title: Malignant triton tumor: a rare case.
abstract: Malignant triton tumor (MTT) is a malignant peripheral nerve sheath tumor (MPNST) with rhabdomyoblastic differentiation. This rare tumor, with fewer than 100 cases reported in the literature, generally affects adult patients with neurofibromatosis 1 (NF-1). We report such a case in a 34-year-old man with NF-1 who presented with a mass over the medial side of the arm. Histopathologically finding of rhabdomyoblasts among malignant Schwann cells in a tumor arising from a peripheral nerve supported by immunostaining with S-100 protein and myogenin confirmed the diagnosis. MTT has a poor prognosis owing to its aggressive biological behavior. The fact that this tumor is extremely rare has prompted us to report this case.
authors.affiliation: Department of Pathology and Surgical, Bhagwan Mahaveer Jain Hospital, Bangalore, Karnataka 560052 India.
authors.forename: Prasad K
authors.initials: PK
authors.lastname: Shetty
authors.affiliation: Department of Pathology and Surgical, Bhagwan Mahaveer Jain Hospital, Bangalore, Karnataka 560052 India.
authors.forename: Sameer V
authors.initials: SV
authors.lastname: Baliga
authors.affiliation: Department of Pathology and Surgical, Bhagwan Mahaveer Jain Hospital, Bangalore, Karnataka 560052 India.
authors.forename: Kopparthi
authors.initials: K
authors.lastname: Balaiah
keywords: Malignant peripheral nerve sheath tumor (MPNST); Malignant triton tumor (MTT); Neurofibromatosis-1 (NF-1); S-100 protein