title: A rare case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve.
abstract: Double-chambered right ventricle (DCRV) is a rare congenital heart disorder involving 2 different right ventricle (RV) pressure compartments that is often associated with ventricular septal defect (VSD). Usually, the obstruction is caused by an anomalous muscle bundle crossing the RV from the interventricular septum to the RV free wall. We are reporting a case of double-chambered right ventricle associated with ventricular septal defect and congenital absence of the pulmonary valve, a rare form of congenital infundibular pulmonary stenosis. In addition to ventricular septal defect, our patient had congenital absence of the pulmonary valve, which is very unusual and has never been reported to our knowledge.
authors.affiliation: Department of Cardiology, Staten Island University Hospital, Staten Island, NY.
authors.forename: Georges
authors.initials: G
authors.lastname: Khoueiry
authors.affiliation: Department of Cardiology, Staten Island University Hospital, Staten Island, NY.
authors.forename: Tariq
authors.initials: T
authors.lastname: Bhat
authors.affiliation: Department of Medicine, Staten Island University Hospital, Staten Island, NY. Corresponding author email: mohivddin_bhat@yahoo.com.
authors.forename: Mohmad
authors.initials: M
authors.lastname: Tantray
authors.affiliation: Department of Medicine, Staten Island University Hospital, Staten Island, NY. Corresponding author email: mohivddin_bhat@yahoo.com.
authors.forename: Mustafain
authors.initials: M
authors.lastname: Meghani
authors.affiliation: Department of Cardiology, Staten Island University Hospital, Staten Island, NY.
authors.forename: Nidal
authors.initials: N
authors.lastname: Abi Rafeh
authors.affiliation: Department of Medicine, Staten Island University Hospital, Staten Island, NY. Corresponding author email: mohivddin_bhat@yahoo.com.
authors.forename: Mokhtar
authors.initials: M
authors.lastname: Abdallah
authors.affiliation: Department of Cardiology, Staten Island University Hospital, Staten Island, NY.
authors.forename: Wissam
authors.initials: W
authors.lastname: Hoyek
keywords: cardiology; doubled-chambered right ventricle; echocardiography; magnetic resonance imaging; ventricular septal defect