[Multiple large hepatocellular adenomas in a patient with glycogen storage disease type Ia].
A man diagnosed at birth with glycogen storage disease type Ia was found to have multiple hepatocellular adenomas at 15 years of age. At 18 years of age, he underwent transarterial tumor embolization in segments 4 and 5. At 27 years of age, the tumor in segment 4 had increased in size on follow-up computed tomography, and he was referred to our hospital. Because the tumor was large, increasing in size, and we could not exclude malignancy, we performed resection of segments 4 and 8 of the liver and partial resection of segment 5 for excisional biopsy. The pathological diagnosis was multiple inflammatory hepatocellular adenomas.
Department of Surgery, Institute of Gastroenterology, Tokyo Women's Medical University.
Shuichiro
S
Uemura
Shun-Ichi
S
Ariizumi
Yutaka
Y
Takahashi
Akiko
A
Omori
Yoshihito
Y
Kotera
Satoshi
S
Katagiri
Etsuko
E
Hashimoto
Masayuki
M
Nakano
Masakazu
M
Yamamoto
D018248:Adenoma, Liver Cell / Q000175:diagnosis* / Q000209:etiology* / Q000473:pathology / Q000628:therapy; D000328:Adult; D003952:Diagnostic Imaging; D004621:Embolization, Therapeutic; D005953:Glycogen Storage Disease Type I / Q000150:complications*; D006498:Hepatectomy; D006801:Humans; D008113:Liver Neoplasms / Q000175:diagnosis* / Q000209:etiology* / Q000473:pathology / Q000628:therapy; D008297:Male; D016896:Treatment Outcome