title: A fatal case of congenital pulmonary airway malformation with aspergillosis in an adult.
abstract: Congenital cystic adenomatoid malformation, currently referred as congenital pulmonary airway malformation (CPAM), is one of the rare lung malformations seen in adults. We report a case of a 59-year-old male with a chronic cough and hemoptysis that was not amenable to bronchial embolization. Further work up revealed cystic changes with fungal ball and type 1 CPAM. Patients with this condition who survive to adulthood usually suffer from recurrent respiratory bacterial infections. Only three cases of fungal involvement have ever been described. We present a fatal case, as well as the oldest patient.
authors.affiliation: Department of Internal Medicine, Richmond University Medical Center, Staten Island, NY, USA.
authors.forename: Hilary A
authors.initials: HA
authors.lastname: Enuh
authors.affiliation: Pulmonary and Critical Care Medicine, Richmond University Medical Center, Staten Island, NY, USA.
authors.forename: Edward L
authors.initials: EL
authors.lastname: Arsura
authors.affiliation: Pulmonary and Critical Care Medicine, Rutgers, The State University of New Jersey, New Jersey Medical School, Newark, NJ, USA.
authors.forename: Zaza
authors.initials: Z
authors.lastname: Cohen
authors.affiliation: Pulmonary and Critical Care Medicine, Richmond University Medical Center, Staten Island, NY, USA.
authors.forename: Keith T
authors.initials: KT
authors.lastname: Diaz
authors.affiliation: Pulmonary and Critical Care Medicine, Richmond University Medical Center, Staten Island, NY, USA.
authors.forename: Jay M
authors.initials: JM
authors.lastname: Nfonoyim
authors.affiliation: Pulmonary and Critical Care Medicine, Richmond University Medical Center, Staten Island, NY, USA.
authors.forename: Phillip J
authors.initials: PJ
authors.lastname: Cosentino
authors.affiliation: Infectious Disease Control Unit, Richmond University Medical Center, Staten Island, NY, USA.
authors.forename: Jessie K
authors.initials: JK
authors.lastname: Saverimuttu
keywords: CPAM; aspergillosis; embolization