The experience of neurofibromatosis type I originating from pterygopalatine fossa and salivary gland.
One patient of neurofibromatosis type I originating from the pterygopalatine fossa and salivary gland underwent surgery in our department. At the outset, the case was misdiagnosed as arising from salivary gland tumors, and surgery was immediately performed. The tumor was entered directly, which induced ferocious bleeding. The subsequent hemostasis with tamponade and compression caused intracranial venous sinus thrombosis, which induced irreversible intracranial complications and finally resulted in death. The experience regarding the diagnosis and treatment of the case was retrospectively reviewed and shared in this article.
From the Department of Otolaryngology-Head & Neck Surgery, Shanghai JiaoTong University Affiliated First People's Hospital, Shanghai, China.
Bin
B
Jin
Bin
B
Shen
Pin
P
Dong
Hongming
H
Xu
Fei
F
Wang
D016063:Blood Loss, Surgical / Q000503:physiopathology; D003951:Diagnostic Errors; D017809:Fatal Outcome; D006470:Hemorrhage / Q000209:etiology; D006488:Hemostasis, Surgical; D006801:Humans; D007431:Intraoperative Complications / Q000209:etiology; D008297:Male; D019300:Medical Errors; D009456:Neurofibromatosis 1 / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000601:surgery*; D056739:Pterygopalatine Fossa / Q000000981:diagnostic imaging / Q000601:surgery*; D012468:Salivary Gland Neoplasms / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000601:surgery*; D012851:Sinus Thrombosis, Intracranial / Q000209:etiology; D014057:Tomography, X-Ray Computed; D055815:Young Adult