title: Management of tetralogy of Fallot with unilateral absence of pulmonary artery: an overview.
abstract: Tetralogy of Fallot with unilateral absence of pulmonary artery (PA) is a rare congenital anomaly that has been reported in isolated case reports and small case series. There is no well-defined treatment algorithm for these patients, and repair has been associated with high mortality, although survival is improving in the more recent era. Recent reports suggest strict case selection criteria based on PA dimensions and size of the left ventricle.
authors.affiliation: Department of Cardiothoracic Surgery, Apollo Hospitals, Bangalore, Karnataka, India.
authors.forename: Balram
authors.initials: B
authors.lastname: Babu
authors.forename: Christopher A
authors.initials: CA
authors.lastname: Caldarone
mesh_terms: D013504:Cardiovascular Surgical Procedures / Q000401:mortality; D006801:Humans; D018579:Patient Selection; D011651:Pulmonary Artery / Q000002:abnormalities*; D012720:Severity of Illness Index; D016019:Survival Analysis; D013771:Tetralogy of Fallot / Q000175:diagnosis* / Q000401:mortality / Q000601:surgery*; D016896:Treatment Outcome
keywords: Nakata index; cyanotic heart disease; tetralogy of Fallot; unilateral absence of pulmonary artery