title: Unusual presentation of intussusception of the small bowel with peutz jeghers syndrome: report of a case.
abstract: The Peutz Jeghers syndrome (PJS) is an autosomal dominant disorder which is characterised by hamartomatous polyposes of the gastrointestinal tract, melanin pigmentation of the skin and mucous membranes, and an increased risk for cancer. We are reporting a case of a 15-year-old male with Peutz Jeghers syndrome, who presented to us with features of chronic intestinal obstruction and anaemia. Initially, patient was managed conservatively, but later on, an elective exploratory laparotomy was done for definitive management of intussusception. Laparotomy revealed a jejuno-jejunal intussusception with spontaneous recanalisation of gut which contained a long segment of gangrenous small bowel in the lumen. Resection and anastomosis of the jejunal segment was done. To the best of our knowledge, this might be the first case report on spontaneous recanalisation of small intestine.
authors.affiliation: Assistant Professor, Department of Surgery, G. R. Medical College , Gwalior, Madhya Pradesh, India .
authors.forename: Ashish
authors.initials: A
authors.lastname: Shrivastava
authors.forename: Akshara
authors.initials: A
authors.lastname: Gupta
authors.forename: Achal
authors.initials: A
authors.lastname: Gupta
authors.forename: Jyoti
authors.initials: J
authors.lastname: Shrivastava
keywords: Peutz Jeghers syndrome; acute abdomen; hamartomatous polyp; intussusception; spontaneous recanalisation