title: [Mauriac syndrome in Argentina in the XXI century: series of 5 cases].
abstract: Mauriac syndrome is associated with poor metabolic control of type 1 diabetes mellitus, hepatomegaly and elevated transaminases characterized by growth failure and delayed puberty, which may be reversible with good glycemic control. There are few references published in recent years following the introduction of glycemic self-monitoring, new insulins and intensified treatment. We describe a series of five patients evaluated in our service with Mauriac syndrome characteristics, conducting a literature review of cases in Argentina.
authors.affiliation: Servicio de Nutrición y Diabetes, Hospital Nacional de Pediatría Prof. Dr. Juan P. Garrahan.
authors.forename: Vanesa Verónica
authors.initials: VV
authors.lastname: Oeschgef
authors.affiliation: Servicio de Nutrición y Diabetes, Hospital Nacional de Pediatría Prof. Dr. Juan P. Garrahan.
authors.forename: Mariana
authors.initials: M
authors.lastname: Prieto
mesh_terms: D000293:Adolescent; D001118:Argentina; D002648:Child; D003480:Cushing Syndrome / Q000175:diagnosis; D003922:Diabetes Mellitus, Type 1 / Q000175:diagnosis; D005260:Female; D006130:Growth Disorders / Q000175:diagnosis; D006529:Hepatomegaly / Q000175:diagnosis; D006801:Humans; D008297:Male; D013577:Syndrome