title: Porokeratosis of Mibelli--literature review and a case report.
abstract: Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report.
authors.affiliation: São Paulo Federal University, Paulista Medical School.
authors.forename: Flávia Regina
authors.initials: FR
authors.lastname: Ferreira
authors.affiliation: University of Taubaté, University Hospital of Taubaté, Dermatology Service, TaubatéSP, Brazil.
authors.forename: Leopoldo Duailibe Nogueira
authors.initials: LD
authors.lastname: Santos
authors.affiliation: University of Taubaté, University Hospital of Taubaté, Dermatology Service, TaubatéSP, Brazil.
authors.forename: Fernando Augusto Nogueira Mendes
authors.initials: FA
authors.lastname: Tagliarini
authors.affiliation: University of Taubaté, Medicine Department, Medicine Department, TaubatéSP, Brazil.
authors.forename: Marcia Lanzoni de Alvarenga
authors.initials: ML
authors.lastname: Lira
mesh_terms: D002675:Child, Preschool; D005148:Facial Dermatoses / Q000473:pathology*; D005260:Female; D006801:Humans; D017499:Porokeratosis / Q000473:pathology*; D012867:Skin / Q000473:pathology