title: Phacomatosis pigmentovascularis type IIa--case report.
abstract: Phacomatosis Pigmentovascularis is a rare syndrome characterized by capillary malformation and pigmentary nevus. A case of a 2-year-old patient is reported, who presented extensive nevus flammeus and an aberrant Mongolian spot, without systemic disease, manifestations that allow us to classify this case as type IIa Phacomatosis Pigmentovascularis, according to Hasegawa's classification.
authors.affiliation: Federal University for Health Sciences, Porto AlegreRS, Brazil.
authors.forename: Majoriê Mergen
authors.initials: MM
authors.lastname: Segatto
authors.affiliation: Sanitary Dermatology Outpatient Clinic, Porto AlegreRS, Brazil.
authors.forename: Eloísa Unfer
authors.initials: EU
authors.lastname: Schmitt
authors.affiliation: Sanitary Dermatology Outpatient Clinic, Porto AlegreRS, Brazil.
authors.forename: Laura Netto
authors.initials: LN
authors.lastname: Hagemann
authors.affiliation: Sanitary Dermatology Outpatient Clinic, Porto AlegreRS, Brazil.
authors.forename: Roberta Castilhos da
authors.initials: RC
authors.lastname: Silva
authors.affiliation: Sanitary Dermatology Outpatient Clinic, Porto AlegreRS, Brazil.
authors.forename: Cristiane Almeida Soares
authors.initials: CA
authors.lastname: Cattani
mesh_terms: D002675:Child, Preschool; D006201:Hair Diseases / Q000473:pathology; D006801:Humans; D008297:Male; D049328:Mongolian Spot / Q000473:pathology*; D020752:Neurocutaneous Syndromes / Q000145:classification / Q000473:pathology*; D009507:Nevus of Ota / Q000473:pathology*; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000473:pathology*