title: [Perioperative management for liver transplant in a patient with familial amyloid polyneuropathy with heart involvement].
abstract: Familial amyloid polyneuropathy (FAP) is a systemic amyloidosis caused by mutated transthyretin. Cardiac amyloidosis, the major prognostic determinant in systemic amyloidosis, is characterized by infiltration of the myocardium, leading to cardiomyopathy and conduction disturbances. Liver transplantation is the only curative option for patients with FAP. The case is presented of a 36-year-old patient with type i FAP with cardiac involvement, proposed for liver transplant surgery, which was successfully performed without any preoperative event of interest.
authors.affiliation: Servicio de Anestesiología y Reanimación, Hospital Universitario Virgen del Rocío, Sevilla, España. Electronic address: dalohero@gmail.com.
authors.forename: D
authors.initials: D
authors.lastname: López-Herrera Rodríguez
authors.affiliation: Servicio de Anestesiología y Reanimación, Hospital Universitario Virgen del Rocío, Sevilla, España.
authors.forename: R
authors.initials: R
authors.lastname: Guerrero Domínguez
authors.affiliation: Servicio de Anestesiología y Reanimación, Hospital Universitario Virgen del Rocío, Sevilla, España.
authors.forename: P
authors.initials: P
authors.lastname: Mellado Miras
authors.affiliation: Servicio de Anestesiología y Reanimación, Hospital Universitario Virgen del Rocío, Sevilla, España.
authors.forename: L
authors.initials: L
authors.lastname: Gómez Sosa
mesh_terms: D000328:Adult; D028227:Amyloid Neuropathies, Familial / Q000150:complications*; D054537:Atrioventricular Block / Q000000981:diagnostic imaging / Q000209:etiology; D009202:Cardiomyopathies / Q000000981:diagnostic imaging / Q000209:etiology*; D006801:Humans; D007431:Intraoperative Complications / Q000517:prevention & control; D016031:Liver Transplantation / Q000379:methods*; D008297:Male; D016343:Monitoring, Intraoperative; D009638:Norepinephrine / Q000627:therapeutic use; D019990:Perioperative Care / Q000379:methods*; D011183:Postoperative Complications / Q000517:prevention & control; D014655:Vascular Resistance / Q000187:drug effects
chemical_list: D009638:Norepinephrine
keywords: Amiloidosis; Amiloidosis cardíaca; Amyloidosis; Cardiac amyloidosis; Familial amyloid polyneuropathy; Liver transplantation; Polineuropatía amiloidótica familiar; Trasplante hepático