title: Percutaneous device closure of Abernethy malformation--a treatable cause of hepatopulmonary syndrome.
abstract: An eight-year-old girl was evaluated for unexplained cyanosis. A contrast echo was suggestive of pulmonary arteriovenous fistula. Further evaluation revealed Abernethy malformation (type 2) leading to hepatopulmonary syndrome. Percutaneous device closure of Abernethy malformation was done after anatomical and physiological evaluation of the portal circulation. Prior to closure, it is important to ensure adequate portal radicals into the liver and normal portal pressure after test balloon occlusion. Subcostal echocardiography can diagnose and guide device closure of Abernethy malformation, a treatable cause of hepatopulmonary syndrome.
authors.affiliation: Department of Cardiology, Sreechitra Tirunal Institute For Medical Sciences and Technology, Thiruvananthapuram, Kerala, India.
authors.forename: Subramanian
authors.initials: S
authors.lastname: Venkateshwaran
authors.forename: Kavassery Mahadevan
authors.initials: KM
authors.lastname: Krishnamoorthy
authors.forename: Sivasubramonian
authors.initials: S
authors.lastname: Sivasankaran
mesh_terms: D001164:Arteriovenous Fistula / Q000175:diagnosis / Q000209:etiology / Q000628:therapy; D002648:Child; D003937:Diagnosis, Differential; D018618:Echocardiography, Doppler, Color; D057510:Endovascular Procedures / Q000295:instrumentation*; D005260:Female; D006530:Hepatorenal Syndrome / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D006801:Humans; D018810:Magnetic Resonance Angiography; D011169:Portal Vein / Q000002:abnormalities* / Q000503:physiopathology; D011474:Prosthesis Design; D011651:Pulmonary Artery / Q000002:abnormalities; D011667:Pulmonary Veins / Q000002:abnormalities; D012039:Regional Blood Flow; D055989:Septal Occluder Device; D013152:Splanchnic Circulation; D016896:Treatment Outcome; D054079:Vascular Malformations / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology / Q000628:therapy*; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000503:physiopathology
keywords: Pediatric interventions; fistulas/shunts; pulmonary angiography