Case for diagnosis. Dermatofibrosarcoma protuberans.
Dermatofibrosarcoma protuberans is a fibrohistiocytic tumor of intermediate malignancy with aggressive localized growth, high recurrence rate, but low metastatic potential. It appears as a hardened plaque, with slow growth, upon which the development of nodules occurs. It predominates in the trunk and is unusual in acral locations. Histopathology reveals spindle cells with storiform pattern and cartwheel-like or whirlwind-like aspect. Immunohistochemistry shows positivity for CD34. The treatment is surgical. We report a case of long evolution, with an unusual location, that relapsed after surgery, to emphasize the importance of early diagnosis and proper treatment, avoiding aggressive resections with increased morbidity.
State of Rio de Janeiro Federal University, Rio de Janeiro, RJ, Brazil.
Joanna Pimenta de Araujo
JP
Franco
State of Rio de Janeiro Federal University, Rio de Janeiro, RJ, Brazil.
Caroline Cruz
CC
Barbosa
State of Rio de Janeiro Federal University, Rio de Janeiro, RJ, Brazil.
Bárbara Ferreira Saraiva da
BF
Fonseca
State of Rio de Janeiro Federal University, Rio de Janeiro, RJ, Brazil.
Ricardo Barbosa
RB
Lima
State of Rio de Janeiro Federal University, Rio de Janeiro, RJ, Brazil.
Antônio Macedo
AM
D'Acri
State of Rio de Janeiro Federal University, Rio de Janeiro, RJ, Brazil.
Carlos José
CJ
Martins
D001706:Biopsy; D018223:Dermatofibrosarcoma / Q000473:pathology* / Q000601:surgery; D005260:Female; D005385:Fingers / Q000473:pathology; D006801:Humans; D007150:Immunohistochemistry; D008875:Middle Aged; D012878:Skin Neoplasms / Q000473:pathology* / Q000601:surgery; D016896:Treatment Outcome