title: Hypertrophic cardiomyopathy with right ventricular outflow tract and left ventricular intracavitary obstruction.
abstract: Obstruction of the right ventricular outflow tract (RVOT) is a rare finding in hypertrophic cardiomyopathy (HCM) patients unlike left ventricular outflow tract (LVOT) obstruction. Although there are guidelines that aid in clinical decision making in patients with LVOT obstruction, there are none addressing RVOT obstruction. As RVOT obstruction may pose serious clinical implications similar to LVOT obstruction, appropriate medical and surgical management is very important. A unique phenotype of HCM with RVOT obstruction in conjunction with left ventricle (LV) intracavitary obstruction is discussed.
authors.affiliation: Cardiovascular Center, Tufts Medical Center, Tufts University School of Medicine, Boston, Massachusetts.
authors.forename: Rabiya
authors.initials: R
authors.lastname: Malik
authors.forename: Martin S
authors.initials: MS
authors.lastname: Maron
authors.forename: Hassan
authors.initials: H
authors.lastname: Rastegar
authors.forename: Natesa G
authors.initials: NG
authors.lastname: Pandian
mesh_terms: D000328:Adult; D002312:Cardiomyopathy, Hypertrophic / Q000150:complications / Q000000981:diagnostic imaging* / Q000503:physiopathology; D003937:Diagnosis, Differential; D019560:Echocardiography, Three-Dimensional / Q000379:methods*; D005260:Female; D005500:Follow-Up Studies; D006352:Heart Ventricles / Q000000981:diagnostic imaging* / Q000503:physiopathology; D006801:Humans; D016277:Ventricular Function, Left / Q000502:physiology*; D016278:Ventricular Function, Right / Q000502:physiology*; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging / Q000209:etiology* / Q000503:physiopathology
keywords: biventricular obstruction; hypertrophic cardiomyopathy; left ventricular intracavitary obstruction; right ventricular outflow tract obstruction