title: A rare aetiology of respiratory failure in a 10-year-old boy: inflammatory myofibroblastic tumour.
abstract: Primary neoplasms of the respiratory tract are rarely encountered in the paediatric population. Inflammatory myofibroblastic tumour (IMT) is a rare soft tissue mesenchymal tumour but a distinct disease entity accounting for less than 1% of all primary lung tumours. We report a case of a 10-year-old boy who presented with respiratory failure and left lung collapse. On flexible fiberoptic bronchoscopy, a pedunculated mass in the lower part of the trachea originating from the left main stem bronchus was identified. The patient subsequently underwent a left-sided pneumonectomy with complete resection of the mass. The histopathological analysis was consistent with IMT. Two years of follow-up and the patient remains well.
authors.affiliation: Medical College, The Aga Khan University Hospital, Karachi, Sindh, Pakistan.
authors.forename: Ali
authors.initials: A
authors.lastname: Khawaja
authors.forename: Prem Kumar
authors.initials: PK
authors.lastname: Maheshwari
authors.forename: Anwarul
authors.initials: A
authors.lastname: Haque
authors.forename: Ali Bin Sarwar
authors.initials: AB
authors.lastname: Zubairi
mesh_terms: D001999:Bronchoscopy; D002648:Child; D003937:Diagnosis, Differential; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging / Q000473:pathology; D008175:Lung Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D008297:Male; D009379:Neoplasms, Muscle Tissue / Q000150:complications* / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D011013:Pneumonectomy; D011859:Radiography; D012131:Respiratory Insufficiency / Q000209:etiology*