title: [Abdominal angina due to fibromuscular dysplasia of the celiac axis. Surgical management].
abstract: The clinical case of a 27-year old man with the diagnosis of chronic mesenteric ischemia ("abdominal angina") is reported, whose chief complaints were severe postprandial pain and remarkable weight loss, for the last 4 months. Following na inconclusive observation in gastroenterology, he underwent an angiographic-CT examination, that disclosed a critical stenosis at the origin of the celiac axis. The remaining digestive vessels, superior and inferior mesenteric arteries, were found free of lesions. The patient was submitted to a revascularization procedure, consisting in the celiac axis resection and its replacement by a prosthetic graft, arising from the supraceliac aorta. The post-operative course was uneventfull, followed by a complete remission of the pain and a progressive weight gain. The histopathological study of the removed artery revealed the diagnosis of arterial fibrodysplasia, a very rare entity in clinical practice, of unknown etiology, affecting predominantely young people and in a decreasing order of frequency the renals, the internal carotids and the external iliac arteries. The localization of the fibrodysplastic disease to the celiac áxis seems to be a unique case, never reported before in the literature, thus justifying its publication and dissemination.
authors: Departamentos de Cirurgia Vascular, de Anestesiologia, de Medicina Interna e Intensiva e de Anatomia Patológica do Hospital da Luz, Lisboa, Portugal.
authors: Diogo
authors: D
authors: Cunha E Sá
authors: António
authors: A
authors: Rosa
authors: Germano Do
authors: GD
authors: Carmo
authors: Tiago
authors: T
authors: Costa
authors: Cristina
authors: C
authors: Pestana
authors: Alexandra
authors: A
authors: Horta
authors: Ana
authors: A
authors: Catarino
authors: A D
authors: AD
authors: Da Gama
mesh_terms: D000328:Adult; D002445:Celiac Artery; D005352:Fibromuscular Dysplasia / Q000150:complications*; D006801:Humans; D008297:Male; D065666:Mesenteric Ischemia / Q000209:etiology* / Q000601:surgery*