title: Focal portal vein stenosis in an adolescent potentially related to complicated umbilical catheter insertion in the neonatal period.
abstract: A 14-year-old girl, with no medical history except for a preterm birth at 7 months, presented with clinical and laboratory signs of pancytopenia. Radiological investigation, including abdominal ultrasound and magnetic resonance imaging revealed a focal irregular main portal vein wall and splenomegaly. Endoscopy showed major esophageal and gastric varices. Definitive diagnosis was made by direct, transhepatic portography revealing a focal stenosis associated with a dissection of the main portal vein. Percutaneous treatment including balloon angioplasty and stent placement resulted in complete re-expansion of the portal vein main branch. Clinical and radiological follow-up over 5 years showed complete disappearance of all clinical signs and normalization of laboratory data and splenic volume.
authors.affiliation: Department of Radiology, UZ Leuven/Department of Imaging & Pathology, KU Leuven.
authors.forename: Geert
authors.initials: G
authors.lastname: Maleux
authors.forename: Ilse
authors.initials: I
authors.lastname: Hoffman
authors.forename: Sam
authors.initials: S
authors.lastname: Heye
authors.forename: David
authors.initials: D
authors.lastname: Cassiman
keywords: Portal hypertension; endoscopy; liver; percutaneous intervention; stent