title: Primary intrarenal neuroblastoma with hypertension and disseminated intravascular coagulation.
abstract: The primary intrarenal neuroblastoma (IRNB) is a rare condition. Intrarenal neuroblastoma typically results from direct renal invasion from an adrenal neuroblastoma, but true intrarenal neuroblastoma originates either sequestered adrenal rests during the fetal life or intrarenal sympathetic ganglia. Clinical, radiological, and pathological correlation is very essential for diagnosis and appropriate management of this type of unusual cases. The distinction of this rare tumor from Wilms' tumor is an important challenge since both tumors have major differences in prognostic and therapeutic response. We present a 3-year-old boy of primary intrarenal neuroblastoma with extensive abdominal and mediastinal mass, persistent hypertension, and disseminated intravascular coagulation (DIC).
authors.affiliation: Pediatric Congenital Hematologic Disorders Research Center, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran ; Department of Pediatric Hematology-Oncology, Mofid Children Hospital, Shariati Avenue, Tehran 15468-15514, Iran.
authors.forename: Bibi Shahin
authors.initials: BS
authors.lastname: Shamsian
authors.affiliation: Pediatric Congenital Hematologic Disorders Research Center, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Mohammad
authors.initials: M
authors.lastname: Kajizadi
authors.affiliation: Research Center for Immunodeficiencies, Children's Medical Center, Tehran University of Medical Sciences, Tehran 14194, Iran ; Molecular Immunology Research Center, School of Medicine, Tehran University of Medical Sciences, Tehran 14194, Iran ; Department of Immunology, School of Medicine, Tehran University of Medical Sciences, Tehran 14194, Iran.
authors.forename: Nima
authors.initials: N
authors.lastname: Rezaei
authors.affiliation: Department of Pediatric Radiology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Nozar
authors.initials: N
authors.lastname: Ghojehvand
authors.affiliation: Department of Pediatric Radiology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Roxana
authors.initials: R
authors.lastname: Azma
authors.affiliation: Department of Pediatric Surgery, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Mohsen
authors.initials: M
authors.lastname: Rouzrokh
authors.affiliation: Department of Pediatric Pathology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Maryam
authors.initials: M
authors.lastname: Kazemi Aghdam
authors.affiliation: Department of Pediatric Radiology, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Seyed Malek
authors.initials: SM
authors.lastname: Mesbah
authors.affiliation: Pediatric Congenital Hematologic Disorders Research Center, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Farid
authors.initials: F
authors.lastname: Ghazizadeh
authors.affiliation: Pediatric Congenital Hematologic Disorders Research Center, Mofid Children's Hospital, Shahid Beheshti University of Medical Sciences, Tehran 15468-15514, Iran.
authors.forename: Mohammad Taghi
authors.initials: MT
authors.lastname: Arzanian