title: Noncoronary sinus of Valsalva rupture into the right atrium with a coexisting perimembranous ventricular septal defect.
abstract: Ruptured sinus of Valsalva is very uncommon, and is < 1% of all congenital defects. The incidence ranges from 0.1%-3.5%. There is a male to female predominance of 4:1, with the highest incidence in the Asian population. Higher incidence is also seen in patients with Marfan's syndrome and Ehlers Danlos syndrome. There is a higher association of ruptured sinus of Valsalva with ventricular septal defect (VSD), aortic stenosis, and bicuspid valve defect. While most patients with VSD often have rupture of their right coronary sinus of Valsalva into the right ventricle due to poor structural integrity, we present a rare case of a patient with VSD who had rupture of his noncoronary sinus of Valsalva into the right atrium.
authors.affiliation: Long-Bao Cao, David Hannon, Assad Movahed, Department of Cardiovascular Sciences, East Carolina University, Brody School of Medicine, East Carolina Heart Institute, Greenville, NC 27858, United States.
authors.forename: Long-Bao
authors.initials: LB
authors.lastname: Cao
authors.forename: David
authors.initials: D
authors.lastname: Hannon
authors.forename: Assad
authors.initials: A
authors.lastname: Movahed
keywords: Rupture; Sinus of Valsalva; Ventricular septal defect; Wind sock deformity