title: Late bidirectional glenn anastomosis in a 54-year-old patient with unoperated functionally univentricular heart.
abstract: We report the case of a 54-year-old patient with complex univentricular physiology who presented with worsening exercise intolerance, chronic cyanosis, and uncontrolled heart failure. Investigations included echocardiography, cardiac magnetic resonance imaging, and cardiac catheterization. After discussion in a multidisciplinary meeting, the patient underwent successful surgery that included a bidirectional Glenn anastomosis and repair of the atrioventricular (AV) junction. She recovered well and on follow-up had substantially less cyanosis and heart failure. We demonstrated that common AV valve repair and Glenn shunt can be used together successfully in appropriately selected older patients as palliation for complex congenital heart disease with functionally univentricular physiology.
authors: Northwest Adult Congenital Heart Disease Unit, Manchester Heart Centre, Central Manchester Foundation Trust, Oxford Road, Manchester, United Kingdom.
authors: Abdelrahman
authors: A
authors: Abdelbar
authors: Vaikom S
authors: VS
authors: Mahadevan
authors: Conal
authors: C
authors: Austin
authors: J Andreas
authors: JA
authors: Hoschtitzky
mesh_terms: D006328:Cardiac Catheterization; D004452:Echocardiography; D005260:Female; D018729:Fontan Procedure / Q000379:methods*; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D008875:Middle Aged
keywords: adult congenital heart disease; atrioventricular septal defect; cavopulmonary anastomosis; congenital heart disease (CHD); heart failure; single ventricle