title: Spontaneous epidural and subdural hematoma in a child with afibrinogenemia and postoperative management.
abstract: Congenital afibrinogenemia is a rare coagulation disorder that exhibits recessive inheritance. The prevalence of this disease is around 1 per 1 000 000, but it is increased in countries where consanguineous marriages are common. Umbilical cord bleeding during the neonatal period is generally the first manifestation of the disease, but a later age of onset is not uncommon. This disease may also be manifested by gastrointestinal, genitourinary, mucosal, muscular, articular, and intracranial bleeding during childhood. Intracranial hemorrhage is a rare condition, but it is the leading cause of death in patients with afibrinogenemia. In this report, we present the case of a 13-year-old female patient with afibrinogenemia who underwent an operation for spontaneous massive extradural and subdural hematoma.
authors: aDepartment of Neurosurgery bDepartment of Pediatric Hematology-Oncology cDepartment of Pediatric Intensive Care Unit dDepartment of Pediatric Emergency, İzmir Behcet Uz Children's Training and Research Hospital, Izmir, Turkey.
authors: Asiyan Kilit
authors: AK
authors: Y
authors: Yontem
authors: Y
authors: Yaman
authors: Rana
authors: R
authors: Isguder
authors: Ozgur
authors: O
authors: Carti
authors: Bengu
authors: B
authors: Demirag
authors: Hasan
authors: H
authors: Agin
authors: Gulcihan
authors: G
authors: Ozek
authors: Burcak Gunes
authors: BG
authors: Tatli
authors: Esin
authors: E
authors: Albudak
authors: Emel
authors: E
authors: Berksoy
mesh_terms: D000293:Adolescent; D000347:Afibrinogenemia / Q000151:congenital* / Q000601:surgery; D019468:Disease Management; D005260:Female; D006407:Hematoma, Epidural, Cranial / Q000601:surgery*; D006408:Hematoma, Subdural / Q000601:surgery*; D006801:Humans; D011184:Postoperative Period