title: Congenital peribronchial myofibroblastic tumor: prenatal imaging clues to differentiate from other fetal chest lesions.
abstract: We present a prenatal case of congenital peribronchial myofibroblastic tumor referred as a congenital pulmonary airway malformation (CPAM) with hydrops and polyhydramnios at 30 weeks' gestational age. US and fetal MRI findings did not fit with the referral diagnosis, raising the possibility of intrinsic lung tumor. Fetal hydrops worsened and the baby was successfully delivered by ex utero intrapartum treatment (EXIT) to resection at 31 weeks' gestational age. To the best of our knowledge, this is a unique case of congenital peribronchial myofibroblastic tumor that underwent comprehensive prenatal evaluation and EXIT procedure with good outcome.
authors.affiliation: Department of Radiology, MLC 5031, Cincinnati Children's Hospital Medical Center, 3333 Burnet Ave., Cincinnati, OH, 45229-3026, USA, maria.calvo@cchmc.org.
authors.forename: Maria A
authors.initials: MA
authors.lastname: Calvo-Garcia
authors.forename: Foong-Yen
authors.initials: FY
authors.lastname: Lim
authors.forename: Jerzy
authors.initials: J
authors.lastname: Stanek
authors.forename: Constance
authors.initials: C
authors.lastname: Bitters
authors.forename: Beth M
authors.initials: BM
authors.lastname: Kline-Fath
mesh_terms: D003937:Diagnosis, Differential; D005260:Female; D005315:Fetal Diseases / Q000175:diagnosis* / Q000601:surgery; D005354:Fibrosarcoma / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008175:Lung Neoplasms / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D008279:Magnetic Resonance Imaging; D008297:Male; D011247:Pregnancy; D011256:Pregnancy Outcome; D011296:Prenatal Diagnosis; D016216:Ultrasonography, Prenatal; D055815:Young Adult