Unusual case of adult hemophagocytic syndrome.
Hemophagocytic syndrome (HPS) is an uncommon manifestation in systemic lupus erythematosus (SLE). Clinical features of HPS include fever, pancytopenia, abnormal liver enzyme, hepatosplenomegaly, lymphadenopathy, and coagulation disorder. HPS comprises primary and reactive forms. Herein, we describe a case of untreated SLE with HPS as one of the first manifestations of systemic Lupus.
Department of Internal Medicine, School of Medicine, Alzahra Hospital, Isfahan, Iran.
Babak
B
Tamizifar
Resident of Internal Medicine, Department of Internal Medicine, Alzahra Hospital, Isfahan, Iran.
Golnaz
G
Samadi
General Physician, Isfahan University of Medical Sciences, Isfahan, Iran.
Maryam
M
Rismankarzadeh
Autoimmunity; hemophagocytic syndrome; hemophagocytosis; systemic lupus erythematosus