title: Transjugular melody valve placement in a small child with protein losing enteropathy.
abstract: The authors present a patient with situs inversus totalis, dextrocardia, and tetralogy of Fallot with complete AV canal who underwent pulmonary valve-sparing complete repair during infancy but developed progressive pulmonary outflow obstruction on serial follow-up. His right ventricular outflow tract (RVOT) was prestented as a precursor for Melody valve placement. After this, he developed protein losing enteropathy (PLE) which was unresponsive to medical management. Finally, he received transcatheter Melody valve percutaneously in the pulmonic position that lead to clinical and biochemical resolution of his PLE symptoms.
authors.affiliation: Rush Center for Congenital and Structural Heart Disease, Rush University Medical Center, Chicago, Illinois.
authors.forename: Kiran K
authors.initials: KK
authors.lastname: Mallula
authors.forename: Damien
authors.initials: D
authors.lastname: Kenny
authors.forename: Ziyad M
authors.initials: ZM
authors.lastname: Hijazi
mesh_terms: D000015:Abnormalities, Multiple; D006328:Cardiac Catheterization / Q000295:instrumentation* / Q000379:methods*; D006348:Cardiac Surgical Procedures / Q000009:adverse effects*; D002675:Child, Preschool; D018618:Echocardiography, Doppler, Color; D017548:Echocardiography, Transesophageal; D006330:Heart Defects, Congenital / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D006350:Heart Valve Prosthesis; D019918:Heart Valve Prosthesis Implantation / Q000295:instrumentation* / Q000379:methods*; D006801:Humans; D007601:Jugular Veins; D008297:Male; D011474:Prosthesis Design; D011504:Protein-Losing Enteropathies / Q000175:diagnosis / Q000209:etiology*; D011664:Pulmonary Valve / Q000000981:diagnostic imaging / Q000503:physiopathology; D011665:Pulmonary Valve Insufficiency / Q000175:diagnosis / Q000209:etiology / Q000503:physiopathology / Q000628:therapy*; D016896:Treatment Outcome
keywords: melody valve; percutaneous; protein losing enteropathy; transcatheter