title: Typical radiological findings of lipoid proteinosis of urbach and wiethe. A case report.
abstract: Lipoid proteinosis is a rare autosomal recessive dermatosis, which can be congenital or have onset in infancy. It is characterized by the progressive deposition of an amorphous hyaline substance with a glycoprotein constitution in the skin and mucous membranes and presents as papular lesions that can aggregate forming plaques with a yellowish discoloration. We present a case of lipoid proteinosis in a seven-year-old boy where characteristic calcifications in the medial temporal lobe helped in early initiation of treatment.
authors.affiliation: Radiology Department, KGS Advanced MR and CT Scan; Madurai, India - mail@kgsscans.com.
authors.forename: K G
authors.initials: KG
authors.lastname: Srinivasan
authors.forename: S
authors.initials: S
authors.lastname: Ramprabananth
authors.forename: S
authors.initials: S
authors.lastname: Srividya
authors.forename: K P
authors.initials: KP
authors.lastname: Ushanandhini