PEComa: A Perivascular Epithelioid Cell Tumor in the Liver-A Case Report and Review of the Literature.
Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemotherapy including mTOR inhibitors for malignant tumors. Here we discuss the radiological and pathological diagnosis, evaluation, and management of a hepatic PEComa. We describe a 51-year-old patient who was diagnosed incidentally after unusual physical exam findings.
Division of Hematology/Oncology, MD Anderson Cancer Center Orlando, 1400 South Orange, MP 700, Orlando, FL 32806, USA.
Faseeh
F
Khaja
Division of Hematology/Oncology, MD Anderson Cancer Center Orlando, 1400 South Orange, MP 700, Orlando, FL 32806, USA.
Allison
A
Carilli
Division of Hematology/Oncology, MD Anderson Cancer Center Orlando, 1400 South Orange, MP 700, Orlando, FL 32806, USA.
Said
S
Baidas
Pathology Department, Orlando Health, 1414 Kuhl Avenue, Orlando, FL 32806, USA.
Aravindhan
A
Sriharan
Pathology Department, Orlando Health, 1414 Kuhl Avenue, Orlando, FL 32806, USA.
Shanedelle
S
Norford