title: Thoracic vertebral hemangioma causing paraplegia in Klippel-Trenaunay-Weber syndrome: case report.
abstract: Vertebral hemangiomas are the most common tumours of the vertebral column. Generally, these tumours are asymptomatic but some patients complain of back pain and develop neurologic symptoms due to extraosseous extension. Vertebral hemangiomas can extend extradurally causing neurological impairment as a result of compression of the spinal cord and nerve roots. Vertebral hemangiomas may be multiple and detectable as a component of the Klippel-Trenaunay-Weber syndrome. Although this syndrome consists of deep venous thrombosis, lymphatic anomalies, cutaneous capillary malformations, and hypertrophy of soft tissue and bone on extremities, its clinical presentation may be very variable. We present a unique case of vertebral hemangioma causing spinal cord compression due to the extradural extension that also had deep venous thrombosis, hematuria, hypophyseal cyst and ventricle asymmetry, diagnosed as the Klippel-Trenaunay-Weber syndrome.
authors.affiliation: Ankara Ataturk Education and Research Hospital, Department of Neurosurgery, Ankara, Turkey.
authors.forename: Ozerk
authors.initials: O
authors.lastname: Okutan
authors.forename: Timur
authors.initials: T
authors.lastname: Yildirim
authors.forename: Serdar
authors.initials: S
authors.lastname: Isik
authors.forename: Berna
authors.initials: B
authors.lastname: Gokce
authors.forename: Barıs
authors.initials: B
authors.lastname: Saygili
authors.forename: Ethem Bes
authors.initials: EB
authors.lastname: Konakli
mesh_terms: D000328:Adult; D003560:Cysts; D006391:Hemangioma / Q000150:complications*; D006417:Hematuria / Q000209:etiology; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000150:complications*; D008279:Magnetic Resonance Imaging; D008297:Male; D010264:Paraplegia / Q000209:etiology*; D010900:Pituitary Diseases / Q000209:etiology; D013117:Spinal Cord Compression / Q000209:etiology / Q000628:therapy; D013125:Spinal Neoplasms / Q000150:complications*; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography; D020246:Venous Thrombosis / Q000000981:diagnostic imaging / Q000209:etiology