Monosegmental hepatobiliary fibropolycystic disease mimicking a mass: report of three cases.
Hepatobiliary fibropolycystic diseases are a unique group of entities involving the liver and biliary tract, which are caused by abnormal embryologic development of the ductal plates at various stages. We experienced strange hepatobiliary fibropolycystic diseases with a complex mass composed of malformed ducts and biliary cysts, which did not belong to, and were different from, previously known malformations. They were unique in imaging and histologic features. We herein report three cases of monosegmental hepatobiliary fibropolycystic disease mimicking a mass.
Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.
Jung Hyeok
JH
Kwon
Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.
Mi Jeong
MJ
Kim
Department of Radiology, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.
Young Hwan
YH
Kim
Department of Hepatobiliary Surgery, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.
Koo Jeong
KJ
Kang
Department of Pathology, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.
Yu Na
YN
Kang
Department of Pathology, Keimyung University School of Medicine, Dongsan Medical Center, Daegu 700-712, Korea.
Sun Young
SY
Kwon
D000328:Adult; D001649:Bile Duct Diseases / Q000175:diagnosis*; D003560:Cysts / Q000175:diagnosis*; D003952:Diagnostic Imaging / Q000379:methods; D005260:Female; D005355:Fibrosis / Q000175:diagnosis; D005705:Gallbladder Diseases / Q000175:diagnosis; D006801:Humans; D008103:Liver Cirrhosis / Q000175:diagnosis; D008107:Liver Diseases / Q000175:diagnosis*; D008113:Liver Neoplasms / Q000175:diagnosis; D008297:Male
Caroli disease; Ductal plate malformations; Fibropolycystic disease; Monosegmental disease