title: Presenting a case of a mucinous adenocarcinoma of an exstrophic bladder in an adult patient and a review of literature.
abstract: BACKGROUND
  Bladder exstrophy occurs in approximately 1 in 35,000 live births and is associated with an increased incidence of bladder cancer.
  
  
  METHODS
  A 55-year old male patient was diagnosed with a primary mucinous adenocarcinoma of an unreconstructed exstrophic bladder. Examination of the entire gastrointestinal tract shown there were not other primary cites. Immunohistochemistry confirmed the nature of the tumour. The patient underwent a radical cystoprostatectomy with en block bilateral pelvic lymphadenectomy, urinary diversion with a cutaneous ureterostomy and epidpadias repair.
  
  
  CONCLUSIONS
  Adult bladder exstrophy and epispadia correction is a very rare practice in urology due the fact that this congenital disease is diagnosed and corrected in neonates. We advocate the radical surgical management, after exclusion of any primary malignant sites related to the gastrointestinal tract.
authors.forename: Giovanni
authors.initials: G
authors.lastname: Di Lauro
authors.forename: Fabrizio
authors.initials: F
authors.lastname: Iacono
authors.forename: Antonio
authors.initials: A
authors.lastname: Ruffo
authors.forename: Leo
authors.initials: L
authors.lastname: Romis
authors.forename: Salvatore
authors.initials: S
authors.lastname: Mordente
authors.forename: Umberto
authors.initials: U
authors.lastname: Pane
authors.forename: Ester
authors.initials: E
authors.lastname: Illiano
authors.forename: Giuseppe
authors.initials: G
authors.lastname: Romeo
authors.forename: Domenico
authors.initials: D
authors.lastname: Prezioso
authors.forename: Bruno
authors.initials: B
authors.lastname: Amato
mesh_terms: D002288:Adenocarcinoma, Mucinous / Q000150:complications*; D001746:Bladder Exstrophy / Q000150:complications*; D006801:Humans; D008297:Male; D008875:Middle Aged; D001749:Urinary Bladder Neoplasms / Q000150:complications*