title: Pseudohypoaldosteronism in a neonate presenting as life-threatening arrhythmia.
abstract: Neonatal hyperkalemia and hyponatremia are medical conditions that require an emergent diagnosis and treatment to avoid morbidity and mortality. Here, we describe the case of a 10-day-old female baby presenting with life-threatening hyperkalemia, hyponatremia, and metabolic acidosis diagnosed as autosomal dominant pseudohypoaldosteronism type 1 (PHA1). This report aims to recognize that PHA1 may present with a life-threatening arrhythmia due to severe hyperkalemia and describes the management of such cases in neonates.
  
  
  CONCLUSIONS
  PHA1 may present with a life-threatening arrhythmia.Presentation of PHA can be confused with congenital adrenal hyperplasia.Timing and appropriate medical management in the critical care unit prevented fatality from severe neonatal PHA.
authors.affiliation: College of Medicine, American University of Antigua Antigua.
authors.forename: Sudeep K
authors.initials: SK
authors.lastname: Rajpoot
authors.affiliation: Pediatric Intensive Care, Miller Children's Hospital Long Beach, California USA.
authors.forename: Carlos
authors.initials: C
authors.lastname: Maggi
authors.affiliation: Children Hospital of Orange County 1201 W. La Veta Ave, Orange, California 92868 USA.
authors.forename: Amrit
authors.initials: A
authors.lastname: Bhangoo