[Anaesthetic implications in a pregnant patient with an extreme thrombocytopenia due to a May-Hegglin anomaly: general o regional anaesthesia?].
The May-Hegglin anomaly is an inherited disorder, so uncommon that the incidence is still unknown. It is characterized by macro-thrombocytopenia with normal platelet function and cytoplasmic inclusion bodies in granulocytes. The case is reported of a 28-year-old primiparous patient who had an urgent caesarean section due to failed induction of labour. The patient had no history of abnormal bleeding. Other causes of thrombocytopenia or platelet dysfunction, such as preeclampsia, HELLP syndrome, or placental abruption, were ruled out. The platelet count prior to surgery was 20,900/mm(3) with normal platelet function. General anaesthesia was performed. No excessive bleeding occurred and a platelet transfusion was not needed.
Servicio de Anestesiología y Reanimación, Hospital Universitario de Guadalajara, Guadalajara, España. Electronic address: gemmavallejo@gmail.com.
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García Vallejo
Servicio de Anestesiología y Reanimación, Hospital Universitario de Guadalajara, Guadalajara, España.
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M
Cabellos
Servicio de Anestesiología y Reanimación, Hospital Universitario de Guadalajara, Guadalajara, España.
M
M
Kabiri
Servicio de Anestesiología y Reanimación, Hospital Universitario de Guadalajara, Guadalajara, España.
J R
JR
Fraile
Servicio de Anestesiología y Reanimación, Hospital Universitario de Guadalajara, Guadalajara, España.
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J
Cuesta
D000328:Adult; D015360:Analgesia, Epidural; D016362:Analgesia, Obstetrical / Q000379:methods; D000768:Anesthesia, General / Q000379:methods*; D000773:Anesthesia, Obstetrical / Q000379:methods*; D002585:Cesarean Section; D000075202:Contraindications; D004630:Emergencies; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000097:blood*; D006801:Humans; D010976:Platelet Count; D011247:Pregnancy; D011250:Pregnancy Complications, Hematologic / Q000209:etiology*; D013921:Thrombocytopenia / Q000097:blood / Q000151:congenital* / Q000209:etiology*
Anestesia obstétrica; Anestesia raquídea; Bleeding; Caesarean; Cesárea; Epidural; Hemorragia; May-Hegglin anomaly; Obstetric anaesthesia; Spinal anaesthesia; Síndrome de May-Hegglin; Thrombocytopenia; Trombocitopenia