title: Schnitzler Syndrome.
abstract: A 48-year-old man with typical features of Schnitzler Syndrome is presented, followed by a discussion of the pathogenesis and clinical aspects of this rare disease. Some of the challenges we and others have faced in diagnosing and treating this disease are also discussed. Clinical pearls and pitfalls are emphasized to aid clinicians from varying specialties in recognizing this syndrome and providing appropriate therapy. Schnitzler Syndrome is associated with high morbidity and increased risk of lymphoproliferative disorders. Accurate diagnosis is vital in restoring quality of life and ensuring appropriate long-term monitoring.
authors.affiliation: 1School of Medicine, University of Kansas Medical Center, Kansas City, Kansas.
authors.forename: Ahmed H
authors.initials: AH
authors.lastname: Badawi
authors.forename: Selina
authors.initials: S
authors.lastname: Gierer
authors.forename: Garth R
authors.initials: GR
authors.lastname: Fraga
mesh_terms: D000305:Adrenal Cortex Hormones / Q000008:administration & dosage / Q000627:therapeutic use; D006801:Humans; D008297:Male; D008875:Middle Aged; D019873:Schnitzler Syndrome / Q000175:diagnosis* / Q000188:drug therapy; D012867:Skin / Q000473:pathology; D016896:Treatment Outcome; D014657:Vasculitis / Q000473:pathology
chemical_list: D000305:Adrenal Cortex Hormones