title: Topsy-turvy heart: a very rare congenital rotational heart disease with tracheobronchial anomalies.
abstract: The topsy-turvy heart is characterized by a global 90°clockwise rotation around the heart's long axis. This rotation displaces all basal great arteries inferiorly and posteriorly, resulting in elongation and stretching of the brachiocephalic arteries and the bronchi. To date, reports of only four living cases have been published in the literature. We report here three new cases, with additional aortopulmonary window defects, and present their morphological details, clinical presentations, and our management.
authors: Department of Cardiovascular Surgery, Istanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Training and Research Hospital, Istanbul, Turkey.
authors: Ersin
authors: E
authors: Erek
authors: Alper
authors: A
authors: Guzeltas
authors: Nilufer Yalindag
authors: NY
authors: Ozturk
authors: Gursu
authors: G
authors: Kiyan
authors: Fazilet
authors: F
authors: Karakoc
authors: Figen
authors: F
authors: Akalin
authors: Ender
authors: E
authors: Odemis
authors: Sinan
authors: S
authors: Arsan
mesh_terms: D001013:Aorta, Thoracic / Q000002:abnormalities*; D001980:Bronchi / Q000002:abnormalities*; D003241:Consanguinity; D005260:Female; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007223:Infant; D008297:Male; D014057:Tomography, X-Ray Computed; D014102:Torsion Abnormality / Q000601:surgery*; D014132:Trachea / Q000002:abnormalities*; D014188:Transposition of Great Vessels / Q000601:surgery*; D016896:Treatment Outcome
keywords: airway; aortic arch; bronchus; cardiac anatomy; congenital heart disease