Diffuse Caroli's disease with atypical presentation: a case report.
This paper describes a case of Caroli's disease in a female patient aged 32, who complained of nonspecific abdominal pain without cholesthasis or cholangitis. Liver resonance shows segment saccular dilations closely connected to intrahepatic biliary ducts, that differ from the Caroli's syndrome, which is more common and consists of multiple intrahepatic cystic dilatations, associated to congenital hepatic fibrosis. This patient has a congenital anomaly with an uncommon oligosymptomatic form of Caroli's disease that should be included in the differential diagnosis of patients with recurrent abdominal pain.
Gastroenterology Department at Faculdade de Medicina Nova Esperança-Famene, João Pessoa, Paraíba, Brazil.
Maíra Lima
ML
Acioli
Gastroenterology Department at Faculdade de Medicina Nova Esperança-Famene, João Pessoa, Paraíba, Brazil.
Lawrence Raizama Gonçalves
LR
Costa
Gastroenterology Department at Faculdade de Medicina Nova Esperança-Famene, João Pessoa, Paraíba, Brazil.
Mônica Souza
MS
de Miranda Henriques
Caroli’s syndrome; Cholangiopathy; Von Meyenburg complex; congenital bile duct dilatation