Primary renal Ewing's sarcoma: a rare entity.
Ewing's sarcoma, a primitive neuroectodermal tumour is a rare entity belonging to a family of neoplasms of neuroectodermal origin. These highly aggressive neoplasms primarily affect older children and young adults. They primarily involve the bones or soft tissues. A quarter of Ewing's sarcomas occur principally in the soft tissues with primary involvement of the kidney being exceptionally rare. We hereby, present a case of 6 years old girl child with primary Ewing's sarcoma of the kidney who presented with abdominal mass and posed much diagnostic challenge. The patient underwent complete surgical excision of tumour, and is being treated with aggressive adjuvant chemotherapy.
Department of Paediatric Haematology and Oncology, The Children's Hospital and ICH, Lahore.
Mahwish
M
Faizan
Department of Paediatric Haematology and Oncology, The Children's Hospital and ICH, Lahore.
Sadia
S
Anwar
Department of Paediatric Surgery, The Children's Hospital and ICH, Lahore.
Shahid
S
Iqbal
Department of Paediatric Radiology, The Children's Hospital and ICH, Lahore.
Qaiser
Q
Mehmood
Department of Histopathology, The Children's Hospital and ICH, Lahore.
Samina
S
Zaman
Department of Paediatric Haematology and Oncology, The Children's Hospital and ICH, Lahore.
Nasir
N
Abbas
Department of Paediatric Haematology and Oncology, The Children's Hospital and ICH, Lahore.
Shahid
S
Mahmood
Department of Paediatrics, Lahore General Hospital / PGMI, Lahore.
Agha Shabbir
AS
Ali
D001706:Biopsy; D017024:Chemotherapy, Adjuvant; D002648:Child; D003131:Combined Modality Therapy; D005260:Female; D006801:Humans; D007680:Kidney Neoplasms / Q000473:pathology* / Q000628:therapy; D009392:Nephrectomy; D018241:Neuroectodermal Tumors, Primitive, Peripheral / Q000473:pathology* / Q000628:therapy; D035583:Rare Diseases; D012512:Sarcoma, Ewing / Q000473:pathology* / Q000628:therapy; D016896:Treatment Outcome