title: Scimitar Syndrome and H-type Tracheo-esophageal Fistula in a Newborn Infant.
abstract: Scimitar syndrome is a rare congenital anomaly characterized by partial anomalous pulmonary venous drainage of the right lung to the inferior vena cava (IVC) creating a tubular opacity paralleling the right cardiac border on chest radiography which resembles a curved Turkish sword or scimitar. Associated pulmonary and vascular anomalies have been reported in cases of Scimitar syndrome, most commonly hypoplasia of right lung, dextroposition of the heart, hypoplasia of the right pulmonary artery, and aberrant arterial supply from the descending aorta to the affected lobe of the right lung. To the best of our knowledge, this is the first case of Scimitar syndrome with an H-type tracheoesophageal fistula that has ever been reported.
authors.affiliation: Department of Pediatrics-Internal Medicine, WVU School of Medicine, Morgantown, WV 26505, USA.
authors.forename: Allison
authors.initials: A
authors.lastname: Lastinger
authors.affiliation: Department of Pediatrics, WVU School of Medicine, Morgantown, WV 26505, USA.
authors.forename: Malek
authors.initials: M
authors.lastname: El Yaman
authors.affiliation: Department of Pediatric Cardiovascular and Thoracic Surgery, WVU School of Medicine, Morgantown, WV 26505, USA.
authors.forename: Robert
authors.initials: R
authors.lastname: Gustafson
authors.affiliation: Department of Pediatrics-Internal Medicine, WVU School of Medicine, Morgantown, WV 26505, USA. Electronic address: pyossuck@hsc.wvu.edu.
authors.forename: Panitan
authors.initials: P
authors.lastname: Yossuck
mesh_terms: D006801:Humans; D007231:Infant, Newborn; D008297:Male; D012587:Scimitar Syndrome / Q000150:complications* / Q000000981:diagnostic imaging; D014138:Tracheoesophageal Fistula / Q000150:complications* / Q000000981:diagnostic imaging
keywords: H-type trachea-esophageal fistula; PAPVR; Scimitar syndrome; partial anomalous pulmonary venous return