Klippel-Trénaunay syndrome, pregnancy and the liver: an unusual interplay.
Klippel-Trénaunay syndrome is a rare congenital syndrome characterized by capillary malformations, soft tissue and bone hypertrophy, and varicose veins. There is a well-established risk for thrombotic complications in these patients. A case of a young patient diagnosed post partum with the very rare liver involvement is presented. The complex clinical course, the multidisciplinary management and the long-term outcome are discussed.
The Royal Free Sheila Sherlock Liver Centre and University Department of Surgery, Royal Free Hospital Hampstead, London UK (Dimitrios N. Samonakis, Penelope Manousou, Andrew K. Burroughs) ; Department of Gastroenterology and Hepatology, University Hospital of Heraklion, Crete, Greece (Dimitrios N. Samonakis, Pantelis Oustamanolakis, Elias A. Kouroumalis).
Dimitrios N
DN
Samonakis
Department of Gastroenterology and Hepatology, University Hospital of Heraklion, Crete, Greece (Dimitrios N. Samonakis, Pantelis Oustamanolakis, Elias A. Kouroumalis).
Pantelis
P
Oustamanolakis
The Royal Free Sheila Sherlock Liver Centre and University Department of Surgery, Royal Free Hospital Hampstead, London UK (Dimitrios N. Samonakis, Penelope Manousou, Andrew K. Burroughs).
Penelope
P
Manousou
Department of Gastroenterology and Hepatology, University Hospital of Heraklion, Crete, Greece (Dimitrios N. Samonakis, Pantelis Oustamanolakis, Elias A. Kouroumalis).
Elias A
EA
Kouroumalis
The Royal Free Sheila Sherlock Liver Centre and University Department of Surgery, Royal Free Hospital Hampstead, London UK (Dimitrios N. Samonakis, Penelope Manousou, Andrew K. Burroughs).
Andrew K
AK
Burroughs
Klippel-Trénaunay syndrome; portal vein thrombosis; pregnancy; varicose veins