title: Soft-tissue necrosis complicating tibial osteotomy in a child with Proteus syndrome.
abstract: BACKGROUND
  Proteus syndrome is a rare congenital hamartomatous disease frequently responsible for musculoskeletal deformities. The results and complications of surgical treatment are not well documented owing to the scarcity of reported cases.
  
  
  METHODS
  The authors report a case of poor evolution of valgus proximal tibial osteotomy in a 6-year-old girl with Proteus syndrome. The surgery was complicated by extensive deep wound necrosis exposing the tibial bone, necessitating surgical excision, antibiotherapy and controlled wound healing. At 1 year postoperatively, the deformity recurred.
  
  
  CONCLUSIONS
  The possibility of serious wound complications and of recurrence must be kept in mind when operating on a limb deformity in patients with Proteus syndrome. Potential complications should be taken into account in selecting the surgical correction technique: epiphysiodesis may be preferable to osteotomy.
authors.affiliation: Service d'Orthopédie de l'Enfant et l'Adolescent, hôpital d'Enfants Béchir-Hamza de Tunis, Bab Saadoun, Tunis 1007, Tunisia. Electronic address: raboudi_taieb@yahoo.fr.
authors.forename: T
authors.initials: T
authors.lastname: Raboudi
authors.affiliation: Service d'Orthopédie de l'Enfant et l'Adolescent, hôpital d'Enfants Béchir-Hamza de Tunis, Bab Saadoun, Tunis 1007, Tunisia.
authors.forename: S
authors.initials: S
authors.lastname: Bouchoucha
authors.affiliation: Service d'Orthopédie de l'Enfant et l'Adolescent, hôpital d'Enfants Béchir-Hamza de Tunis, Bab Saadoun, Tunis 1007, Tunisia.
authors.forename: B
authors.initials: B
authors.lastname: Hamdi
authors.affiliation: Service d'Orthopédie de l'Enfant et l'Adolescent, hôpital d'Enfants Béchir-Hamza de Tunis, Bab Saadoun, Tunis 1007, Tunisia.
authors.forename: R
authors.initials: R
authors.lastname: Boussetta
authors.affiliation: Service d'Orthopédie de l'Enfant et l'Adolescent, hôpital d'Enfants Béchir-Hamza de Tunis, Bab Saadoun, Tunis 1007, Tunisia.
authors.forename: W
authors.initials: W
authors.lastname: Saied
authors.affiliation: Service d'Orthopédie de l'Enfant et l'Adolescent, hôpital d'Enfants Béchir-Hamza de Tunis, Bab Saadoun, Tunis 1007, Tunisia.
authors.forename: C
authors.initials: C
authors.lastname: Jalel
authors.affiliation: Service d'Orthopédie de l'Enfant et l'Adolescent, hôpital d'Enfants Béchir-Hamza de Tunis, Bab Saadoun, Tunis 1007, Tunisia.
authors.forename: M
authors.initials: M
authors.lastname: Smida
mesh_terms: D002648:Child; D005260:Female; D006801:Humans; D009336:Necrosis; D010019:Osteomyelitis / Q000473:pathology / Q000601:surgery; D010027:Osteotomy; D011183:Postoperative Complications; D016715:Proteus Syndrome / Q000150:complications*; D018461:Soft Tissue Infections / Q000473:pathology* / Q000601:surgery; D013977:Tibia / Q000601:surgery*
keywords: Genu varum; Hemi-hypertrophy; Macrodactyly; Proteus syndrome