title: Superior mediastinal paraganglioma associated with von Hippel-Lindau syndrome: report of a case.
abstract: Extra-adrenal pheochromocytomas are termed paragangliomas. Paragangliomas in the mediastinum, especially the superior mediastinum, are extremely rare. It is known that paragangliomas or pheochromocytomas occur in combination with von Hippel-Lindau syndrome. We present the case of a non-functional superior mediastinal paraganglioma in a patient with von Hippel-Lindau syndrome, without a familial history suggestive of the condition. This case highlights that we should be aware of possible sporadic von Hippel-Lindau syndrome in patients with a mediastinal paraganglioma.
authors.affiliation: Department of Surgery, Yaizu City Hospital, 1000 Dobara, Yaizu-City, Shizuoka 425-8505, Japan. t_t1980@msn.com.
authors.forename: Tsuyoshi
authors.initials: T
authors.lastname: Takahashi
authors.forename: Hiroshi
authors.initials: H
authors.lastname: Nogimura
authors.forename: Ken
authors.initials: K
authors.lastname: Kuriki
authors.forename: Ryo
authors.initials: R
authors.lastname: Kobayashi
mesh_terms: D000293:Adolescent; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008479:Mediastinal Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D010235:Paraganglioma / Q000150:complications* / Q000175:diagnosis / Q000601:surgery; D011379:Prognosis; D006623:von Hippel-Lindau Disease / Q000150:complications* / Q000175:diagnosis / Q000601:surgery