title: Immunoglobulin g4 non-related sclerosing disease with intracardiac mass mimicking mitral stenosis: case report.
abstract: The cardiovascular system may be one of the target organs of both immunoglobulin G4 related and non-related systemic multifocal fibrosclerosis. We present a case of IgG4 non-related systemic multifocal fibrosclerosis mimicking mitral stenosis on echocardiography. For a more detailed differential diagnosis, we used multimodal imaging techniques. After surgical biopsy around the abdominal aortic area in the retroperitoneum, histological examination revealed IgG4 non-related systemic multifocal fibrosclerosis. We describe the multimodal imaging used to diagnose IgG4 non-related systemic multifocal fibrosclerosis and a positive response to steroid treatment. There have been no previous case reports of IgG4 non-related systemic multifocal fibrosclerosis with intracardiac involvement. Here, we report a case of IgG4 non-related systemic multifocal fibrosclerosis mimicking mitral stenosis.
authors: Department of Internal Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.
authors: Ji-won
authors: JW
authors: Hwang
authors: Sung-Ji
authors: SJ
authors: Park
authors: Hye bin
authors: Hb
authors: Gwag
authors: Jung Min
authors: JM
authors: Ha
authors: Woo Joo
authors: WJ
authors: Lee
authors: Eun
authors: E
authors: Kim
authors: Sehyo
authors: S
authors: Yune
authors: Jung-Sun
authors: JS
authors: Kim
authors: Yang Jin
authors: YJ
authors: Park
authors: Duk-Kyung
authors: DK
authors: Kim
mesh_terms: D000368:Aged; D001012:Aorta, Abdominal / Q000473:pathology; D003937:Diagnosis, Differential; D004452:Echocardiography; D005260:Female; D006801:Humans; D007074:Immunoglobulin G / Q000097:blood* / Q000276:immunology; D008279:Magnetic Resonance Imaging; D008946:Mitral Valve Stenosis / Q000175:diagnosis; D009206:Myocardium / Q000473:pathology*; D010537:Peritoneum / Q000601:surgery; D049268:Positron-Emission Tomography; D012185:Retroperitoneal Fibrosis / Q000151:congenital* / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000188:drug therapy; D013256:Steroids / Q000627:therapeutic use; D014057:Tomography, X-Ray Computed
chemical_list: D007074:Immunoglobulin G; D013256:Steroids
keywords: Immunoglobulin G4 Non-Related Sclerosing Disease; Left Atrium Mass; Mitral Valve Stenosis; Periaortitis