title: Pneumonectomy case in a newborn with congenital pulmonary lymphangiectasia.
abstract: Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregnancy, exhibited respiratory distress 1 hr after birth, which necessitated intubation and aggressive ventilator care. Right pneumonectomy was performed after her symptoms worsened. Histologic examination indicated CPL. She is currently 12 months old and developing normally. Pneumonectomy can be considered for treating respiratory symptoms for improving chances of survival in cases with unilateral CPL.
authors.affiliation: Department of Pediatrics, Eulji University College of Medicine, Daejeon, Korea.
authors.forename: Joon Ho
authors.identifier: 0000-0002-4251-6406
authors.initials: JH
authors.lastname: Hwang
authors.affiliation: Department of Thorasic and Cardiovascular Surgery, Eulji University College of Medicine, Daejeon, Korea.
authors.forename: Joo Heon
authors.initials: JH
authors.lastname: Kim
authors.affiliation: Department of Pathology, Eulji University College of Medicine, Daejeon, Korea.
authors.forename: Jung Ju
authors.initials: JJ
authors.lastname: Hwang
authors.affiliation: Department of Radiology, Eulji University College of Medicine, Daejeon, Korea.
authors.forename: Kyu Soon
authors.initials: KS
authors.lastname: Kim
authors.affiliation: Department of Pediatrics, Eulji University College of Medicine, Daejeon, Korea.
authors.forename: Seung Yeon
authors.identifier: 0000-0002-7004-4821
authors.initials: SY
authors.lastname: Kim
mesh_terms: D005260:Female; D005865:Gestational Age; D006801:Humans; D007231:Infant, Newborn; D008168:Lung / Q000473:pathology; D008171:Lung Diseases / Q000151:congenital* / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D008200:Lymphangiectasis / Q000151:congenital* / Q000175:diagnosis / Q000000981:diagnostic imaging / Q000473:pathology; D042601:Lymphatic Vessels / Q000473:pathology; D014057:Tomography, X-Ray Computed
keywords: Infant, Newborn; Lymphangiectasia, Pulmonary, Congenital; Pneumonectomy
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