title: Bilateral cerebellar dysplastic gangliocytomas (lhermitte duclos disease) with cerebellar ectopia and presyrinx cord changes. A case report.
abstract: Lhermitte-Duclos disease (LDD) is a rare cerebellar lesion with features of both malformation and benign neoplasm. However, the fundamental nature of the entity, its pathogenesis, and the exact genetic alterations remain unknown. We describe a rare case of bilateral LDD with cerebellar ectopia and presyrinx spinal cord changes. Bilaterality of lesions should argue against a neoplastic origin and support a hamartomatous origin.
authors.affiliation: All India Institute of Medical Sciences; New Delhi, India - ajaygarg1971@yahoo.com.
authors.forename: A S
authors.initials: AS
authors.lastname: Puri
authors.forename: A
authors.initials: A
authors.lastname: Garg
authors.forename: N K
authors.initials: NK
authors.lastname: Mishra
authors.forename: S B
authors.initials: SB
authors.lastname: Gaikwad
authors.forename: V S
authors.initials: VS
authors.lastname: Mehta
authors.forename: S
authors.initials: S
authors.lastname: Cirillo