title: Isolated persistent left-sided superior vena cava, giant coronary sinus, atrial tachycardia and heart failure in a child.
abstract: Persistence of a left-sided superior vena cava (PLSVC) with absent right superior vena cava (isolated PLSVC) is a very rare venous malformation and commonly associated with congenital heart disease or alterations of the cardiac situs. We describe an unusual case of a young boy presenting with persistent atrial tachycardia and congestive heart failure. He was detected to have unexplained grossly dilated right atrium, right ventricle with systolic dysfunction and a giant coronary sinus (CS). The dilated CS closely mimicked a pseudo cor-triatriatum on echocardiography. Contrast echocardiography from both arms revealed opacification of the CS before the right atrium. Bilateral upper limb venography confirmed the presence of absent right SVC and isolated persistent left SVC draining into the giant coronary sinus.
authors.affiliation: Department of Cardiology, Sanjay Gandhi Postgraduate Institute of Medical Sciences, Lucknow, India.
authors.forename: Nagaraja
authors.initials: N
authors.lastname: Moorthy
authors.forename: Aditya
authors.initials: A
authors.lastname: Kapoor
authors.forename: Sudeep
authors.initials: S
authors.lastname: Kumar
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000293:Adolescent; D000792:Angiography / Q000379:methods; D054326:Coronary Sinus / Q000002:abnormalities*; D019560:Echocardiography, Three-Dimensional / Q000379:methods; D004562:Electrocardiography / Q000379:methods; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000175:diagnosis; D006333:Heart Failure / Q000175:diagnosis*; D006801:Humans; D008297:Male; D035583:Rare Diseases; D013612:Tachycardia, Ectopic Atrial / Q000175:diagnosis*; D014057:Tomography, X-Ray Computed / Q000379:methods; D054079:Vascular Malformations / Q000175:diagnosis; D014683:Vena Cava, Superior / Q000002:abnormalities* / Q000000981:diagnostic imaging
keywords: Atrial tachycardia; Congestive heart failure; Coronary sinus; Persistent LSVC