title: Haemangiopericytoma of the jaw.
abstract: Haemangiopericytoma (HPC) is a vascular tumour which originates in the pericytes of vessels and therefore it may occur at any site, but it is very uncommon in the jaw. From January 2000 to December 2011, a retrospective analysis of nine consecutive patients with HPCJ was performed. There were five patients with a primary tumour and four patients with a recurrent tumour. Of the nine patients, eight were male and one female. Their ages ranged from 23 years to 51 years, with a median age of 38 years. The tumours were located in the mandible in six patients and in maxilla in three cases. The median course of disease was 7.6 months (range 2-12 months). All patients underwent surgery. Two patients had postoperative adjuvant radiotherapy, and two cases were given postoperative adjuvant chemotherapy. The median follow-up period was 49 months (10-101 months). One patient suffered from lumbar metastasis, while another case had metastasis at local and multiple distant sites, and eventually died. There was no local recurrence or metastasis in other seven cases. HPCJ are rare and the clinical characteristics are not specific. The first choice of treatment is radical surgery. Adjuvant radiotherapy may be effective to improve the prognosis of HPCJ.
authors.affiliation: Department of Oncology, Cancer Hospital/Cancer Institute, Shanghai Medical College, Fudan University, Shanghai, China; Department of Oral and Maxillofacial-Head and Neck Oncology, Stomatology Hospital of Xi'an Jiaotong University College of Medicine, Xi'an, China.
authors.forename: Alimujiang
authors.initials: A
authors.lastname: Wushou
authors.affiliation: Department of Oral and Maxillofacial-Head and Neck Oncology, Stomatology Hospital of Xi'an Jiaotong University College of Medicine, Xi'an, China.
authors.forename: Xiu Feng
authors.initials: XF
authors.lastname: Bai
authors.affiliation: Department of Oral Pathology, Stomatology Hospital of Xi'an Jiaotong University College of Medicine, Xi'an, China.
authors.forename: Hong
authors.initials: H
authors.lastname: Qi
authors.affiliation: Department of Oral and Maxillofacial-Head and Neck Oncology, Stomatology Hospital of Xi'an Jiaotong University College of Medicine, Xi'an, China.
authors.forename: Zhe
authors.initials: Z
authors.lastname: Xu
authors.affiliation: Department of Oral and Maxillofacial-Head and Neck Oncology, Stomatology Hospital of Xi'an Jiaotong University College of Medicine, Xi'an, China.
authors.forename: Jun
authors.initials: J
authors.lastname: Zheng
authors.affiliation: Department of Oral and Maxillofacial-Head and Neck Oncology, Stomatology Hospital of Xi'an Jiaotong University College of Medicine, Xi'an, China. Electronic address: alimjan.wushur@gmail.com.
authors.forename: Gang
authors.initials: G
authors.lastname: Li
mesh_terms: D000328:Adult; D044963:Biopsy, Fine-Needle / Q000379:methods; D017024:Chemotherapy, Adjuvant; D005260:Female; D005500:Follow-Up Studies; D006393:Hemangiopericytoma / Q000556:secondary / Q000601:surgery*; D006801:Humans; D008159:Lumbar Vertebrae / Q000473:pathology; D008297:Male; D008339:Mandibular Neoplasms / Q000601:surgery*; D008441:Maxillary Neoplasms / Q000601:surgery*; D008875:Middle Aged; D037981:Neck Dissection / Q000379:methods; D009361:Neoplasm Invasiveness; D009364:Neoplasm Recurrence, Local / Q000601:surgery; D018714:Radiotherapy, Adjuvant; D019651:Plastic Surgery Procedures / Q000379:methods; D012189:Retrospective Studies; D013125:Spinal Neoplasms / Q000556:secondary; D015996:Survival Rate; D016896:Treatment Outcome; D055815:Young Adult
keywords: Haemangiopericytoma; Jaw; Outcome; Treatment