OHVIRA syndrome presenting with acute abdomen: a case report and review of the literature.
Uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis (OHVIRA) or Herlyn-Werner-Wunderlich (HWW) syndrome is a rare congenital urogenital anomaly. A 13-year-old female presented with acute abdominal pain and dysmenorrhea. Ultrasonography and magnetic resonance imaging showed uterus didelphys, hematometrocolpos, obstructed hemivagina, and right renal agenesis. Hemivaginal septal resection and anastomosis between the obstructed hemivagina and the normal vagina was tried, but it was not possible. Unilateral hysterectomy was performed. HWW syndrome may present with acute abdomen and is usually treated with vaginal septum resection and drainage of the hematometrocolpos.
Istanbul University School of Medicine, Department of Obstetrics and Gynecology, Istanbul, Turkey.
Funda
F
Gungor Ugurlucan
Istanbul University School of Medicine, Department of Obstetrics and Gynecology, Istanbul, Turkey. Electronic address: ercan.bastu@istanbul.edu.tr.
Ercan
E
Bastu
Istanbul Haseki State Hospital, Department of Radiology, Istanbul, Turkey.
Gokce
G
Gulsen
Istanbul University School of Medicine, Department of Obstetrics and Gynecology, Istanbul, Turkey.
Meryem
M
Kurek Eken
Istanbul University School of Medicine, Department of Obstetrics and Gynecology, Istanbul, Turkey.
Suleyman Engin
SE
Akhan
D000006:Abdomen, Acute / Q000175:diagnosis*; D015746:Abdominal Pain / Q000175:diagnosis*; D000015:Abnormalities, Multiple / Q000175:diagnosis*; D000293:Adolescent; D000013:Congenital Abnormalities / Q000175:diagnosis*; D005260:Female; D006801:Humans; D007044:Hysterectomy; D007668:Kidney / Q000002:abnormalities*; D007674:Kidney Diseases / Q000151:congenital* / Q000175:diagnosis; D008279:Magnetic Resonance Imaging; D013577:Syndrome; D014564:Urogenital Abnormalities / Q000175:diagnosis* / Q000601:surgery; D014599:Uterus / Q000002:abnormalities* / Q000601:surgery; D014621:Vagina / Q000002:abnormalities* / Q000601:surgery
Mullerian anomaly; OHVIRA syndrome; Obstructed hemivagina; Unilateral hysterectomy; Uterus didelphys; Vaginoplasty