Giant remnant of fetal circulation leading to cyanosis: pseudo-cor triatriatum dexter.
Remnants of the right valve of the sinus venosus, which fail to regress may present as an obstructing membrane within the right atrium as a very rare congenital anomaly. When associated with an atrial septal defect, primary cyanosis may occur due to a large right-to-left shunt. We report on a 1-week old girl with a pseudo-cor triatriatum dexter and immediate cyanosis after an uncomplicated birth. She was successfully treated with surgical excision of the obstructing membrane.
Department of Pediatric Cardiac Surgery, Children's Heart Center Giessen, Justus-Liebig-University, Giessen, Germany.
Can
C
Yerebakan
Klaus
K
Valeske
Anoosh
A
Esmaeili
Hakan
H
Akintuerk
D006348:Cardiac Surgical Procedures; D003310:Cor Triatriatum / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D003490:Cyanosis / Q000175:diagnosis / Q000209:etiology* / Q000503:physiopathology; D018618:Echocardiography, Doppler, Color; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D016896:Treatment Outcome
Cardiac surgery; Congenital; Cor triatriatum; Cyanosis; Right atrium