title: Clinical and histological features of different types of Budd-Chiari syndrome: a comparison of 4 cases.
abstract: Budd-Chiari syndrome (BCS) is a rare condition characterized by hepatic venous outflow obstruction. In this report, we present 4 cases of BCS with complete and incomplete obstruction of the inferior vena cava (IVC) and hepatic vein (HV). Each case showed different and unique features of liver damage, which were attributed to the site and degree of obstruction. Interestingly, improved liver functions such as increased serum albumin levels, decreased hyaluronic acid levels and a normal indocyanine green clearance test were evident within 1 month of the balloon angioplasty. Pericellular fibrosis and hypervascular regenerative nodules were also reversible after obstruction removal. Therefore, it is very important to manage this rare disease before it progresses to liver cirrhosis.
authors.affiliation: Department of Gastroenterology and Hepatology, Kinki University School of Medicine, Osakasayama, Japan.
authors.forename: Naoshi
authors.initials: N
authors.lastname: Nishida
authors.forename: Shinichi
authors.initials: S
authors.lastname: Iwamura
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Ida
authors.forename: Satoshi
authors.initials: S
authors.lastname: Hagiwara
authors.forename: Yoshinori
authors.initials: Y
authors.lastname: Kagioka
authors.forename: Yasunori
authors.initials: Y
authors.lastname: Minami
authors.forename: Yoji
authors.initials: Y
authors.lastname: Maetani
authors.forename: Kyo
authors.initials: K
authors.lastname: Itoh
authors.forename: Masatoshi
authors.initials: M
authors.lastname: Kudo
mesh_terms: D006502:Budd-Chiari Syndrome / Q000145:classification* / Q000000981:diagnostic imaging / Q000473:pathology*; D005260:Female; D006503:Hepatic Veins / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D011859:Radiography; D014682:Vena Cava, Inferior / Q000000981:diagnostic imaging / Q000473:pathology; D055815:Young Adult