title: Epidemiology of pulmonary arterial hypertension.
abstract: Changes in the epidemiology of pulmonary arterial hypertension (PAH) have resulted from changes in classification schemes and an increased emphasis on diagnosis because of the availability of effective therapies. The terms primary pulmonary hypertension and secondary pulmonary hypertension are considered inappropriate, confusing, and should not be used. Recent registries of patients with PAH have provided improved data regarding prognosis in the era of advanced therapies.
authors.affiliation: Annals of Internal Medicine, American College of Physicians; Penn Presbyterian Medical Center, University of Pennsylvania Perelman School of Medicine, 190 North Independence Mall West, Philadelphia, PA 19104, USA. Electronic address: darren.taichman@uphs.upenn.edu.
authors.forename: Darren B
authors.initials: DB
authors.lastname: Taichman
authors.forename: Jess
authors.initials: J
authors.lastname: Mandel
mesh_terms: D065627:Familial Primary Pulmonary Hypertension; D049672:History, 19th Century; D049673:History, 20th Century; D006801:Humans; D006976:Hypertension, Pulmonary / Q000145:classification* / Q000175:diagnosis / Q000453:epidemiology / Q000266:history; D011379:Prognosis
keywords: Anorectic drugs; HIV infection; Hemolytic anemia; Idiopathic pulmonary arterial hypertension; Portopulmonary hypertension; Pulmonary arterial hypertension; Pulmonary veno-occlusive disease; Systemic sclerosis