title: Hearing restoration in NF2 patients and patients with vestibular schwannoma in the only hearing ear: report of two cases.
abstract: OBJECTIVE
  To explore audiologic outcome of auditory brain stem implantation (ABI) and cochlear implantation (CI) in NF2 patients and patients with vestibular schwannoma (VS) in the only hearing ear.
  
  
  METHODS
  Study includes retrospective analysis of 2 cases. One is totally deaf patient due to NF2, and the other one is totally deaf due to VS development in only hearing ear. Tumor was removed by retrosigmoid approach in NF2 patient and ABI was performed simultaneously. For the VS in only hearing ear case, tumor was removed by translabyrinthine approach and CI was performed simultaneously.
  
  
  RESULTS
  ABI patient showed quite well outcome during the 15 months of follow-up. She has 25 dB hearing threshold at speaking frequencies. She developed open set speech discrimination with 87.5% word discrimination score, and 70% sentence discrimination score. She uses device daily manner, she can use telephone. For CI patient, outcome is not perfect but satisfactory. She couldn't develop open set speech discrimination during the 18 months of follow-up. She has 67% the disyllabic words recognition score (close set). She is daily user of device. CI improves quite well lip reading.
  
  
  CONCLUSIONS
  ABI and CI are the two options to restore hearing in VS caused deafness. We advocate giving every effort to preserve cochlear nerve during the VS resection and place CI simultaneously. However if it is not possible to preserve cochlear nerve during surgery, ABI is also a good alternative for hearing restoration.
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Otolaryngology, Ankara, Turkey; Karabük University, Department of Otolaryngology, Karabük, Turkey.
authors.forename: Ali
authors.initials: A
authors.lastname: Ozdek
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Otolaryngology, Ankara, Turkey. Electronic address: bayiromer@hotmail.com.
authors.forename: Omer
authors.initials: O
authors.lastname: Bayır
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Neurosurgery, Ankara, Turkey.
authors.forename: Teoman
authors.initials: T
authors.lastname: Dönmez
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Neurosurgery, Ankara, Turkey.
authors.forename: Pınar
authors.initials: P
authors.lastname: Ozışık
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Otolaryngology, Ankara, Turkey.
authors.forename: Mustafa
authors.initials: M
authors.lastname: Sahin
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Otolaryngology, Ankara, Turkey.
authors.forename: Meltem
authors.initials: M
authors.lastname: Tulgar
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Otolaryngology, Ankara, Turkey.
authors.forename: Emel Çadallı
authors.initials: EÇ
authors.lastname: Tatar
authors.affiliation: Ministry of Health, Dışkapı Yıldırım Beyazıt Research Hospital, Department of Otolaryngology, Ankara, Turkey; Yıldırım Beyazıt University, Department of Otolaryngology, Ankara, Turkey.
authors.forename: Mehmet Hakan
authors.initials: MH
authors.lastname: Korkmaz
mesh_terms: D001301:Audiometry, Pure-Tone; D038263:Auditory Brain Stem Implantation / Q000379:methods*; D019929:Cochlear Implantation / Q000379:methods*; D003638:Deafness / Q000150:complications / Q000503:physiopathology / Q000601:surgery*; D005260:Female; D006309:Hearing / Q000502:physiology*; D006801:Humans; D008875:Middle Aged; D016518:Neurofibromatosis 2 / Q000150:complications*; D009464:Neuroma, Acoustic / Q000150:complications / Q000503:physiopathology* / Q000601:surgery; D020127:Recovery of Function