title: An adult patient of double-chambered right ventricle with ventricular septal defect incidentally diagnosed after presentation with acute myocardial infarction.
abstract: The double-chambered right ventricle (DCRV) is a rare congenital heart disease caused by hypertrophic anomalous muscle bands that divide the ventricular cavity, resulting in the formation of a high-pressure proximal chamber and other low-pressure distal one. Because of its evolving nature, its diagnosis is usually made during childhood/adolescence and very rarely during adulthood. It accounts for approximately 0.5-1% of patients with congenital heart disease. We report a case of a 50-year-old man who presented to us with acute inferior wall myocardial infarction (MI). Echocardiography revealed the features of DCRV and ventricular septal defect. Coronary angiogram revealed significant stenosis in right coronary artery. This is the first case where an adult patient with DCRV incidentally diagnosed after presentation with acute MI and had undergone successful coronary angioplasty.
authors.affiliation: Department of Cardiology, Sri Jayadeva Institute of Cardiovascular Sciences & Research, Bangalore, Karnataka, India.
authors.forename: Ravindranath K
authors.initials: RK
authors.lastname: Shankarappa
authors.forename: Soumya
authors.initials: S
authors.lastname: Patra
authors.forename: Satish
authors.initials: S
authors.lastname: Karur
authors.forename: Ajitpal
authors.initials: A
authors.lastname: Singh
authors.forename: Manjunath C
authors.initials: MC
authors.lastname: Nanjappa
authors.forename: Dhanlakshmi
authors.initials: D
authors.lastname: Chandrasekaran
mesh_terms: D017023:Coronary Angiography; D023921:Coronary Stenosis / Q000150:complications / Q000175:diagnosis; D004452:Echocardiography; D006345:Heart Septal Defects, Ventricular / Q000150:complications* / Q000175:diagnosis*; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D033162:Incidental Findings; D008297:Male; D008875:Middle Aged; D009203:Myocardial Infarction / Q000209:etiology*
keywords: adult; double-chambered right ventricle; myocardial infarction