title: Portal hypertension and acute liver failure as uncommon manifestations of primary amyloidosis.
abstract: Hepatic involvement in primary amyloidosis is an infrequent challenge to the hepatologist. Although usually asymptomatic, amyloidosis may have unusual manifestations. Liver biopsy is an important diagnostic tool for this condition. Herein, we report three cases of portal hypertension related to primary hepatic amyloidosis, one of them in the form of acute liver failure.
authors.affiliation: Departments of Gastroenterology School of Medicine, Pontificia Universidad Católica de Chile. Santiago, Chile.
authors.forename: Blanca
authors.initials: B
authors.lastname: Norero
authors.affiliation: Departments of Gastroenterology School of Medicine, Pontificia Universidad Católica de Chile. Santiago, Chile.
authors.forename: Rosa María
authors.initials: RM
authors.lastname: Pérez-Ayuso
authors.affiliation: Department of Pathology School of Medicine, Pontificia Universidad Católica de Chile. Santiago, Chile.
authors.forename: Ignacio
authors.initials: I
authors.lastname: Duarte
authors.affiliation: Department of Hemato-oncology, School of Medicine, Pontificia Universidad Católica de Chile. Santiago, Chile.
authors.forename: Pablo
authors.initials: P
authors.lastname: Ramirez
authors.affiliation: Departments of Gastroenterology School of Medicine, Pontificia Universidad Católica de Chile. Santiago, Chile.
authors.forename: Alejandro
authors.initials: A
authors.lastname: Soza
authors.affiliation: Departments of Gastroenterology School of Medicine, Pontificia Universidad Católica de Chile. Santiago, Chile.
authors.forename: Marco
authors.initials: M
authors.lastname: Arrese
authors.affiliation: Departments of Gastroenterology School of Medicine, Pontificia Universidad Católica de Chile. Santiago, Chile.
authors.forename: Carlos
authors.initials: C
authors.lastname: Benítez
mesh_terms: D000368:Aged; D000686:Amyloidosis / Q000150:complications* / Q000378:metabolism / Q000473:pathology; D005260:Female; D006801:Humans; D006975:Hypertension, Portal / Q000209:etiology*; D000075363:Immunoglobulin Light-chain Amyloidosis; D007145:Immunoglobulin kappa-Chains / Q000378:metabolism; D008099:Liver / Q000473:pathology; D017114:Liver Failure, Acute / Q000209:etiology* / Q000378:metabolism / Q000473:pathology; D008297:Male; D008875:Middle Aged; D009101:Multiple Myeloma / Q000150:complications / Q000378:metabolism
chemical_list: D007145:Immunoglobulin kappa-Chains