title: [Linear IgA bullous dermatosis of childhood: case report].
abstract: Linear IgA bullous dermatosis is a rare acquired autoinmune vesiculobullous disease characterized by linear IgA deposit on the dermo-epidermal basement membrane observed with direct inmunofluorescence. The characteristic lesions are vesicles and tense serous bullae, which most often are grouped giving a "cluster of jewels" appearance. Differential diagnosis must be established with other autoimmune dermatosis, such as dermatitis herpetiformis and bullous pemphigoid. Dapsone is the first line therapy, with excellent response in a short period. This is a benign disease that tends to wax and wane in severity until it disappears spontaneously. We report the case of a 5-year-old girl presenting with bullous lesions, being diagnosed a linear IgA bullous dermatosis, with excellent response to dapsone in less than 2 weeks.
authors.affiliation: Consultorio Pudahuel.
authors.forename: Francisco
authors.initials: F
authors.lastname: Reyes-Baraona
authors.affiliation: Servicio de Dermatología, Pontificia Universidad Católica, Chile.
authors.forename: Romina
authors.initials: R
authors.lastname: Andino
authors.affiliation: Servicio de Dermatología, Pontificia Universidad Católica, Chile.
authors.forename: Juan Eduardo
authors.initials: JE
authors.lastname: Carrasco
authors.affiliation: Facultad de Medicina, Pontificia Universidad Católica, Chile.
authors.forename: Camila
authors.initials: C
authors.lastname: Arriagada
authors.affiliation: Servicio de Dermatología, Complejo Asistencial Doctor Sótero del Río, Santiago, Chile.
authors.forename: Silvia
authors.initials: S
authors.lastname: Guerrero
mesh_terms: D002675:Child, Preschool; D005260:Female; D006801:Humans; D062027:Linear IgA Bullous Dermatosis / Q000175:diagnosis