Touraine Solente Gole syndrome: The elephant skin disease.
Touraine Solente Gole syndrome is a rare hereditary syndrome of primary pachydermoperiostosis, with the characteristic triad of pachydermia (or elephant like skin), periostosis and acropachia. A 27-year-old patient presented with aesthetic deformity of forehead due to deep skin folds and coarsening of facial features due to progressive thickening of skin. Associated palmoplantar hyperkeratosis with broadened of finger and toe tips and digital clubbing were noticed. Dermatologic evaluation revealed cutis verticis gyrata of scalp, seborrhoeic hyperplasia of face and hyperhidrosis. Natural history of the disease and aetiopathogenesis were reviewed. Aesthetic correction of forehead through frontal rhytidectomy was attempted.
Department of Plastic & Reconstructive Surgery, Calicut, Kerala, India.
T M Sheeja
TM
Rajan
Department of Plastic & Reconstructive Surgery, Calicut, Kerala, India.
N C
NC
Sreekumar
Department of Dermatology & Venerology, Government Medical College, Calicut, Kerala, India.
S
S
Sarita
Department of Plastic & Reconstructive Surgery, Calicut, Kerala, India.
K R
KR
Thushara
Clubbing; cutis verticis gyrata; frontal rhytidectomy; hypertrophic osteoarthropathy; pachyderma; periostosis