title: [Peritoneal pseudomyxoma: an overview emphasizing pathological assessment and therapeutic strategies].
abstract: Pseudomyxoma peritonei is a clinical entity characterized by a gelatinous ascite associated with mucinous tumor deposits spreading on peritoneal surface and potentially invading abdominal organs. It is considered as a tumor process linked, in most of cases, to a mucinous appendiceal neoplasm. Pseudomyxoma peritonei may benefit from a therapeutic strategy combining cytoreductive surgery and intra-peritoneal chemotherapy, which has led to a major prognosis improvement. Different classifications are available and the last one corresponds to the WHO 2010 version, which individualizes pseudomyxoma peritonei in two classes: low grade and high grade mucinous carcinoma. The very low frequency of this entity and its specific therapeutic strategy need specific health care centres, as well as physicians and pathologists collaborating through dedicated networks. The aim of this article is to summarize the pathology, causes, mechanisms and therapeutic approaches of pseudomyxoma peritonei, as well as their interfaces with dedicated networks.
authors.affiliation: Département d'anatomie pathologique, institut Gustave-Roussy, 94805 Villejuif, France.
authors.forename: Peggy
authors.initials: P
authors.lastname: Dartigues
authors.affiliation: Service d'anatomie pathologique, centre hospitalier Lyon-Sud, hospices civils de Lyon, 69495 Pierre-Bénite, France.
authors.forename: Sylvie
authors.initials: S
authors.lastname: Isaac
authors.affiliation: Pôle information médicale, unité de recherche clinique, hospices civils de Lyon, 69495 Lyon, France.
authors.forename: Laurent
authors.initials: L
authors.lastname: Villeneuve
authors.affiliation: Service de chirurgie générale et digestive, centre hospitalier Lyon-Sud, hospices civils de Lyon, 69495 Pierre-Bénite, France.
authors.forename: Olivier
authors.initials: O
authors.lastname: Glehen
authors.affiliation: Département d'anatomie pathologique, centre François-Baclesse, 14076 Caen, France.
authors.forename: Mathieu
authors.initials: M
authors.lastname: Capovilla
authors.affiliation: Service d'anatomie pathologique, CHU l'Archet II, 06200 Nice, France.
authors.forename: Anne
authors.initials: A
authors.lastname: Chevallier
authors.affiliation: Département d'anatomie pathologique, institut Bergonié, 33076 Bordeaux, France.
authors.forename: Sabrina
authors.initials: S
authors.lastname: Croce
authors.affiliation: Service d'anatomie pathologique, CHU Lariboisière, 75010 Paris, France.
authors.forename: Rachid
authors.initials: R
authors.lastname: Kaci
authors.affiliation: Service d'anatomie pathologique, CHRU de Hautepierre, 67091 Strasbourg, France.
authors.forename: Gerlinde
authors.initials: G
authors.lastname: Lang-Averous
authors.affiliation: Service d'anatomie pathologique, CHU Albert-Michallon, 38043 Grenoble, France.
authors.forename: Marie-Hélène
authors.initials: MH
authors.lastname: Laverriere
authors.affiliation: Département d'anatomie pathologique, institut de cancérologie de Lorraine, 54519 Vandœuvre-lès-Nancy, France.
authors.forename: Agnès
authors.initials: A
authors.lastname: Leroux-Broussier
authors.affiliation: Département d'anatomie pathologique, institut Claudius-Regaud, 31052 Toulouse, France.
authors.forename: Éliane
authors.initials: É
authors.lastname: Mery
authors.affiliation: Département d'anatomie pathologique, institut Paoli-Calmettes, 13273 Marseille, France.
authors.forename: Flora
authors.initials: F
authors.lastname: Poizat
authors.affiliation: Service d'anatomie pathologique, CHU Jean-Minjoz, 25030 Besançon, France.
authors.forename: Séverine
authors.initials: S
authors.lastname: Valmary-Degano
authors.affiliation: Service d'anatomie pathologique, centre Paul-Papin, 49933 Angers, France.
authors.forename: Véronique
authors.initials: V
authors.lastname: Verriele-Beurrier
authors.affiliation: Service de chirurgie générale et digestive, centre hospitalier Lyon-Sud, hospices civils de Lyon, 69495 Pierre-Bénite, France.
authors.forename: François-Noël
authors.initials: FN
authors.lastname: Gilly
authors.affiliation: Service d'anatomie pathologique, Institut Régional du Cancer de Montpellier-Val d'Aurelle, 34298 Montpellier, France. Electronic address: frederic.bibeau@icm.unicancer.fr.
authors.forename: Frédéric
authors.initials: F
authors.lastname: Bibeau
mesh_terms: D006801:Humans; D010534:Peritoneal Neoplasms / Q000145:classification / Q000473:pathology* / Q000628:therapy*; D011553:Pseudomyxoma Peritonei / Q000145:classification / Q000473:pathology* / Q000628:therapy*
keywords: Appendice; Networks; Pseudomyxoma peritonei; Pseudomyxomes péritonéaux; Rares tumors; Réseaux; Tumeurs rares