title: Brown bowel syndrome (intestinal lipofuscinosis) - a case report and review of the literature.
abstract: Brown bowel syndrome (BBS) is a very rare condition occurring in association with malabsorption syndromes. It is characterised by deposition of granular, brown pigment (lipofuscin or ceroid) in intestinal smooth muscles. Rarely BBS can be complicated by distention of any segment of the bowel. We present a case of BBS associated with massive dilation of first loop of the small intestine and moderate dilation of the sigmoid colon with functional intestinal disturbances requiring surgical intervention in an 11-year-old boy.
authors.affiliation: Magdalena Białas, MD, Department of Pathomorphology, ul. Grzegórzecka 16, 31-351 Kraków, tel. +48 12 421 15 64, e-mail: mbialas7@gmail.com.
authors.forename: Magdalena
authors.initials: M
authors.lastname: Białas
authors.forename: Sergiusz
authors.initials: S
authors.lastname: Demczuk
authors.forename: Grzegorz
authors.initials: G
authors.lastname: Dyduch
authors.forename: Grażyna
authors.initials: G
authors.lastname: Drabik
authors.forename: Małgorzata
authors.initials: M
authors.lastname: Chrupek
authors.forename: Krzysztof
authors.initials: K
authors.lastname: Okoń
mesh_terms: D002648:Child; D006801:Humans; D007410:Intestinal Diseases / Q000150:complications / Q000378:metabolism / Q000473:pathology*; D007420:Intestine, Large / Q000378:metabolism / Q000473:pathology*; D008062:Lipofuscin / Q000378:metabolism*; D008286:Malabsorption Syndromes / Q000150:complications / Q000151:congenital; D008297:Male
chemical_list: D008062:Lipofuscin