title: Pattern dystrophy of the macula in a case of steinert disease.
abstract: BACKGROUND
  Myotonic dystrophies are typically associated with ocular complications like ptosis, weakness of the ocular muscle and cataracts, but also with less recognized retinal changes.
  
  
  METHODS
  A 41-year-old female with type 1 myotonic dystrophy complained of progressive vision loss. Slit lamp examination revealed the presence of typical bilateral polychromatic cataract with posterior subcapsular component. Dilated fundus examination was remarkable for bilateral macular depigmented changes. Multimodal imaging analysis of the macula suggested the presence of a butterfly-shaped pattern dystrophy.
  
  
  CONCLUSIONS
  In cases of myotonic dystrophies it is of great relevance to analyze the presence of retinal changes that might limit the visual improvement following cataract extraction.
authors.affiliation: Department of Ophthalmology, Centro Hospitalar de Entre o Douro e Vouga, Santa Maria da Feira, Portugal ; Unit of Macula and Medical Retina, Department of Ophthalmology, University and Polytechnic Hospital La Fe, Valencia, Spain.
authors.forename: Filipe
authors.initials: F
authors.lastname: Esteves
authors.forename: Rosa
authors.initials: R
authors.lastname: Dolz-Marco
authors.forename: Pablo
authors.initials: P
authors.lastname: Hernández-Martínez
authors.forename: Manuel
authors.initials: M
authors.lastname: Díaz-Llopis
authors.forename: Roberto
authors.initials: R
authors.lastname: Gallego-Pinazo
keywords: Acquired vitelliform deposit; Maculopathy; Myotonic dystrophy; Pattern dystrophy; Steinert disease