Fast and early mandibular osteodistraction (FEMOD) in severe Pierre Robin Sequence.
Pierre Robin Sequence (PRS) is a congenital abnormality characterized by mandibular hypoplasia, glossoptosis and often secondary palate cleft. It may be an isolated or part of a most complicated syndrome. The genetic syndrome that most frequently co-occurs is Stickler syndrome characterized by skeletal abnormalities, joint pain, congenital myopia and retinal detachment. The authors describe their fast and early mandibular osteodistraction (FEMOD) protocol in severe cases of PRS airway obstruction.
Maxillo-Facial Surgery Dept (Chair: G. Iannetti, MD, PhD), "Sapienza" Università di Roma, Via del Policlinico, Roma, Italy.
Piero
P
Cascone
Department of Pediatrics PICU, Sapienza University, Rome, Italy.
Paola
P
Papoff
Maxillo-Facial Surgery Dept (Chair: G. Iannetti, MD, PhD), "Sapienza" Università di Roma, Via del Policlinico, Roma, Italy.
Paolo
P
Arangio
Maxillo-Facial Surgery Dept (Chair: G. Iannetti, MD, PhD), "Sapienza" Università di Roma, Via del Policlinico, Roma, Italy. Electronic address: valentino.vellone@gmail.com.
Valentino
V
Vellone
Maxillo-Facial Surgery Dept (Chair: G. Iannetti, MD, PhD), "Sapienza" Università di Roma, Via del Policlinico, Roma, Italy.
Vincenzo
V
Calafati
Clinica Odontoiatrica Dept, "Sapienza" Univesità di Roma, Italy.
Alessandro
A
Silvestri
D000402:Airway Obstruction / Q000601:surgery; D001168:Arthritis / Q000601:surgery; D002972:Cleft Palate / Q000473:pathology; D003240:Connective Tissue Diseases / Q000601:surgery; D016267:External Fixators; D005260:Female; D065710:Glossoptosis / Q000473:pathology; D006319:Hearing Loss, Sensorineural / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D008334:Mandible / Q000002:abnormalities / Q000601:surgery*; D063168:Mandibular Osteotomy / Q000379:methods; D008844:Micrognathism / Q000601:surgery; D019857:Osteogenesis, Distraction / Q000295:instrumentation / Q000379:methods*; D010348:Patient Care Team; D010855:Pierre Robin Syndrome / Q000473:pathology / Q000601:surgery*; D059745:Piezosurgery / Q000379:methods; D012163:Retinal Detachment / Q000601:surgery
Airway obstruction; Mandibular hypoplasia; Osteodistraction; Pierre Robin Sequence