title: A novel approach in managing right-sided haemothorax in neurofibromatosis type 1.
abstract: Spontaneous haemothorax due to vasculopathy in patients with neurofibromatosis type 1 is rare but life-threatening. A 56-year-old lady with neurofibromatosis type 1 presented with right-sided chest pain, dyspnoea, and collapse. Computed tomography showed a right-sided hemothorax. Urgent angiography showed contrast leakage from a right subclavian artery pseudoaneurysm. A Gore Viabahn endovascular stent graft was deployed. Completion angiography revealed satisfactory haemostasis. She underwent video-assisted thoracoscopic evacuation of the hemothorax, with good results. This case highlights a novel approach to managing a rare emergency, using combined procedures.
authors.affiliation: Department of Thoracic Surgery, City Hospital, Nottingham, UK izanee.mydin@gmail.com.
authors.forename: Muhammad Izanee Mohamed
authors.initials: MI
authors.lastname: Mydin
authors.affiliation: Department of Thoracic Surgery, City Hospital, Nottingham, UK.
authors.forename: Amit
authors.initials: A
authors.lastname: Sharma
authors.affiliation: Department of Interventional Radiology, City Hospital, Nottingham, UK.
authors.forename: Zergham
authors.initials: Z
authors.lastname: Zia
authors.affiliation: Department of Thoracic Surgery, City Hospital, Nottingham, UK.
authors.forename: Mohammad
authors.initials: M
authors.lastname: Hawari
authors.affiliation: Department of Thoracic Surgery, City Hospital, Nottingham, UK.
authors.forename: Mehmood
authors.initials: M
authors.lastname: Jadoon
authors.affiliation: Department of Thoracic Surgery, City Hospital, Nottingham, UK.
authors.forename: Andrzej
authors.initials: A
authors.lastname: Majewski
mesh_terms: D017541:Aneurysm, False / Q000150:complications / Q000000981:diagnostic imaging / Q000628:therapy*; D000792:Angiography; D001807:Blood Vessel Prosthesis; D019917:Blood Vessel Prosthesis Implantation / Q000295:instrumentation / Q000379:methods; D004621:Embolization, Therapeutic / Q000379:methods; D057510:Endovascular Procedures / Q000295:instrumentation* / Q000379:methods*; D005260:Female; D006491:Hemothorax / Q000000981:diagnostic imaging / Q000209:etiology / Q000628:therapy*; D006801:Humans; D008875:Middle Aged; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000000981:diagnostic imaging; D015607:Stents; D013348:Subclavian Artery / Q000000981:diagnostic imaging* / Q000473:pathology; D013906:Thoracoscopy; D014057:Tomography, X-Ray Computed; D016896:Treatment Outcome
keywords: Aneurysm; endovascular stenting; haemothorax; neurofibromatosis 1; ruptured; subclavian artery