title: Rarely metastasizing soft tissue tumours.
abstract: Soft tissue tumours that rarely metastasize have been afforded their own subcategory in recent WHO classifications. This review discusses the nature of these tumours and the difficulty in constructing usefully simple classifications for heterogeneous and complex groups of tumours. We also highlight the specific rarely metastasizing soft tissue tumours that have been recently added to the WHO classification (phosphaturic mesenchymal tumour, pseudomyogenic haemangioendothelioma) and those entities where there have been recent important defining genetic discoveries (myxoinflammatory fibroblastic sarcoma, solitary fibrous tumour, myoepitheliomas).
authors.affiliation: Department of Musculoskeletal Pathology, Royal Orthopaedic Hospital NHS Trust, Robert Aitken Institute of Clinical Research and School of Cancer Sciences, Medical School, Birmingham University, Birmingham, UK; Department of Musculoskeletal Pathology, Robert Jones and Agnes Hunt Orthopaedic Hospital NHS Trust, Oswestry, UK.
authors.forename: D Chas
authors.initials: DC
authors.lastname: Mangham
authors.forename: Lars-Gunnar
authors.initials: LG
authors.lastname: Kindblom
mesh_terms: D006801:Humans; D012983:Soft Tissue Neoplasms / Q000145:classification* / Q000235:genetics / Q000473:pathology*
keywords: GIST; PEComa; grade; intermediate; melanotic schwannoma; myoepithelioma; myxoinflammatory fibroblastic sarcoma; phosphaturic mesenchymal tumour; pseudomyogenic haemangioendothelioma; rarely metastasizing; sarcoma; solitary fibrous tumour