title: Aggressive fibromatosis of the head and neck in the pediatric population.
abstract: BACKGROUND
  Aggressive fibromatosis, previously referred to as desmoid tumor, is a rare tumor. It is classified as benign, however, has a high potential for local invasion and recurrence. It is most commonly found in the abdomen, with an origin in the head and neck accounting for less than a quarter of the total cases.
  
  
  METHODS
  Literature review using PubMed and OVID and a combination of the words, "desmoid", "fibromatosis", "pediatric", "children", and "head and neck".
  
  
  RESULTS
  Annual occurrence is 0.2 - 0.4 per 100,000, with origins in the head and neck accounting for 10-25%. Since 1954, 97 cases of pediatric head and neck fibromatosis were reported. The age range was from birth to 16 years, with the average being 4 years and 5 months old. The overwhelming majority of tumors were of the mandible (38%). 74% patients underwent a large resection as the primary treatment modality. The most common treatment complication was tumor recurrence (16%).
  
  
  CONCLUSIONS
  Fibromatosis is a rare tumor of muscoloaponeurotic origin. Surgery is the mainstay of treatment; however recurrence rates are high, even despite negative surgical margins.
authors.affiliation: Department of Otorhinolaryngology, Louisiana State University-Health Science Center, 533 Bolivar Street Suite 566, New Orleans, LA 70112, USA.
authors.forename: Sarah
authors.initials: S
authors.lastname: Peña
authors.affiliation: Department of Otorhinolaryngology, Louisiana State University-Health Science Center, 533 Bolivar Street Suite 566, New Orleans, LA 70112, USA.
authors.forename: Todd
authors.initials: T
authors.lastname: Brickman
authors.affiliation: Department of Plastic Surgery, Louisiana State University-Health Science Center, New Orleans, LA 70112, USA.
authors.forename: Hugo
authors.initials: H
authors.lastname: StHilaire
authors.affiliation: Department of Otorhinolaryngology, Louisiana State University-Health Science Center, 533 Bolivar Street Suite 566, New Orleans, LA 70112, USA. Electronic address: ajeyak@lsuhsc.edu.
authors.forename: Anita
authors.initials: A
authors.lastname: Jeyakumar
mesh_terms: D002648:Child; D002675:Child, Preschool; D018222:Desmoid Tumors / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D006258:Head and Neck Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology* / Q000601:surgery; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local; D014057:Tomography, X-Ray Computed
keywords: Desmoid tumor; Fibromatosis