Hairy cell leukemia presenting initially with symptoms of Behçet's disease.
Vasculitis is relatively uncommon in lymphoproliferative disease and may predate the diagnosis of lymphoproliferative disease. Many vasculitides have been associated with hairy cell leukemia (HCL), including polyarteritis nodosa (PAN) and leukocytoclastic vasculitis. We herein report a case whose initial presentation was like Behçet's disease (BD) (arthritis, oral and genital ulcerations, papulopustular skin lesions) in addition to pancytopenia, but turned out to have HCL. Because of the overlap between their symptoms, like oral ulcerations, skin lesions, arthritis and constitutional findings, HCL and BD may mimic each other. We should keep in mind other reasons for vasculitis such as lymphoproliferative disease, especially whose who have hematological abnormalities such as pancytopenia.
Department of Rheumatology, Faculty of Medicine, University of Uludag, Bursa, Turkey.
Mustafa Ferhat
MF
Oksuz
Belkis Nihan
BN
Coskun
Ayse Nur
AN
Tufan
Nurdan
N
Orucoglu
Ediz
E
Dalkilic
Hülya
H
Oztürk Nazlıoğlu
Yavuz
Y
Pehlivan
D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D001168:Arthritis / Q000209:etiology; D001528:Behcet Syndrome / Q000150:complications / Q000175:diagnosis*; D001706:Biopsy; D017338:Cladribine / Q000008:administration & dosage; D003937:Diagnosis, Differential; D006801:Humans; D007150:Immunohistochemistry; D007943:Leukemia, Hairy Cell / Q000150:complications / Q000175:diagnosis* / Q000188:drug therapy; D008297:Male; D008875:Middle Aged; D019226:Oral Ulcer / Q000209:etiology; D010198:Pancytopenia / Q000209:etiology; D010257:Paraneoplastic Syndromes / Q000209:etiology; D011237:Predictive Value of Tests; D011241:Prednisone / Q000008:administration & dosage; D012611:Scrotum / Q000473:pathology; D012871:Skin Diseases / Q000209:etiology; D016896:Treatment Outcome
D017338:Cladribine; D011241:Prednisone
Behçet's disease; diagnosis; hairy cell leukemia