title: Pseudomyxoma peritonei originating from urachus-case report and review of the literature.
abstract: Pseudomyxoma peritonei (pmp) is a rare clinical condition defined as extensive intraperitoneal spread of mucus associated with a variety of mucinous tumours of varying biologic behavior. Although appendix or ovaries have usually been implicated as the primary site, cases have been reported in association with neoplastic lesions of other sites. Pseudomyxoma peritonei originating from urachal remnants is a unique entity, reported only 18 times in the English literature thus far. Considering the rarity of the lesion, we report the case of a 50-year-old man surgically treated for pmp associated with a low-grade mucinous urachal neoplasm. Unique aspects of case are the low histologic aggressiveness of the causative lesion (reported only twice worldwide) and the early stage of the disease, with a relatively small amount of intraperitoneal free mucin. Review of the literature about pmp in general and a collation of previously reported cases of pmp originating from the urachus are presented and discussed.
authors: Second Department of General and Oncological Surgery, Wroclaw Medical University, Wroclaw, Poland.
authors: A K
authors: AK
authors: Agrawal
authors: Department of General Surgery ii , Lower-Silesian Specialised Hospital, Wroclaw, Poland.
authors: P
authors: P
authors: Bobiński
authors: Second Department of General and Oncological Surgery, Wroclaw Medical University, Wroclaw, Poland.
authors: Z
authors: Z
authors: Grzebieniak
authors: Wroclaw Medical University, Wroclaw, Poland.
authors: J
authors: J
authors: Rudnicki
authors: Second Department of General and Oncological Surgery, Wroclaw Medical University, Wroclaw, Poland.
authors: G
authors: G
authors: Marek
authors: Second Department of General and Oncological Surgery, Wroclaw Medical University, Wroclaw, Poland.
authors: P
authors: P
authors: Kobielak
authors: Second Department of General and Oncological Surgery, Wroclaw Medical University, Wroclaw, Poland.
authors: M
authors: M
authors: Kazanowski
authors: Wroclaw Medical University, Wroclaw, Poland.
authors: S
authors: S
authors: Agrawal
authors: Division of Pathomorphology and Oncological Cytology, Wroclaw Medical University, Wroclaw, Poland.
authors: A
authors: A
authors: Hałoń
keywords: Pseudomyxoma peritonei; mucinous neoplasms; urachal adenocarcinoma; urachus