title: Pattern of inner retinal layers involvement in pigmented paravenous retinochoroidal atrophy as determined by SD-OCT: case report.
abstract: Pigmented paravenous retinochoroidal atrophy is an ocular disease characterized by outer retina and choroidal atrophy often with overlying intraretinal bone spicule pigment deposition along the retinal veins. As a rare condition, there is scant information in the literature regarding the pattern of inner retinal layers involvement. We present a case of a 41-year-old white man initially referred for a glaucoma evaluation. Fundoscopy revealed patches of retinochoroidal atrophy and light pigmentation extending from the optic nerve head along the inferior-temporal retinal veins in both eyes. Using different spectral-domain optical coherence tomography (SD-OCT) protocols we identified a significant thinning of the inner retinal layers along the inferior-temporal veins, but with a lucid interval surrounding the optic nerve head. Standard automated perimetry revealed a superior absolute arcuate scotoma sparing the central fixation (good structure-functional correlation). This pattern of inner retinal layers involvement was not previously described. We believe SD-OCT added significantly to the anatomical description of this case. Physicians should consider these new anatomical findings and correlate them with functional status while assessing these patients.
authors: Daniela Laura Melo
authors: DL
authors: Junqueira
authors: Flavio Siqueira Santos
authors: FS
authors: Lopes
authors: Luís Gustavo
authors: LG
authors: Biteli
authors: Tiago Santos
authors: TS
authors: Prata
mesh_terms: D000328:Adult; D002829:Choroid / Q000473:pathology*; D015785:Eye Diseases, Hereditary / Q000473:pathology*; D006801:Humans; D008297:Male; D009898:Optic Disk / Q000473:pathology; D015203:Reproducibility of Results; D012160:Retina / Q000473:pathology*; D012162:Retinal Degeneration / Q000473:pathology*; D012169:Retinal Vein / Q000473:pathology; D041623:Tomography, Optical Coherence / Q000379:methods*