title: Influencing factors on the functional level of haemophilic patients assessed by FISH.
abstract: Joint destruction in early adulthood brings the patients to the orthopaedic clinics. If a haemophilic patient becomes disabled, it shows a number of factors such as timely diagnosis, availability of appropriate treatment depending on the country, access and affordability to treatments and equally importantly the responsibility of the patient in managing self care by remaining compliant by prescribed treatment regimen. We assessed the functional level by functional independence score in haemophilia (FISH). Overall, 104 patients with haemophilia A and 29 with haemophilia B were evaluated. We assessed the function of the patients by FISH. We divided the sum scores into weak (FISH score 8-16), moderate (17-24), and good (25-32). For evaluating the level of functional deficit in a 2 × 2 table, we categorized the weak and moderate levels into Disordered Group and the good level into Not-Disordered Group. The average age was 26.9 ± 14.24. Each 1 year increase in age can increase 1.07 fold the possibility of being placed in Disordered Function Group. Severe haemophilia can increase 7.34 fold, presence of inhibitor can increase 9.75 fold and home self-care increases 3.89 fold the possibility of being placed in Disordered Function Group. To decrease the burden of the cost on patient, family and the government, education plays the most important role. We suggest that we send a trained team of physician and nurses to the deprived villages and cities instead of waiting for the patient to refer to our Care Center.
authors.affiliation: Orthopedic and Trauma Research Center, Ghaem Hospital, Mashhad, Iran.
authors.forename: A R
authors.initials: AR
authors.lastname: Kachooei
authors.forename: Z
authors.initials: Z
authors.lastname: Badiei
authors.forename: M E
authors.initials: ME
authors.lastname: Zandinezhad
authors.forename: M H
authors.initials: MH
authors.lastname: Ebrahimzadeh
authors.forename: S M
authors.initials: SM
authors.lastname: Mazloumi
authors.forename: F
authors.initials: F
authors.lastname: Omidi-Kashani
authors.forename: A
authors.initials: A
authors.lastname: Moradi
authors.forename: R
authors.initials: R
authors.lastname: Mahdavian-Naghashzargar
authors.forename: S
authors.initials: S
authors.lastname: Razi
mesh_terms: D000203:Activities of Daily Living; D000293:Adolescent; D000328:Adult; D002648:Child; D003430:Cross-Sectional Studies; D019468:Disease Management; D006395:Hemarthrosis / Q000209:etiology* / Q000534:rehabilitation*; D006467:Hemophilia A / Q000150:complications* / Q000453:epidemiology* / Q000628:therapy; D002836:Hemophilia B / Q000150:complications* / Q000453:epidemiology* / Q000628:therapy; D006801:Humans; D012307:Risk Factors; D012648:Self Care; D011795:Surveys and Questionnaires; D055815:Young Adult
keywords: FISH; hemophilia A; hemophilia B; home care; inhibitor; nurse care