title: Sinus node dysfunction as the first manifestation of left ventricular noncompaction with multiple cardiac abnormalities.
abstract: Left ventricular noncompaction (LVNC) is a genetically heterogenous form of cardiomyopathy which may remain undiagnosed till adulthood due to the late presentation of typical symptoms such as dyspnea, congestion, ventricular arrhythmias and thromboembolism. Symptomatic bradycardia secondary to persistent sinus node dysfunction is very rare. Coexistent cardiac defects are common in children however in adults the disease is usually in isolated form. Here, we present a case of twenty-three year-old female LVNC patient with patent ductus arteriosus, bicuspid aortic valve and persistent sinus node dysfunction who presented with dizziness as the first manifestation of the disease.
authors.affiliation: Department of Cardiology, Siyami Ersek Thoracic and Cardiovascular Surgery Center, Training and Research Hospital, Istanbul, Turkey.
authors.forename: Baris
authors.initials: B
authors.lastname: Gungor
authors.forename: Ahmet T
authors.initials: AT
authors.lastname: Alper
authors.forename: Ahmet
authors.initials: A
authors.lastname: Celebi
authors.forename: Osman
authors.initials: O
authors.lastname: Bolca
keywords: Cardiomyopathy; congenital heart disease; sinus node dysfunction