title: [Pediatric Behçet's disease].
abstract: Behçet's disease is a chronic multisystem vasculitis of unknown etiology. The disease is commonly described in young adults but can occur in childhood. Diagnosis is based on clinical manifestations since there are no pathognomonic laboratory findings. Early diagnosis in children is challenging due to the insidious nature of the disease and the low sensitivity of adult criteria in the pediatric population. The purpose of this review is to describe the demographic and clinical features of Behçet's disease in childhood, its complications and recent advances in therapeutics highlighting differences with the adult onset disease.
authors.affiliation: Service de pédiatrie et rhumatologie pédiatrique, Centre de référence des maladies auto-inflammatoires de l'enfant (CeRéMAI), CHU de Bicêtre, AP-HP, université Paris Sud, 78, avenue du Général-Leclerc, 94270 Le Kremlin Bicêtre, France. Electronic address: maryam.piram@bct.aphp.fr.
authors.forename: M
authors.initials: M
authors.lastname: Piram
authors.affiliation: Service de pédiatrie et rhumatologie pédiatrique, Centre de référence des maladies auto-inflammatoires de l'enfant (CeRéMAI), CHU de Bicêtre, AP-HP, université Paris Sud, 78, avenue du Général-Leclerc, 94270 Le Kremlin Bicêtre, France.
authors.forename: I
authors.initials: I
authors.lastname: Koné-Paut
mesh_terms: D000328:Adult; D000367:Age Factors; D001528:Behcet Syndrome / Q000175:diagnosis / Q000453:epidemiology* / Q000628:therapy; D002648:Child; D018450:Disease Progression; D006801:Humans
keywords: Behçet's disease; Maladie de Behçet; Pediatrics; Pédiatrie; Vascularite; Vasculitis