title: Primary intracranial ectopic craniopharyngioma in a patient with probable Gardner's syndrome.
abstract: The authors describe a patient with an adamantinomatous craniopharyngioma (CPG) arising in the cerebellopontine angle (CPA), who also had probable Gardner's syndrome. This 31-year-old man presented with headache and dizziness. Brain CT and MRI showed a 5 × 4-cm lesion with multiple small calcifications in the left CPA. The patient underwent suboccipital craniotomy with tumor removal. Histopathological findings indicated an adamantinomatous CPG. This patient also showed characteristics of Gardner's syndrome. Although this syndrome is associated with intracranial neoplasms, it is unclear whether patients with both Gardner's syndrome and CPG are part of the heterogeneity of Gardner's syndrome.
authors.affiliation: Departments of Neurosurgery.
authors.forename: Myoung Soo
authors.initials: MS
authors.lastname: Kim
authors.forename: You Sun
authors.initials: YS
authors.lastname: Kim
authors.forename: Hye Kyung
authors.initials: HK
authors.lastname: Lee
authors.forename: Ghi Jai
authors.initials: GJ
authors.lastname: Lee
authors.forename: Chan Young
authors.initials: CY
authors.lastname: Choi
authors.forename: Chae Heuck
authors.initials: CH
authors.lastname: Lee
mesh_terms: D025601:Adenomatous Polyposis Coli Protein / Q000235:genetics; D000328:Adult; D001921:Brain / Q000000981:diagnostic imaging / Q000473:pathology; D001932:Brain Neoplasms / Q000150:complications; D002530:Cerebellopontine Angle; D003397:Craniopharyngioma / Q000150:complications / Q000235:genetics / Q000473:pathology*; D003399:Craniotomy; D005500:Follow-Up Studies; D005736:Gardner Syndrome / Q000150:complications / Q000235:genetics / Q000473:pathology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D019635:Neurosurgical Procedures; D010911:Pituitary Neoplasms / Q000150:complications / Q000235:genetics / Q000473:pathology*; D016634:Radiosurgery; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
chemical_list: D025601:Adenomatous Polyposis Coli Protein