Endodontic management of a patient with Bernard-Soulier syndrome.
Bernard-Soulier syndrome is a rare inherited disorder with giant platelets, thrombocytopenia and a prolonged bleeding time. These abnormalities are caused by genetic defects of the glycoprotein Ib/IX/V complex that constitutes the von Willebrand factor receptor on the platelet surface. We are documenting a 30-year-old female patient reported with a chief complaint of swelling in relation to right maxillary canine for 5 days. The primary treatment remains platelet transfusion. Root canal treatment was performed following platelet rich plasma transfusion. As the tooth was necrotic and had a periapical pathology post-operative bleeding was absent. The root canal treatment was uneventful and the patient was asymptomatic. Optimum oral hygiene practices were emphasized to avoid dental diseases.
Department of Endodontics, Government Dental College, Calicut, Kerala, India.
Dexton Antony
DA
Johns
Department of Endodontics, Government Dental College, Calicut, Kerala, India.
Reji P
RP
Gopalan
Department of Prosthodontics, Government Dental College, Calicut, Kerala, India.
Ganesh Tukaram
GT
Kamble
Department of Oral and Maxillofacial Pathology, KMCT Dental College, Calicut, Kerala, India.
S
S
Vidyanath
Bernard-Soulier syndrome; bleeding disorder; root canal therapy