title: Retroperitoneal Castlemans disease associated with paraneoplastic pemphigus.
abstract: Paraneoplastic pemphigus is a rare dermatologic condition that can occur as a paraneoplastic manifestation of lymphoproliferative disorders, visceral malignancies, Castleman disease and thymomas. In a pediatric age group paraneoplastic pemphigus has a striking association with Castleman disease and has a particularly poor prognosis in this age group. We describe a case of paraneoplastic pemphigus associated with retroperitoneal hyaline vascular variant of Castleman disease with a fatal outcome despite aggressive management.
authors: Dept of Radiodiagnosis, Sheri Kashmir Institute of Medical Sciences, Srinagar, India. Electronic address: naseerchoh@rediffmail.com.
authors: Naseer A
authors: NA
authors: Choh
authors: Dept of Dermatology, Sheri Kashmir Institute of Medical Sciences, Srinagar, India.
authors: Seema
authors: S
authors: Qayoom
authors: Dept of Radiodiagnosis, Sheri Kashmir Institute of Medical Sciences, Srinagar, India.
authors: Feroze
authors: F
authors: Shaheen
authors: Dept of Pathology, Sheri Kashmir Institute of Medical Sciences, Srinagar, India.
authors: Rais A
authors: RA
authors: Malik
authors: Dept of Radiodiagnosis, Sheri Kashmir Institute of Medical Sciences, Srinagar, India.
authors: Irfan
authors: I
authors: Rabbani
authors: Dept of Radiodiagnosis, Sheri Kashmir Institute of Medical Sciences, Srinagar, India.
authors: Tariq
authors: T
authors: Gojwari
mesh_terms: D000293:Adolescent; D005871:Castleman Disease / Q000150:complications*; D006801:Humans; D008297:Male; D010257:Paraneoplastic Syndromes / Q000473:pathology*; D010392:Pemphigus / Q000209:etiology* / Q000473:pathology*