title: Annuloaortic ectasia in a patient with congenital absence of the left pericardium.
abstract: We report a patient with congenital absence of the left pericardium with development of progressive annuloaortic ectasia and aortic insufficiency during a 12-year period. The patient was treated with a Bentall procedure. Pathologic examination of the aorta revealed cystic medial necrosis. The surgical management and a possible association between congenital absence of pericardium and Marfan syndrome are discussed.
authors.affiliation: Division of Cardiac Surgery, The Ohio State University Wexner Medical Center, Columbus, Ohio.
authors.forename: Chigozirim N
authors.initials: CN
authors.lastname: Ekeke
authors.forename: Curt
authors.initials: C
authors.lastname: Daniels
authors.forename: Subha V
authors.initials: SV
authors.lastname: Raman
authors.forename: Charles
authors.initials: C
authors.lastname: Hitchcock
authors.forename: Steven E
authors.initials: SE
authors.lastname: Katz
authors.forename: Juan A
authors.initials: JA
authors.lastname: Crestanello
mesh_terms: D000015:Abnormalities, Multiple; D001021:Aortic Valve / Q000002:abnormalities* / Q000601:surgery; D001022:Aortic Valve Insufficiency / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D006348:Cardiac Surgical Procedures / Q000379:methods*; D003937:Diagnosis, Differential; D006801:Humans; D019028:Magnetic Resonance Imaging, Cine; D008297:Male; D008875:Middle Aged; D010496:Pericardium / Q000002:abnormalities* / Q000601:surgery; D014057:Tomography, X-Ray Computed
keywords: 26