title: Progressive systemic sclerosis in a child.
abstract: Systemic sclerosis is a clinically heterogeneous systemic disease affecting the connective tissues of skin, walls of blood vessels and internal organs like lung, heart and kidneys. Systemic sclerosis is very unusual in pediatric population. Children represent fewer than 10% of all cases. We report a case of 11 years old girl of progressive systemic sclerosis presenting with features of cutaneous sclerosis, microstomia, mask-like facies, sclerodactyly, esophageal dysmotility, Raynaud's phenomenon, arthralgia and pulmonary fibrosis.
authors.affiliation: Department of Pediatric Medicine, Medical College, Kolkata, India.
authors.forename: Arun K
authors.initials: AK
authors.lastname: De
authors.forename: Kallol
authors.initials: K
authors.lastname: Das
authors.forename: Archan
authors.initials: A
authors.lastname: Sil
authors.forename: Swarnali
authors.initials: S
authors.lastname: Joardar
keywords: Microstomia; Raynaud's phenomenon; progressive systemic sclerosis; pulmonary fibrosis; sclerodactyly