Angiokeratoma circumscriptum in a young male.
A 20-year-old male presented with multiple eruptions on his right leg since birth; these bled and were painful on trivial trauma. Examination revealed dark brown, hyperkeratotic, indurated, verrucous linear plaques with irregular borders. Histopathological evidence of hyperkeratosis, acanthosis, and extensive vascular proliferation in papillary dermis confirmed clinical suspicion of angiokeratoma circumscriptum (AKC). Excision and skin grafting yielded a cosmetically favorable outcome. Angiokeratomas, first described by Mibeli in 1889, are a group of vascular ectasias involving the papillary dermis. Angiokeratomas are more common in males; however, AKC-the rarest of its five variants-exhibits a female preponderance (F:M:3:1). AKC is an extremely rare nevoid disorder, only 100 of its cases having been reported in the world literature until 2006. Herein, we have reported a typical case of AKC in a young male that was previously misdiagnosed, and the patient wrongly counseled about the likelihood of its spontaneous regression.
Department of Dermatology, Dr. D. Y. Patil Medical College and Hospital, Pimpri, Pune, Maharashtra, India.
Dinkar
D
Sadana
Department of Dermatology, Dr. D. Y. Patil Medical College and Hospital, Pimpri, Pune, Maharashtra, India.
Yugal K
YK
Sharma
Department of Dermatology, Dr. D. Y. Patil Medical College and Hospital, Pimpri, Pune, Maharashtra, India.
Kedarnath
K
Dash
Department of Dermatology, Dr. D. Y. Patil Medical College and Hospital, Pimpri, Pune, Maharashtra, India.
Nitin D
ND
Chaudhari
Department of Pathology, Dr. D. Y. Patil Medical College and Hospital, Pimpri, Pune, Maharashtra, India.
Arpana Anil
AA
Dharwadkar
Department of Surgery, Dr. D. Y. Patil Medical College and Hospital, Pimpri, Pune, Maharashtra, India.
Bharat B
BB
Dogra
Angiokeratoma circumscriptum; vascular malformation; verrucous hemangioma