title: Redo cardiac surgery for active prosthetic valve endocarditis associated with hereditary hemorrhagic telangiectasia: report of a case.
abstract: Hereditary hemorrhagic telangiectasia (HHT) is caused by an autosomal dominant gene and characterized by multiple arteriovenous malformations in several organs, leading to bleeding or shunting. These patients often suffer severe infections and heart failure, which should be managed in the perioperative period, when open heart surgery is indicated. We report a case of successful aortic root replacement for active prosthetic valve endocarditis and ventricular septal perforation in a patient with HHT, who had severe heart failure.
authors.affiliation: Department of Cardiovascular Surgery, Ehime University Hospital, Shitsukawa, Toon, Ehime, 791-0295, Japan, yukihtky@yahoo.co.jp.
authors.forename: Yuki
authors.initials: Y
authors.lastname: Nakamura
authors.forename: Fumiaki
authors.initials: F
authors.lastname: Shikata
authors.forename: Masahiro
authors.initials: M
authors.lastname: Ryugo
authors.forename: Toru
authors.initials: T
authors.lastname: Okamura
authors.forename: Takumi
authors.initials: T
authors.lastname: Yasugi
authors.forename: Hironori
authors.initials: H
authors.lastname: Izutani
mesh_terms: D000368:Aged; D001021:Aortic Valve / Q000601:surgery*; D001165:Arteriovenous Malformations / Q000150:complications; D006348:Cardiac Surgical Procedures; D018450:Disease Progression; D004697:Endocarditis, Bacterial / Q000209:etiology / Q000382:microbiology* / Q000601:surgery*; D005260:Female; D019918:Heart Valve Prosthesis Implantation; D006801:Humans; D019990:Perioperative Care; D012086:Reoperation; D013203:Staphylococcal Infections; D013212:Staphylococcus epidermidis; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications* / Q000601:surgery*; D016896:Treatment Outcome; D018658:Ventricular Septal Rupture / Q000209:etiology / Q000601:surgery