[Surgical management of a spontaneous dissection of the celiac axis caused by fibromuscular dysplasia. First clinical report].
The clinical case of a 46 years old male is reported, who complained of a sudden and sharp epigastric pain, with no other accompanying symptoms or signs. The patient was evaluated in the emergency department of a local hospital and the clinical and laboratory analysis excluded the occurrence of a common acute abdominal pathology. A CT and an angio CT study disclosed a spontaneous dissection and aneurismal dilatation of the celiac axis, along its extension. The patient underwent surgical management, consisting in the resection and prosthetic replacement of the celiac axis and the pathological studies of the specimen revealed a fibromuscular dysplasia, which seems to be, according to the literature, an exceptional situation, never reported before, thus justifying its publication and dissemination.
Departamentos de Cirurgia Vascular, de Anestesiologia e de Anatomia Patológica dos Hospital da Luz, Lisboa, Portugal.
A Dinis
AD
da Gama
Augusto
A
Ministro
Gonçalo
G
Cabral
Cristina
C
Pestana
Pedro
P
Oliveira
D015746:Abdominal Pain / Q000209:etiology; D000784:Aortic Dissection / Q000209:etiology / Q000473:pathology / Q000601:surgery*; D000792:Angiography / Q000379:methods; D002445:Celiac Artery / Q000473:pathology / Q000601:surgery*; D004636:Emergency Service, Hospital; D005352:Fibromuscular Dysplasia / Q000150:complications*; D006801:Humans; D008297:Male; D008875:Middle Aged; D014057:Tomography, X-Ray Computed