title: Meningioma associated with Gorlin's syndrome.
abstract: Gorlin's syndrome or naevoid basal cell carcinoma syndrome is a rare autosominal dominant condition characterised by a variety of congenital anomalies and various malignancies. The chief manifestations include multiple basal cell naevi, mandibular cysts, plantar and palmar pits, vertebral and rib abnormalities and intracranial calcifications. We report a patient with Gorlin's syndrome associated with meningioma treated at our institution. The clinical and radiological features together with the management strategies of this unusual disease entity are discussed.
authors.affiliation: Department of Neurosurgery, Queen Elizabeth Hospital, 30 Gascoigne Road, Kowloon, Hong Kong.
authors.forename: Chun-Wai
authors.initials: CW
authors.lastname: Lee
authors.affiliation: Department of Neurosurgery, Queen Elizabeth Hospital, 30 Gascoigne Road, Kowloon, Hong Kong. Electronic address: tzechingtan@yahoo.com.
authors.forename: Tze-Ching
authors.initials: TC
authors.lastname: Tan
mesh_terms: D000328:Adult; D001478:Basal Cell Nevus Syndrome / Q000150:complications* / Q000473:pathology; D001921:Brain / Q000000981:diagnostic imaging; D001932:Brain Neoplasms / Q000150:complications* / Q000473:pathology / Q000601:surgery; D005260:Female; D006801:Humans; D007570:Jaw Cysts / Q000000981:diagnostic imaging; D008279:Magnetic Resonance Imaging; D008334:Mandible / Q000000981:diagnostic imaging; D008579:Meningioma / Q000150:complications* / Q000473:pathology / Q000601:surgery; D012272:Ribs / Q000002:abnormalities / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed
keywords: Gorlin’s syndrome; Meningioma; Naevoid basal cell carcinoma syndrome