Cerebral Erdheim-Chester disease mimicking high-grade glial tumor: a case report.
Erdheim-Chester disease (ECD) is a non-Langerhans histiocytosis. It may present in every organ in the body, but isolated central nervous system involvement, especially a supratentorial intra-axial location, is extremely rare. We present a case of ECD of supratentorial intra-axial origin and discuss the clinical presentation, diagnosis and management strategies.
Department of Neurosurgery, Marmara University Medical School, Istanbul, Turkey.
Murat Şakir
MŞ
Ekşi
Gülden
G
Demirci Otluoğlu
Süheyla
S
Uyar Bozkurt
Aydın
A
Sav
Yaşar
Y
Bayri
Adnan
A
Dağçınar
D000293:Adolescent; D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D001932:Brain Neoplasms / Q000175:diagnosis* / Q000188:drug therapy; D003937:Diagnosis, Differential; D031249:Erdheim-Chester Disease / Q000175:diagnosis* / Q000188:drug therapy; D005260:Female; D005910:Glioma / Q000175:diagnosis* / Q000188:drug therapy; D006801:Humans
D000305:Adrenal Cortex Hormones