[The portopulmonary hypertension: an overview from diagnosis to treatment].
Portopulmonary hypertension (POPH) refers to the condition of pulmonary arterial hypertension (PAH) in association with portal hypertension. Among patients with portal hypertension, reported incidence rates of POPH range from 2 to 10% and long-term prognosis in cases of POPH is poor. Fundamental issues of management of POPH include identification of patients likely to benefit from liver transplantation (LTx) and treatment with specific pulmonary vasodilators before and after LTx. This review presents as an overview of the current knowledge on the epidemiology, diagnosis, treatment and prognosis of patients with portopulmonary hypertension.
Department of Translational Medical Sciences, University "Federico II", Naples, Italy. antonio.cittadini@unina.it
Andrea
A
Salzano
Department of Translational Medical Sciences, University "Federico II", Naples, Italy.
Domenico
D
Sirico
Department of Translational Medical Sciences, University "Federico II", Naples, Italy.
Luisa
L
Golia
Department of Translational Medical Sciences, University "Federico II", Naples, Italy.
Valentina
V
Faga
Department of Translational Medical Sciences, University "Federico II", Naples, Italy.
Martina
M
Flora
Department of Cardiology and Cardiac Surgery, University Hospital "Scuola Medica Salernitana", Salerno, Italy.
Eduardo
E
Bossone
Department of Translational Medical Sciences, University "Federico II", Naples, Italy.
Antonio
A
Cittadini
D006801:Humans; D006975:Hypertension, Portal / Q000150:complications* / Q000175:diagnosis / Q000628:therapy; D006976:Hypertension, Pulmonary / Q000150:complications* / Q000175:diagnosis / Q000628:therapy