title: Scimitar syndrome: the curved Turkish sabre.
abstract: Scimitar syndrome is a rare association of congenital cardiopulmonary anomalies characterized by an anomalous pulmonary vein (scimitar vein) that drains into the inferior vena cava, a hypogenetic right lung, and dextroposition of the heart. It has been reported in 3% to 6% of patients with partial anomalous pulmonary venous connection. Patients are either diagnosed early with severe symptoms (infantile type) or late with minimal symptoms (childhood/adult type). In this chapter we reviewed the history, pathophysiology, presentation, diagnosis, and treatment methods of Scimitar syndrome in the current era.
authors.affiliation: Anadolu Medical Center Hospital, Center for Heart and Vascular Care, Section of Cardiovascular Surgery and Cardiac Anesthesia, Kocaeli, Turkey. Electronic address: sertac.cicek@anadolusaglik.org.
authors.forename: Sertaç
authors.initials: S
authors.lastname: Ciçek
authors.affiliation: Anadolu Medical Center Hospital, Center for Heart and Vascular Care, Section of Cardiovascular Surgery and Cardiac Anesthesia, Kocaeli, Turkey.
authors.forename: Ahmet Hulusi
authors.initials: AH
authors.lastname: Arslan
authors.affiliation: Anadolu Medical Center Hospital, Center for Heart and Vascular Care, Section of Cardiovascular Surgery and Cardiac Anesthesia, Kocaeli, Turkey.
authors.forename: Murat
authors.initials: M
authors.lastname: Ugurlucan
authors.affiliation: Anadolu Medical Center Hospital, Center for Heart and Vascular Care, Section of Cardiovascular Surgery and Cardiac Anesthesia, Kocaeli, Turkey.
authors.forename: Yahya
authors.initials: Y
authors.lastname: Yildiz
authors.affiliation: Anadolu Medical Center Hospital, Center for Heart and Vascular Care, Section of Cardiovascular Surgery and Cardiac Anesthesia, Kocaeli, Turkey.
authors.forename: Sibel
authors.initials: S
authors.lastname: Ay
mesh_terms: D000328:Adult; D006348:Cardiac Surgical Procedures / Q000379:methods*; D003937:Diagnosis, Differential; D003952:Diagnostic Imaging; D006801:Humans; D007231:Infant, Newborn; D012587:Scimitar Syndrome / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*