adult; D002545:Brain Ischemia / Q000175:diagnosis / Q000209:etiology*; D003952:Diagnostic Imaging; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D012189:Retrospective Studies
keywords: Ehlers–Danlos syndrome; acute brain ischemia; arterial dissection