Polycystic liver disease presenting as pruritus.
Polycystic liver disease (PCLD) is a rare autosomal dominant disorder which usually occurs in association with autosomal dominant polycystic kidney disease. Biliary obstruction is a rare complication of PCLD. Treatment options include percutaneous aspiration and sclerosis, surgical deroofing of cysts, liver resection or liver transplantation. Medical treatment involves the use of somatostatin analogues or mTOR inhibitors. We present a case of PCLD presenting for the first time with longstanding pruritus as the only symptom.
Department of Gastroenterology, Calicut Medical College, Calicut, India.
Deepak Kochummen
DK
Johnson
Department of Gastroenterology, Calicut Medical College, Calicut, India.
Shihab
S
Panchili
Department of Gastroenterology, Calicut Medical College, Calicut, India.
Sandesh
S
Kolasseri
Department of Gastroenterology, Calicut Medical College, Calicut, India.
Ramachandran Thazhath
RT
Mavali
Polycystic liver disease; autosomal dominant polycystic kidney disease; pruritus