title: Occlusion of the left main coronary artery os by a tethered aortic valve cusp.
abstract: We report a 4-month-old girl who presented with poor ventricular function and was found to have occlusion of the left main coronary artery os by a tethered aortic cusp. The patient underwent surgical delamination of the aortic valve leaflet, revealing a normal left coronary os. After operative repair, her left ventricular function improved significantly. This diagnosis should be included in the differential in all children presenting with cardiac dysfunction.
authors.affiliation: Division of Pediatric Cardiology, Vanderbilt University Medical Center, Nashville, Tennessee. Electronic address: jonathan.h.soslow@vanderbilt.edu.
authors.forename: Jonathan H
authors.initials: JH
authors.lastname: Soslow
authors.affiliation: Division of Pediatric Cardiology, Vanderbilt University Medical Center, Nashville, Tennessee.
authors.forename: Daniel L
authors.initials: DL
authors.lastname: Saurers
authors.affiliation: Division of Pediatric Cardiology, Vanderbilt University Medical Center, Nashville, Tennessee.
authors.forename: Debra A
authors.initials: DA
authors.lastname: Dodd
authors.affiliation: Division of Pediatric Cardiology, Vanderbilt University Medical Center, Nashville, Tennessee.
authors.forename: Thomas P
authors.initials: TP
authors.lastname: Doyle
authors.affiliation: Cardiothoracic Surgery, Vanderbilt University Medical Center, Nashville, Tennessee.
authors.forename: David P
authors.initials: DP
authors.lastname: Bichell
authors.affiliation: Division of Pediatric Cardiology, Vanderbilt University Medical Center, Nashville, Tennessee.
authors.forename: Ann
authors.initials: A
authors.lastname: Kavanaugh-McHugh
mesh_terms: D001021:Aortic Valve / Q000002:abnormalities* / Q000601:surgery; D002675:Child, Preschool; D054059:Coronary Occlusion / Q000209:etiology* / Q000601:surgery; D005260:Female; D006801:Humans