A case of ichthyosis hystrix: unusual manifestation of this rare disease.
Ichthyosis hystrix is a term used to describe an ichthyosiform dermatosis which is characterized by hyperkeratotic spiny scales mainly over extensor aspects of limbs with palmoplantar keratoderma and occasionally associated with deafness and neurological deficit. It is a rare autosomal dominant form of ichthyosis and very few cases are reported in literature. We are presenting a 46 years-old-male patient of ichthyosis hystrix with unusual presentation. He had lesions mainly over the face and scalp with palmoplantar keratoderma and significant nail changes.
Departments of Dermatology, Institute of Post Graduate Medical Education Research, Kolkata, India.
Projna
P
Biswas
Departments of Dermatology, Institute of Post Graduate Medical Education Research, Kolkata, India.
Abhishek
A
De
Departments of Dermatology, Institute of Post Graduate Medical Education Research, Kolkata, India.
Sampreeti
S
Sendur
Departments of Dermatology, Institute of Post Graduate Medical Education Research, Kolkata, India.
Falguni
F
Nag
Departments of Dermatology, Institute of Post Graduate Medical Education Research, Kolkata, India.
Archana
A
Saha
Departments of Dermatology, Institute of Post Graduate Medical Education Research, Kolkata, India.
Gobinda
G
Chatterjee
Ichthyosis; onychogryphosis; porcupine