title: Novel two-stage surgical treatment for Cantrell syndrome complicated by severe pulmonary hypertension: a case report.
abstract: BACKGROUND
  Cantrell syndrome is a rare syndrome of congenital defects, which can be complicated by severe pulmonary hypertension and left ventricular diverticulum; it has proved difficult to treat in clinical practice.
  
  
  METHODS
  A 6-month-old Han Chinese baby girl weighing 3.5 kg was diagnosed, using ultrasonography and radiography, as having Cantrell syndrome complicated by severe pulmonary hypertension. For safety, we divided management into two stages. For the first stage, we dealt with the left ventricular diverticulum and pulmonary hypertension. Three months later, we performed diorthosis for an intracardiac malformation.
  
  
  CONCLUSIONS
  Cantrell syndrome with pulmonary hypertension may respond well to this novel two-stage operation, which needs more verification via clinical practice.
authors.forename: Xiaochen
authors.initials: X
authors.lastname: Wu
authors.affiliation: Department of Cardiovascular, Chengdu Millitary General Hospital, 270th Rongdu Road, Chengdu City 610083, China. nowwilson@yeah.net.
authors.forename: Jinbao
authors.initials: J
authors.lastname: Zhang
authors.forename: Hui
authors.initials: H
authors.lastname: Ouyang
authors.forename: Qin
authors.initials: Q
authors.lastname: Yue
authors.forename: Heng
authors.initials: H
authors.lastname: Zhao
mesh_terms: D000208:Acute Disease; D004240:Diverticulum / Q000601:surgery; D005260:Female; D006352:Heart Ventricles / Q000002:abnormalities / Q000601:surgery; D006554:Hernia, Umbilical / Q000150:complications / Q000601:surgery; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology* / Q000601:surgery; D007223:Infant; D058502:Pentalogy of Cantrell / Q000150:complications* / Q000601:surgery