title: XY gonadal dysgenesis--development of a germ cell tumor: case report.
abstract: Gonadal dysgenesis (GD) is a rare congenital malformation that affects about one in 3,000 births. The authors present a case of a 17-year-old woman with primary amenorrhea and poor breast development. They conducted a laparoscopic surgery and bilaterally removed hypoplastic streak gonads. Histopathology of the ovaries revealed bilateral streak gonads with gonadoblastomas and a right-sided dysgerminoma.
authors.affiliation: Department of Obstetrics and Gynecology, Universitäts-Frauenklinik Würzburg, Würzburg, Germany.
authors.forename: J
authors.initials: J
authors.lastname: Diessner
authors.affiliation: Department of Obstetrics and Gynecology, Universitäts-Frauenklinik Würzburg, Würzburg, Germany.
authors.forename: T
authors.initials: T
authors.lastname: Stüber
authors.affiliation: Department of Obstetrics and Gynecology, Universitäts-Frauenklinik Würzburg, Würzburg, Germany.
authors.forename: B
authors.initials: B
authors.lastname: Niederle
authors.affiliation: Department of Obstetrics and Gynecology, Universitäts-Frauenklinik Würzburg, Würzburg, Germany.
authors.forename: M
authors.initials: M
authors.lastname: Pawlik
authors.affiliation: Department of Obstetrics and Gynecology, Universitäts-Frauenklinik Würzburg, Würzburg, Germany.
authors.forename: J
authors.initials: J
authors.lastname: Dietl
authors.affiliation: Department of Obstetrics and Gynecology, Universitäts-Frauenklinik Würzburg, Würzburg, Germany.
authors.forename: A
authors.initials: A
authors.lastname: Honig
mesh_terms: D000293:Adolescent; D000568:Amenorrhea / Q000209:etiology; D004407:Dysgerminoma / Q000150:complications* / Q000473:pathology / Q000601:surgery; D005260:Female; D006061:Gonadal Dysgenesis, 46,XY / Q000150:complications*; D018238:Gonadoblastoma / Q000150:complications / Q000473:pathology / Q000601:surgery; D006801:Humans; D010051:Ovarian Neoplasms / Q000150:complications* / Q000473:pathology / Q000601:surgery