title: Accessory tricuspid valve leaflet and an anomalous muscle bundle in the right ventricular outflow tract in a patient with double-outlet right ventricle: a rare case report.
abstract: Double-outlet right ventricle (DORV), a clinically important congenital heart disease, occurs in 1-3% of persons with congenital heart disease. It may occur as an isolated cardiac defect, together with other cardiac lesions, or in association with extracardiac anomalies. Other rare cardiac anomalies include an anomalous muscle bundle (AMB) in the right ventricular outflow tract (RVOT) and an accessory tricuspid valve leaflet. We report a very rare case of concomitant DORV, AMB in the RVOT and accessory tricuspid valve leaflet in a 17-year-old male patient. The patient eventually died from severe decompensated heart failure. To the best of our knowledge, such a case has not been previously reported in the literature.
authors.affiliation: Department of Cardiology, Faculty of Medicine, Mazandaran University of Medical Sciences, Sari, Iran.
authors.forename: Maryam
authors.initials: M
authors.lastname: Nabati
authors.forename: Mozhdeh
authors.initials: M
authors.lastname: Dabirian
authors.forename: Babak
authors.initials: B
authors.lastname: Bagheri
authors.forename: Ali
authors.initials: A
authors.lastname: Ghaemian
authors.forename: Mojtaba
authors.initials: M
authors.lastname: Shokri
mesh_terms: D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D000293:Adolescent; D003937:Diagnosis, Differential; D004452:Echocardiography / Q000379:methods; D006352:Heart Ventricles / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D006801:Humans; D008297:Male; D035583:Rare Diseases / Q000000981:diagnostic imaging; D014261:Tricuspid Valve / Q000002:abnormalities* / Q000000981:diagnostic imaging*; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging* / Q000209:etiology*
keywords: accessory mitral valve; anomalous muscle bundle; cardiac anomaly; cardiac defect; heart disease; right ventricle; tricuspid valve