title: Papillary fibroelastoma of the pulmonary valve--a systematic review.
abstract: The pulmonary valve is the least affected site for valvular papillary fibroelastoma. With increasing use of routine echocardiography and other modalities of imaging, pulmonary valve papillary fibroelastomas (PVPFE) are being recognized more frequently. PVPFE is more often an incidental diagnosis and symptomatic patients usually present with shortness of breath. Embolic phenomena and right ventricular outflow tract obstruction are the most serious complications of PVPFE. Since PVPFE is rare, the purpose of this systematic review is to address demographic characteristics, the clinical presentation, management, and outcome of this benign tumor of the pulmonary valve.
authors.affiliation: Division of Cardiovascular Diseases, Department of Medicine, Mayo Clinic, Scottsdale, Arizona.
authors.forename: Fayaz A
authors.initials: FA
authors.lastname: Hakim
authors.forename: Madan Raj
authors.initials: MR
authors.lastname: Aryal
authors.forename: Anil
authors.initials: A
authors.lastname: Pandit
authors.forename: Aashrayata Aryal
authors.initials: AA
authors.lastname: Pandit
authors.forename: Jorge R
authors.initials: JR
authors.lastname: Alegria
authors.forename: Christopher B
authors.initials: CB
authors.lastname: Kendall
authors.forename: Roger L
authors.initials: RL
authors.lastname: Click
mesh_terms: D000328:Adult; D000368:Aged; D000369:Aged, 80 and over; D004452:Echocardiography / Q000379:methods*; D005260:Female; D005350:Fibroma / Q000000981:diagnostic imaging*; D006338:Heart Neoplasms / Q000000981:diagnostic imaging*; D006349:Heart Valve Diseases / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D008875:Middle Aged; D011664:Pulmonary Valve / Q000000981:diagnostic imaging*
keywords: papillary fibroelastoma; pulmonary valve