title: Desmoplastic small round cell tumor: a case report and review of the literature.
abstract: Desmoplastic small round cell tumor is a rare malignant tumor that has a poor prognosis. It affects predominantly young males. In the current report, a 14-year-old male patient was admitted to the hospital for evaluation of abdominal distension, and abdominal pain. Imaging examination revealed a high prevalence of multiple intraperitoneal and liver parenchymal cystic and solid tumors. After an explorative surgery, the pathological findings confirmed the presentation of desmoplastic small round cell tumor. Diagnosis of desmoplastic small round cell tumor could easily have been overlooked since there was no specific evidence for this condition available in the clinical and imaging examinations. In the present study, ultrasound examination detected solid cystic masses, which suggested the presence of necrosis and hemorrhage. Immunohistochemistry and cytogenetic studies confirmed the diagnosis of desmoplastic small round cell tumor in this patient.
authors.forename: Xiang
authors.initials: X
authors.lastname: Li
authors.forename: Jing
authors.initials: J
authors.lastname: Yu
authors.forename: Shibao
authors.initials: S
authors.lastname: Fang
authors.forename: Xiaoming
authors.initials: X
authors.lastname: Xing
authors.affiliation: Department of Pathology, Affiliated Hospital of Medical College Qingdao University, 16 Jiangsu Road, Qingdao 266003, China. qdjzhao2013@163.com.
authors.forename: Jie
authors.initials: J
authors.lastname: Zhao
mesh_terms: D000008:Abdominal Neoplasms / Q000378:metabolism / Q000473:pathology*; D000293:Adolescent; D014408:Biomarkers, Tumor / Q000378:metabolism*; D058405:Desmoplastic Small Round Cell Tumor / Q000378:metabolism / Q000473:pathology*; D006801:Humans; D007124:Immunoenzyme Techniques; D008297:Male; D011379:Prognosis
chemical_list: D014408:Biomarkers, Tumor